Radiofrequency Ablation of Atrial Fibrillation in Patients with Ebstein's Anomaly: A Two-Case Report

Cardiology ◽  
2017 ◽  
Vol 139 (1) ◽  
pp. 33-36 ◽  
Author(s):  
Konstantinos E. Iliodromitis ◽  
Marc Bonsels ◽  
Rolf Borchard ◽  
Anja Dorszewski
Keyword(s):  
Atrial Fibrillation ◽  
Radiofrequency Ablation ◽  
Right Ventricle ◽  
Ebstein’S Anomaly ◽  
Atrioventricular Nodal Reentrant Tachycardia ◽  
Reentrant Tachycardia ◽  
Ebstein's Anomaly ◽  
The Right ◽  
Apical Displacement

Ebstein's anomaly (EA) is a rare congenital heart disease characterized by “atrialization” of the right ventricle, due to apical displacement of the tricuspid leaflets into the right ventricle. Patients with EA may develop all kinds of supraventricular arrhythmias requiring radiofrequency ablation. Atrial fibrillation (Afib) is a common arrhythmia in EA patients, and results in debilitating symptoms that often require surgical treatment. This is a follow-up report of 2 patients with EA undergoing radiofrequency ablation for Afib. The first patient underwent pulmonary vein isolation (PVI) and the ablation of a concomitant atrioventricular nodal reentrant tachycardia. The second patient was also treated with a PVI and a redo PVI 8 months later. Both patients remain in sinus rhythm 8 months on. Radiofrequency ablation is the therapy of choice for patients with pharmacological refractory Afib, but it is not common in patients with EA.

scholarly journals Left heart matters in Ebstein’s anomaly: the importance of a closer follow up—a case report

2020 ◽  
Vol 4 (4) ◽  
pp. 1-5 ◽  
Author(s):  
Maria Victoria Ordoñez ◽  
Radwa Bedair ◽  
Stephanie L Curtis
Keyword(s):  
Right Ventricle ◽  
Dynamic Compression ◽  
Symptomatic Patient ◽  
Left Ventricular ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Ventricular Outflow Obstruction ◽  
Left Ventricular Outflow ◽  
The Right

Abstract Background Ebstein’s anomaly (EA) is mainly thought of as a right heart condition, however, congenital left-sided lesions can co-exist. Therefore, it is paramount to include the left side of the heart as part of a routine investigation in these patients. We present a 57-year-old symptomatic patient with EA and progressive tricuspid regurgitation (TR) associated with acquired left ventricular outflow obstruction (LVOTO). Case summary A 57-year-old women, known to have severe EA presented with shortness of breath and chest pain on exertion secondary to progression of the tricuspid valve regurgitation and right ventricle dilatation leading to a dynamic compression of the left outflow tract requiring surgical intervention. Discussion Left ventricular obstruction secondary to severe TR and dilation of the right ventricle can present and remain silent at rest but becoming significant on exertion. Therefore, we recommend that all patients with EA and significant TR undergo exercise echocardiography at regular intervals to specifically look for acquired dynamic LVOTO.

scholarly journals Ebstein's anomaly as a cause of paroxysmal atrial fibrillation

2008 ◽  
Vol 65 (11) ◽  
pp. 847-850
Author(s):  
Miodrag Damjanovic ◽  
Danijela Djordjevic-Radojkovic ◽  
Zoran Perisic ◽  
Svetlana Apostolovic ◽  
Goran Koracevic ◽  
...  
Keyword(s):  
Atrial Fibrillation ◽  
Right Ventricle ◽  
Tricuspid Valve ◽  
Paroxysmal Atrial Fibrillation ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Wpw Syndrome ◽  
Echocardiographic Examination ◽  
Electrophysiological Examination ◽  
The Right

