Unilateral High-Altitude Pulmonary Edema in a Subject with Right Pulmonary Artery Hypoplasia

Respiration ◽  
1994 ◽  
Vol 61 (1) ◽  
pp. 51-54 ◽  
Author(s):  
G. Fiorenzano ◽  
V. Rastelli ◽  
V. Greco ◽  
A. Di Stefano ◽  
M. Dottorini
Keyword(s):  
Pulmonary Artery ◽  
Pulmonary Edema ◽  
High Altitude ◽  
High Altitude Pulmonary Edema ◽  
Right Pulmonary Artery ◽  
Pulmonary Artery Hypoplasia

High-Altitude Pulmonary Edema with Absent Right Pulmonary Artery

PEDIATRICS ◽  
1985 ◽  
Vol 75 (2) ◽  
pp. 314-317
Author(s):  
Billy Rios ◽  
David J. Driscoll ◽  
Dan G. McNamara
Keyword(s):  
Pulmonary Artery ◽  
Pulmonary Edema ◽  
High Altitude ◽  
Congenital Absence ◽  
High Altitude Pulmonary Edema ◽  
Threatening Condition ◽  
Right Pulmonary Artery ◽  
Life Threatening ◽  
Low Altitude ◽  
The Right

High-altitude pulmonary edema potentially is fatal. Adults with unilateral absence of a right pulmonary artery are particularly susceptible to high-altitude pulmonary edema. The occurrence of high-altitude pulmonary edema was documented in a child with congenital absence of the right pulmonary artery. Improvement occurred only upon descent to low altitude. Physicians should be aware of this life-threatening condition in children ascending to high altitude, particularly in individuals with unilateral absence of a pulmonary artery.

High-Altitude Pulmonary Edema in Persons without the Right Pulmonary Artery

1980 ◽  
Vol 302 (19) ◽  
pp. 1070-1073 ◽  
Author(s):  
Peter H. Hackett ◽  
C. Edward Creagh ◽  
Robert F. Grover ◽  
Benjamin Honigman ◽  
Charles S. Houston ◽  
...  
Keyword(s):  
Pulmonary Artery ◽  
Pulmonary Edema ◽  
High Altitude ◽  
High Altitude Pulmonary Edema ◽  
Right Pulmonary Artery ◽  
The Right

scholarly journals Genetics of pulmonary hypertension and high-altitude pulmonary edema

2020 ◽  
Vol 128 (5) ◽  
pp. 1432-1438
Author(s):  
Christina A. Eichstaedt ◽  
Nicola Benjamin ◽  
Ekkehard Grünig
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Artery ◽  
Pulmonary Edema ◽  
High Altitude ◽  
Clinical Feature ◽  
Future Research ◽  
Inherited Disease ◽  
Research Perspectives ◽  
Protein Receptor ◽  
High Altitude Pulmonary Edema

Heritable pulmonary arterial hypertension (PAH) is an autosomal dominantly inherited disease caused by mutations in the bone morphogenetic protein receptor 2 ( BMPR2) gene and/or genes of its signaling pathway in ~85% of patients. A genetic predisposition to high-altitude pulmonary edema (HAPE) has long been suspected because of familial HAPE cases, but very few possibly disease-causing mutations have been identified to date. This minireview provides an overview of genetic analyses investigating common polymorphisms in HAPE-susceptible patients and the directed identification of disease-causing mutations in PAH patients. Increased pulmonary artery pressure is highlighted as an overlapping clinical feature of the two diseases. Moreover, studies showing increased pulmonary artery pressures in HAPE-susceptible patients during exercise or hypoxia as well as in healthy BMPR2 mutation carriers are illustrated. Finally, high-altitude pulmonary hypertension is introduced and future research perspectives outlined.

Unilateral Absence of Pulmonary Artery

2010 ◽  
pp. 239-246
Author(s):  
Edward C. Rosenow
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Pulmonary Artery ◽  
Pulmonary Edema ◽  
High Altitude ◽  
Tetralogy Of Fallot ◽  
Congenital Heart ◽  
Congestive Heart Disease ◽  
High Altitude Pulmonary Edema

• If congenital, half of cases are associated with congenital heart disease ∘ Left: tetralogy of Fallot ∘ Right: less severe congestive heart disease • Right and left sides are affected equally • May be asymptomatic ∘ Affected patients are predisposed to high-altitude pulmonary edema...

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