scholarly journals A Challenging Giant Dermatofibrosarcoma Protuberans on the Face

2016 ◽  
Vol 2016 ◽  
pp. 1-4 ◽  
Author(s):  
Gimena Castro Pérez ◽  
Cintia Arias ◽  
Paula Luna ◽  
Irene Sorín ◽  
Luis Daniel Mazzuoccolo
Keyword(s):  
Local Recurrence ◽  
Head And Neck ◽  
Soft Tissue Tumor ◽  
Dermatofibrosarcoma Protuberans ◽  
Low Grade ◽  
Total Head ◽  
Malignant Soft Tissue Tumor ◽  
The Face ◽  
Subcutaneous Tissues ◽  
Malignant Soft Tissue

Dermatofibrosarcoma protuberans (DFSP) is a malignant fibrohistiocytic tumor that appears exclusively on the skin. It is a low-grade malignant soft tissue tumor of subcutaneous tissues that has a propensity for local recurrence but seldom metastasizes. It may rarely occur on the head and neck accounting for less than one percent of total head and neck malignancies. We present a man with a giant DFSP on the face. Oncological, functional, and aesthetic aspects are set forth.

A low‐grade malignant soft tissue tumor with S100 and CD34 co‐expression showing novel CDC42SE2‐BRAF fusion with distinct features

2020 ◽  
Vol 59 (10) ◽  
pp. 595-600 ◽  
Author(s):  
Shao‐Jie Sheng ◽  
Ju‐Ming Li ◽  
Yue‐Fen Zou ◽  
Xiao‐Jing Peng ◽  
Qian‐Yu Wang ◽  
...  
Keyword(s):  
Soft Tissue ◽  
Soft Tissue Tumor ◽  
Low Grade ◽  
Tissue Tumor ◽  
Malignant Soft Tissue Tumor ◽  
Braf Fusion ◽  
Distinct Features ◽  
Malignant Soft Tissue

scholarly journals Giant Diaphragmatic Angiosarcoma of Adult: A Case Report and Review of Literature

2012 ◽  
Vol 2012 ◽  
pp. 1-3
Author(s):  
Tao Ren ◽  
Xue-qian Chen
Keyword(s):  
Case Report ◽  
Soft Tissue ◽  
Local Recurrence ◽  
Adult Patient ◽  
Distant Metastasis ◽  
Soft Tissue Tumor ◽  
Review Of Literature ◽  
Tissue Tumor ◽  
Malignant Soft Tissue Tumor ◽  
Malignant Soft Tissue

Angiosarcoma is a rare vascular malignant soft tissue tumor, with highly malignant, invasive, and multifocal characteristics of biology, which is prone to local recurrence and distant metastasis, so the prognosis is extremely poor. It rarely involves the diaphragm. We present the case of an adult patient who had a primary giant angiosarcoma of the left-sided diaphragm.

scholarly journals Recurrent dermatofibrosarcoma protuberans of head and neck with fibrosarcomatous change: a challenge for the head and neck surgeon

2020 ◽  
Vol 6 (8) ◽  
pp. 1563
Author(s):  
Balaji Ramamourthy ◽  
Kanika Arora ◽  
Balamurugan Thirunavukkarasu ◽  
Anurag S. Ramavat ◽  
Amanjit Bal
Keyword(s):  
Head And Neck ◽  
Neck Region ◽  
Dermatofibrosarcoma Protuberans ◽  
Low Grade ◽  
Soft Tissue Neoplasm ◽  
Head And Neck Region ◽  
Management Protocol ◽  
Key Points ◽  
Slow Growing ◽  
Malignant Soft Tissue

<p class="abstract">Dermatofibrosarcoma protuberans (DFSP) of head and neck is a rare, slow growing, intermediate to low grade malignant soft tissue neoplasm with high rates of local recurrence requiring multiple surgeries posing great distress for both the patient and treating physician alike. Fibrasarcomatous change is a very rare occurrence in such tumors increasing risk of distant metastasis. We report such a rare case of recurrent DFSP with fibrosarcomatous change of the head and neck region, the management protocol and the key points a surgeon should keep in mind while treating such patients.</p><p class="abstract"> </p>

scholarly journals Wide Local Excision for Dermatofibrosarcoma Protuberans: A Single-Center Series of 90 Patients

2015 ◽  
Vol 2015 ◽  
pp. 1-9 ◽  
Author(s):  
Byung Jun Kim ◽  
Hyeonwoo Kim ◽  
Ung Sik Jin ◽  
Kyung Won Minn ◽  
Hak Chang
Keyword(s):  
Local Recurrence ◽  
Local Excision ◽  
Wide Local Excision ◽  
Safety Margin ◽  
Dermatofibrosarcoma Protuberans ◽  
Low Grade ◽  
Recurrence Free Survival ◽  
Free Survival ◽  
Incomplete Removal ◽  
Surgical Methods