Background. Ebstein's anomaly is characterized by a displacement of the tricuspid valve toward apex, because of anomalous attachment of the tricuspid leaflets. There are type B of Wolff-Parkinson-White (WPW) syndrome and paroxysmal arrhythmias in more than a half of all patients. Case report. We presented a female, 32-year old, with frequent paroxysms of atrial fibrillation. After conversion of rhythm an ECG showed WPW syndrome. Echocardiographic examination discovered normal size of the left cardiac chambers with paradoxical ventricular septal motion. The right ventricle was very small because of its atrialization. The origin of the tricuspid valve was 20 mm closer to apex of the right ventricle than the origin of the mitral valve. Electrophysiological examination showed a posterolateral right accesorial pathway. Atrial fibrillation was induced very easily in electrophysiological laboratory and a successful ablation of accessorial pathway was made. There were no WPW syndrome and paroxysms of atrial fibrillation after that. Conclusion. Ebstein's anomaly is one of the reasons of paroxysmal atrial fibrillation, especially in young persons with WPW syndrome.

SUCCESSFUL CORRECTION OF EBSTEIN’S ANOMALY CRITICAL FORM COMPLICATED BY THROMBOSIS OF THE RIGHT VENTRICLE IN 10 MONTH-OLD CHILD

2017 ◽  
Vol 96 (1) ◽  
pp. 206-208
Author(s):  
R. R. Movsesyan ◽  
V. A. Bolsunovskiy ◽  
A. V. Bolsunovskiy ◽  
A. L. Tsytko ◽  
D. R. Yamgurov
Keyword(s):  
Right Ventricle ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Critical Form ◽  
The Right

Two decades of experience on ablation in children with Ebstein’s anomaly

2021 ◽  
pp. 1-7
Author(s):  
Tevfik Karagöz ◽  
İlker Ertuğrul ◽  
Ebru Aypar ◽  
Aydın Adıgüzel ◽  
Hayrettin Hakan Aykan ◽  
...  
Keyword(s):  
Atrial Flutter ◽  
Atrial Tachycardia ◽  
Ebstein’S Anomaly ◽  
Atrioventricular Nodal Reentrant Tachycardia ◽  
Success Rates ◽  
Recurrence Rates ◽  
Ebstein's Anomaly ◽  
Accessory Pathways ◽  
Rare Occasion ◽  
The Right

Abstract Introduction: Accessory pathways are commonly seen due to delamination of tricuspid valve leaflets. In addition to accessory pathways, an enlarged right atrium due to tricuspid regurgitation and incisional scars creates substrates for atrial re-entries and ectopic tachycardia. We sought to describe our experience with catheter ablation in children with Ebstein’s anomaly. Methods and results: During the study period, of 89 patients diagnosed with Ebstein’s anomaly, 26 (30.9%) of them who underwent 33 ablation procedures were included in the study. Accessory pathways were observed in the majority of procedures (n = 27), whereas atrial flutter was observed in five, atrioventricular nodal reentrant tachycardia in five, and atrial tachycardia in two procedures. Accessory pathways were commonly localised in the right posteroseptal (n = 10 patients), right posterolateral (n = 14 patients), septal (n = two patients), and left posteroseptal (n = one patient) areas. Multiple accessory pathways and coexistent arrhythmia were observed in six procedures. All ablation attempts related to the accessory pathways were successful, but recurrence was observed in five (19%) of the ablations. Ablation for atrial flutter was performed in five patients; two of them were ablated successfully. One of the atrial tachycardia cases was ablated successfully. Conclusions: Ablation in patients with Ebstein’s anomaly is challenging, and due to nature of the disease, it is not a rare occasion in this group of patients. Ablation of accessory pathways has high success, but also relatively high recurrence rates, whereas ablation of atrial arrhythmias has lower success rates, especially in operated patients.

scholarly journals Ebstein’s Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)

2021 ◽  
Vol 2021 ◽  
pp. 1-5
Author(s):  
Mohammad Mehdi ◽  
Snigdha Bhatia ◽  
Mehul Patel ◽  
Ashraf Aly
Keyword(s):  
Heart Defects ◽  
Fontan Procedure ◽  
Left Ventricular ◽  
Ebstein’S Anomaly ◽  
Left Ventricular Noncompaction ◽  
Fetal Diagnosis ◽  
Ventricular Noncompaction ◽  
Ebstein's Anomaly ◽  
The Right ◽  
Apical Displacement

