Quantitative Assessment of Trunk Muscles Involvement in Patients with Myotonic Dystrophy Type 1 Using a Whole Body Muscle Magnetic Resonance Imaging

2017 ◽  
Vol 77 (5-6) ◽  
pp. 238-245 ◽  
Author(s):  
Donghwi Park ◽  
Jin-Sung Park
Keyword(s):  
Magnetic Resonance Imaging ◽  
Magnetic Resonance ◽  
Quantitative Assessment ◽  
Trunk Muscles ◽  
Whole Body ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Resonance Imaging ◽  
Muscle Magnetic Resonance Imaging

Whole-body high-field magnetic resonance imaging in myotonic dystrophy type 1 and type 2

2005 ◽  
Vol 32 (S 4) ◽  
Author(s):  
C Kornblum ◽  
R Schröder ◽  
K Kesper ◽  
T Klockgether ◽  
H Schild ◽  
...  
Keyword(s):  
Magnetic Resonance Imaging ◽  
Magnetic Resonance ◽  
Myotonic Dystrophy ◽  
High Field ◽  
Whole Body ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Resonance Imaging

Cranial magnetic resonance imaging in genetically proven myotonic dystrophy type 1 and 2

2004 ◽  
Vol 251 (6) ◽  
Author(s):  
Cornelia Kornblum ◽  
J�rgen Reul ◽  
Wolfram Kress ◽  
Christoph Grothe ◽  
Niki Amanatidis ◽  
...  
Keyword(s):  
Magnetic Resonance Imaging ◽  
Magnetic Resonance ◽  
Myotonic Dystrophy ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Resonance Imaging ◽  
Cranial Magnetic Resonance Imaging

scholarly journals MRI of Tibialis Anterior Skeletal Muscle in Myotonic Dystrophy Type 1

2011 ◽  
Vol 38 (1) ◽  
pp. 112-118 ◽  
Author(s):  
Chantal Coté ◽  
Bassem Hiba ◽  
Luc J. Hebert ◽  
Christophe Vial ◽  
Jean François Remec ◽  
...  
Keyword(s):  
Magnetic Resonance Imaging ◽  
Skeletal Muscle ◽  
Magnetic Resonance ◽  
Tibialis Anterior ◽  
Myotonic Dystrophy Type 1 ◽  
Myotonic Dystrophy Type ◽  
Resonance Imaging ◽  
Muscle Mri ◽  
Ctg Repeats

Abstract:Objective:The aim of this study was to evaluate whether magnetic resonance imaging (MRI) can be used as a noninvasive approach to assessment of disease severity and muscle damage in Myotonic Dystrophy type 1 (DM1).Methods:The MRI findings in legs of 41 patients with DM1 were evaluated with respect to the tibialis anterior (TA) skeletal muscle impairment. Magnetic resonance imaging findings were compared with TA strength measurements obtained by quantitative manual testing, duration of the disease and with the length of the CTG repeats.Results:Muscle MRI abnormalities were observed in 80% of DM1 patients, ranging from edema-like abnormalities alone to severe atrophy / fatty replacement. Edema-like abnormalities seem to be an earlier MRI marker of the disease. Fatty infiltration/atrophy correlated with the TA muscle force (r = 0.95), the severity (P = 0.00001) of the disease but not with the duration of the disease (P = 0.3) or the length of the CTG repeats (P > 0.10), measured in peripheral leukocytes. Evaluation of other muscles of the legs revealed that the medial gastrocnemius and soleus muscles were the most frequently and severely affected muscles, while tibialis posterior muscles were relatively spared. Edema-like abnormalities are most frequently observed in the skeletal muscles of the anterior compartment.Conclusion:Muscle MRI is helpful to depict muscle abnormalities but does not seem to be a reliable indicator of skeletal muscle involvement in DM1 since the decrease in TAmuscle force is not correlated with MRI abnormalities in some patients.

Whole-body muscle magnetic resonance imaging inSEPN1-related myopathy shows a homogeneous and recognizable pattern

2015 ◽  
Vol 52 (5) ◽  
pp. 728-735 ◽  
Author(s):  
Karolina Hankiewicz ◽  
Robert Y. Carlier ◽  
Leila Lazaro ◽  
Javier Linzoain ◽  
Christine Barnerias ◽  
...  
Keyword(s):  
Magnetic Resonance Imaging ◽  
Magnetic Resonance ◽  
Whole Body ◽  
Resonance Imaging ◽  
Body Muscle ◽  
Muscle Magnetic Resonance Imaging
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