Neurosurgical Pathology and Management of Limited Dorsal Myeloschisis Associated with Congenital Dermal Sinus in Infancy

2020 ◽  
Vol 55 (2) ◽  
pp. 113-125 ◽  
Author(s):  
Takato Morioka ◽  
Nobuya Murakami ◽  
Satoshi O. Suzuki ◽  
Akira Takada ◽  
Seiji Tajiri ◽  
...  
Keyword(s):  
Dermal Sinus ◽  
Congenital Dermal Sinus

Congenital Dermal Sinus Elements in Each Tethering Stalk of Coexisting Thoracic Limited Dorsal Myeloschisis and Retained Medullary Cord

2020 ◽  
pp. 1-8
Author(s):  
Takato Morioka ◽  
Nobuya Murakami ◽  
Masako Ichiyama ◽  
Takeshi Kusuda ◽  
Satoshi O. Suzuki
Keyword(s):  
Present Article ◽  
Dermoid Cyst ◽  
Spinal Dysraphism ◽  
Conus Medullaris ◽  
Dermal Sinus ◽  
Case Presentation ◽  
Upper Tract ◽  
Secondary Neurulation ◽  
Extradural Space ◽  
Congenital Dermal Sinus

<b><i>Introduction:</i></b> The embryogenesis of limited dorsal myeloschisis (LDM) likely involves impaired disjunction between the cutaneous and neural ectoderms during primary neurulation. Because LDM and congenital dermal sinus (CDS) have a shared origin in this regard, CDS elements can be found in the LDM stalk. Retained medullary cord (RMC) is a closed spinal dysraphism involving a robust, elongated, cord-like structure extending from the conus medullaris to the dural cul-de-sac. Because the RMC is assumed to be caused by impaired secondary neurulation, concurrent RMC and CDS cannot be explained embryologically. In the present article, we report a case in which CDS elements were noted in each tethering stalk of a coexisting LDM and RMC. <b><i>Case Presentation:</i></b> A 2.5-month-old boy with left clubfoot and frequent urinary and fecal leakage had 2 tethering tracts. The upper tract, which ran from the thoracic tail-like cutaneous appendage, had CDS elements in the extradural stalk and a tiny dermoid cyst in the intradural stalk immediately after the dural entry. In the lower tract, which ran from the lumbosacral dimple, the CDS as an extradural stalk continued to the RMC at the dural cul-de-sac. Both stalks were entirely resected through skip laminotomy/laminectomy at 1 stage to untether the cord and resect the CDS elements. <b><i>Conclusion:</i></b> Surgeons should be aware that CDS elements, in addition to LDM, may coexist with RMC that extends out to the extradural space.

Unusual Presentation of Congenital Dermal Sinus

2015 ◽  
Vol 25 (2) ◽  
pp. 238-241
Author(s):  
Mesut Mete ◽  
Tamay Simsek ◽  
Ahmet S. Umur ◽  
Mehmet Selçuki ◽  
Nurcan Umur ◽  
...  
Keyword(s):  
Unusual Presentation ◽  
Dermal Sinus ◽  
Congenital Dermal Sinus

CONGENITAL PTERIONAL DERMAL SINUS IN AN 18-MONTH-OLD CHILD

Neurosurgery ◽  
2007 ◽  
Vol 61 (3) ◽  
pp. E661-E661 ◽  
Author(s):  
William J. Mack ◽  
Saadi Ghatan
Keyword(s):  
Clinical Features ◽  
Neural Tube ◽  
Clinical Presentation ◽  
Sinus Tract ◽  
Dermal Sinus ◽  
Operating Microscope ◽  
First Case ◽  
Dermal Sinus Tract ◽  
Cranial Fossa ◽  
Congenital Dermal Sinus

Abstract OBJECTIVE Congenital dermal sinus tracts most frequently occur in the midline and are often associated with dermoid or epidermoid inclusion cysts. A lateral cranial origin is extremely rare and anatomically inconsistent with an etiology involving closure of the rostral neural tube during embryogenesis. CLINICAL PRESENTATION We describe the first case of a pterional cranial dermal sinus tract associated with a small epidermoid, with extension to the dura of the anterior cranial fossa. INTERVENTION The extra- and intracranial portions of the tract were visualized and resected with the use of an operating microscope. Pathological diagnosis confirmed dermal sinus tract. CONCLUSION We review the existing literature and address the developmental and clinical features pertinent to the management of cranial dermal sinus tracts, emphasizing the need for exploration of these potentially harmful lesions.

INTRACRANIAL COMPLICATIONS OF CONGENITAL DERMAL SINUSES

PEDIATRICS ◽  
1951 ◽  
Vol 8 (4) ◽  
pp. 463-474
Author(s):  
DONALD D. MATSON ◽  
FRANC D. INGRAHAM
Keyword(s):  
Surgical Treatment ◽  
Intracranial Extension ◽  
Dermal Sinus ◽  
Skull Defect ◽  
Complete Cure ◽  
Neural Axis ◽  
Intracranial Complications ◽  
Subcutaneous Mass ◽  
Sinus Opening ◽  
Congenital Dermal Sinus

Ten patients are presented in whom intracranial extension of a congenital dermal sinus was disclosed by operation. The complications of this lesion include infection in the form of meningitis, abscess formation and osteomyelitis as well as hydrocephalus due to obstruction of the spinal fluid pathways. In unexplained meningitis, the entire midline area of skin over the neural axis should be examined carefully for evidence of a dermal sinus opening. Whenever a dimple or subcutaneous mass is found in the midline of the scalp, RGs should be examined carefully for an underlying skull defect. When such a defect exists, intracranial exploration is indicated. Surgical treatment previous to development of intracranial infection is relatively simple and should be rewarded by complete cure. Excision after infection has occurred is difficult and the results in this group have been poor.

Congenital Dermal Sinus Tract of the Spine

2014 ◽  
Vol 29 (10) ◽  
pp. 1277-1282 ◽  
Author(s):  
Mesut Mete ◽  
Ahmet Sukru Umur ◽  
Yusuf Kurtuluş Duransoy ◽  
Mustafa Barutçuoğlu ◽  
Nurcan Umur ◽  
...  
Keyword(s):  
Sinus Tract ◽  
Dermal Sinus ◽  
Dermal Sinus Tract ◽  
Congenital Dermal Sinus

scholarly journals Complicated congenital dermal sinus: Diagnosis and management

2020 ◽  
Vol 21 ◽  
pp. 100739
Author(s):  
Mohamed Abdel Bari Mattar ◽  
Mohamed Kassem ◽  
Amin Mohamad Sabry
Keyword(s):  
Dermal Sinus ◽  
Diagnosis And Management ◽  
Congenital Dermal Sinus
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