Ebstein’s anomaly is characterized by the apical displacement of the septal and posterior leaflets of the tricuspid valve with atrialization of the right ventricle (RV). It is commonly associated with other heart defects including left ventricular noncompaction. We describe a case of prenatally diagnosed Ebstein’s anomaly in association with left ventricular noncompaction and a septal defect between the left ventricle and the atrialized portion of the RV (Gerbode-like defect). The patient underwent a modified Blalock−Taussig shunt followed by Glenn procedure because of severe RV hypoplasia and RV outflow tract obstruction. The patient tolerated both procedures and is doing clinically well in anticipation of Fontan procedure for single ventricle palliation.

scholarly journals SURGICAL PALLIATION IN PATIENTS WITH EBSTEIN'S ANOMALY AND CONGENITAL HYPOPLASIA OF THE RIGHT VENTRICLE

1960 ◽  
Vol 40 (3) ◽  
pp. 310-320 ◽  
Author(s):  
Milton Weinberg ◽  
Juan P. Bicoff ◽  
Magnus H. Agustsson ◽  
Zwi Steiger ◽  
Benjamin M. Gasul ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Surgical Palliation ◽  
The Right

scholarly journals Hypereosinophilic Syndrome Leading to Severe Right-Sided Heart Failure in a Patient with Ebstein's Anomaly

2013 ◽  
Vol 2013 ◽  
pp. 1-3 ◽  
Author(s):  
Joas John Kyabonaki ◽  
Bjarne Linde Nørgaard ◽  
Søren Høyer ◽  
Niels Holmark Andersen
Keyword(s):  
Heart Failure ◽  
Right Ventricle ◽  
Tricuspid Regurgitation ◽  
Hypereosinophilic Syndrome ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Long Course ◽  
The Right ◽  
Explanted Heart ◽  
Severe Fibrosis

A 36-year-old male with mild Ebstein's anomaly developed severe right-sided heart failure, following a 5-year-long course of hypereosinophilic syndrome. No regular followups had been done, during the years of antineoplastic therapy. A year after being cured from the hypereosinophilic syndrome, the patient developed right-sided heart failure symptoms and was found to have excessive fibrosis of the right ventricular endocardium and free tricuspid regurgitation. The findings were compatible with substantial scarring of the endocardium caused by the hypereosinophilic syndrome. Over a few years, the patient deteriorated significantly and was finally offered a heart transplant. Examination of the explanted heart revealed severe fibrosis of the right ventricle and almost complete sparing of the left.

Long-term follow-up of fast pathway radiofrequency ablation in atrioventricular nodal reentrant tachycardia

2002 ◽  
Vol 89 (9) ◽  
pp. 1124-1125 ◽  
Author(s):  
Lars Lickfett ◽  
Dietrich Pfeiffer ◽  
Rainer Schimpf ◽  
Hugh Calkins ◽  
Berndt Lüderitz ◽  
...  
Keyword(s):  
Radiofrequency Ablation ◽  
Atrioventricular Nodal Reentrant Tachycardia ◽  
Reentrant Tachycardia ◽  
Long Term Follow Up ◽  
Fast Pathway

Cone repair for Ebstein’s anomaly and atrial fibrillation ablation in an adult patient

2021 ◽  
Keyword(s):  
Atrial Fibrillation ◽  
Tricuspid Valve ◽  
Pulmonary Veins ◽  
Maze Procedure ◽  
Right Atrial ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Previously Treated ◽  
Cone Repair ◽  
The Right

We present a 52-year-old woman with Ebstein’s anomaly not previously treated. In this subset of patients, there are no clear guidelines regarding the best surgical strategy for treating the tricuspid valve: replace it or repair it. In this case, extensive repair of the tricuspid valve and the right ventricle is achieved using the cone repair technique popularized by Dr. José Pedro Da Silva. Because the patient also presented with symptomatic paroxysmal atrial fibrillation, a right atrial maze procedure combined with isolation of the pulmonary veins was performed using both radiofrequency and cryotherapy. At the last follow-up, 2 years after the repair, the patient is asymptomatic and maintains sinus rhythm. The last echocardiogram showed mild tricuspid regurgitation with normal right ventricular function.

Sign in / Sign up

Export Citation Format

Share Document