Background. Dermatofibrosarcoma protuberans (DFSP), a rare low-grade sarcoma of fibroblast origin, tends to extend in a finger-like fashion beyond macroscopic tumor margins. Therefore, incomplete removal and subsequent recurrence are common. This study aimed to determine the efficacy of wide local excision (WLE) for controlling local recurrence of DFSP.Methods. The medical records of 90 DFSP patients who received WLE at our hospital between June 1992 and January 2015 were retrospectively reviewed. WLE was conducted including a 3 cm (range, 1 to 5 cm) safety margin according to tumor size, location, and recurrence status. Clinical and tumor characteristics and surgical methods were evaluated for risk factor analysis and local recurrence-free survival.Results. DFSP occurred most often in patients in their 30s (30%) and on the trunk (51.1%). Five patients (5.5%) experienced local recurrence during the 43.4-month follow-up period. Recurrence was found at a mean of 10.8 months after WLE. Although no factors were significantly associated with recurrence, recurrences were more frequent in head and neck. Recurrence-free survival was 87% in 6 years and 77% in 7 years.Conclusions. WLE with adequate lateral and deep margins can effectively control local recurrence rate and is a simple and effective method to treat DFSP.

Preoperative evaluation of intraoperative blood loss during malignant soft tissue tumor resection by ultrasonography

2018 ◽  
Vol 23 (2) ◽  
pp. 403-407 ◽  
Author(s):  
Takeshi Morii ◽  
Tomonori Kishino ◽  
Naoko Shimamori ◽  
Mitsue Motohashi ◽  
Hiroaki Ohnishi ◽  
...  
Keyword(s):  
Soft Tissue ◽  
Blood Loss ◽  
Soft Tissue Tumor ◽  
Preoperative Evaluation ◽  
Tumor Resection ◽  
Intraoperative Blood Loss ◽  
Tissue Tumor ◽  
Malignant Soft Tissue Tumor ◽  
Malignant Soft Tissue

Alveolar Soft Part Sarcoma Presenting as a Uterine Polyp

2019 ◽  
Vol 152 (Supplement_1) ◽  
pp. S37-S37
Author(s):  
Mariangela Gomez ◽  
Kerry Whiting
Keyword(s):  
Soft Tissue Tumor ◽  
Soft Part ◽  
Female Genital Tract ◽  
Alveolar Soft Part Sarcoma ◽  
Complete Excision ◽  
Molecular Features ◽  
Malignant Soft Tissue Tumor ◽  
Pathological Evaluation ◽  
Malignant Soft Tissue ◽  
Female Genital

Abstract Background Alveolar soft part sarcoma (ASPS) is a rare malignant soft tissue tumor, mainly localized in the extremities, occurring principally in adolescents and young adults. ASPS is uncommon in the female genital tract. Case report We here report a case of ASPS in a 20-year-old nullipara, presenting with vaginal bleeding and profound anemia requiring blood transfusions. Ultrasonographic examination revealed a polyp in the lower uterine segment. Surgical resection of the polyp was performed, and pathological evaluation showed the typical histological, immunohistochemical, and molecular features consistent with ASPS. At the time of this report, the patient was scheduled for total hysterectomy with promising results. Conclusion Given the infrequency of ASPS, pathological evaluation is or utmost importance in order to establish an accurate diagnosis. When presenting as a primary tumor, complete excision is fundamental in the treatment.

Synovial Sarcoma of the Brachial Plexus

Neurosurgery ◽  
2011 ◽  
Vol 70 (5) ◽  
pp. 1329-1333 ◽  
Author(s):  
Farhad Pirouzmand ◽  
Kavya Kommaraju ◽  
Kenneth J. Craddock ◽  
David Howarth
Keyword(s):  
Brachial Plexus ◽  
Synovial Sarcoma ◽  
Soft Tissue Tumor ◽  
Clinical Presentation ◽  
Clinical Course ◽  
Relevant Literature ◽  
Adjuvant Radiation ◽  
Malignant Soft Tissue Tumor ◽  
Malignant Soft Tissue ◽  
Firm Mass

Abstract BACKGROUND AND IMPORTANCE: Synovial sarcoma (SS) is a malignant soft-tissue tumor that rarely involves brachial plexus. The authors report a case of brachial plexus SS and review the relevant literature. CLINICAL PRESENTATION: A 53-year-old woman presented with gradually enlarging right subclavicular mass over 5 years associated with sharp aching pain radiating down toward the radial 3 fingers. On examination, she had a corresponding firm mass in the supraclavicular region with a positive Tinel sign. There was no objective neurological deficit. She underwent partial excision of this mass without any further adjuvant radiation or chemotherapy. Pathology was consistent with SS. CONCLUSION: Lack of any recurrence in this case 6 years after incomplete excision with no adjuvant therapy suggests slow clinical course in some of these sarcomas.

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