scholarly journals Congenital Portosystemic Shunt: Our Experience

2015 ◽  
Vol 2015 ◽  
pp. 1-5 ◽  
Author(s):  
Tiziana Timpanaro ◽  
Stefano Passanisi ◽  
Alessandra Sauna ◽  
Claudia Trombatore ◽  
Monica Pennisi ◽  
...  
Keyword(s):  
Multidisciplinary Approach ◽  
Case Reports ◽  
Endovascular Embolization ◽  
Portosystemic Shunt ◽  
Type Ii ◽  
Systemic Vein ◽  
Congenital Portosystemic Shunt ◽  
Congenital Extrahepatic Portosystemic Shunt ◽  
Case Presentations ◽  
Rule Out

Introduction. Congenital portosystemic venous malformations are rare abnormalities in which the portal blood drains into a systemic vein and which are characterized by extreme clinical variability.Case Presentations. The authors present two case reports of a congenital extrahepatic portosystemic shunt (Type II). In the first patient, apparently nonspecific symptoms, such as headache and fatigue, proved to be secondary to hypoglycemic episodes related to the presence of a portosystemic shunt, later confirmed on imaging. During portal vein angiography, endovascular embolization of the portocaval fistula achieved occlusion of the anomalous venous tract. In the second patient, affected by Down’s syndrome, the diagnosis of a portosystemic malformation was made by routine ultrasonography, performed to rule out concurrent congenital anomalies. Because of the absence of symptoms, we chose to observe this patient.Conclusions. These two case reports demonstrate the clinical heterogeneity of this malformation and the need for a multidisciplinary approach. As part of a proper workup, clinical evaluation must always be followed by radiographic diagnosis.

scholarly journals Comparison of Surgical Ligation and Endovascular Embolization in the Management of Type II Congenital Extrahepatic Portosystemic Shunt: A Retrospective Clinical Study

2021 ◽  
Author(s):  
Jin-long Zhang ◽  
Wei Dong Duan ◽  
Zhu Ting Fang ◽  
Mao Qiang Wang ◽  
Li Cui ◽  
...  
Keyword(s):  
Endovascular Embolization ◽  
Portosystemic Shunt ◽  
Type Ii ◽  
Intraoperative Blood Loss ◽  
Procedure Time ◽  
Surgical Ligation ◽  
Post Procedure ◽  
Congenital Extrahepatic Portosystemic Shunt ◽  
Interventional Group ◽  
Surgical Group

Abstract Background: Surgical ligation and endovascular embolization have been recommended for type II congenital extrahepatic portosystemic shunt (CEPS); however, no consensus has been reached. This study was designed to compare the safety and efficacy of surgical ligation and endovascular embolization for the treatment of type II CEPS. Methods: In this retrospective study, 23 consecutive patients diagnosed with type II CEPS between March 2011 and April 2019 were divided into either a surgical group (n=13; 41.5±19.9years) or the interventional group (n =10; 44.9±19.7years). The surgical group underwent laparoscopic surgical ligation of the shunt alone or ligation of the shunt and splenic artery and/or vein. The interventional group underwent endovascular embolization using microcoils, detachable coils and vascular plug. Results: All 23 patients received a one-step shunt closure, and their clinical symptoms were significantly improved within 3 months post-procedure and without recurrence during follow-up. The serum ammonia levels in both groups decreased after the procedure and dropped to normal level at 6 to 12 months post-procedure. Compared with baseline, the portal vein diameter in interventional group increased significantly at 3-, 6-, 12-, and 36-month post-occlusion (P=0.01 for all). The procedure time was shorter in interventional group (127.0±43.2minutes) than surgical group (219.8±56.7minutes; P <0.001). The intraoperative blood loss in interventional group (32.0±62.5mL) was less than that in surgical group (238.5±396.9mL; P=0.001).Conclusion: Both surgical ligation and endovascular embolization are effective in the treatment of type II CEPS. Endovascular embolization has the advantages of shorter procedure time, and less intraoperative blood loss. The ligation of the portosystemic shunt and splenic artery and vein is feasible with apparent safety, and it could avoid a second surgical treatment.

scholarly journals Efficacy and Safety of Surgical Ligation versus Endovascular Embolization for Type II Congenital Extrahepatic Portosystemic Shunt

2021 ◽  
Vol 2021 ◽  
pp. 1-13
Author(s):  
Jinlong Zhang ◽  
Weidong Duan ◽  
Zhuting Fang ◽  
Maoqiang Wang ◽  
Li Cui ◽  
...  
Keyword(s):  
Splenic Artery ◽  
Endovascular Embolization ◽  
Portosystemic Shunt ◽  
Type Ii ◽  
Intraoperative Blood Loss ◽  
Procedure Time ◽  
Surgical Ligation ◽  
Congenital Extrahepatic Portosystemic Shunt ◽  
Interventional Group ◽  
Surgical Group

Objective. To evaluate the safety and efficacy of surgical ligation and endovascular embolization for the treatment of type II congenital extrahepatic portosystemic shunt (CEPS). Methods. In this retrospective study, 23 patients diagnosed with type II CEPS between March 2011 and April 2019 were divided into either a surgical group ( n = 13 ; 41.5 ± 19.9 years) or the interventional group ( n = 10 ; 44.9 ± 19.7 years). The surgical group underwent laparoscopic surgical ligation of the shunt alone or ligation of the shunt and splenic artery and/or vein. The interventional group underwent endovascular embolization using microcoils, detachable coils, and vascular plug. Results. All 23 patients received a one-step shunt closure, and their clinical symptoms were significantly improved within 3-month postprocedure and without recurrence during follow-up. The serum ammonia levels in both groups decreased after the procedure and dropped to normal level at 6- to 12-month postprocedure. Compared with baseline, the portal vein diameter in interventional group increased significantly at 3-, 6-, 12-, and 36-month postocclusion ( P = 0.01 for all). The procedure time was shorter in the interventional group ( 127.0 ± 43.2 minutes) than the surgical group ( 219.8 ± 56.7 minutes; P < 0.001 ). The intraoperative blood loss in the interventional group ( 32.0 ± 62.5  mL) was less than that in the surgical group ( 238.5 ± 396.9  mL; P = 0.001 ). Conclusion. Both surgical ligation and endovascular embolization are effective in the treatment of type II CEPS. Endovascular embolization has the advantages of shorter procedure time and less intraoperative blood loss. The ligation of the portosystemic shunt and splenic artery and vein is feasible with apparent safety, and it could avoid a second surgical treatment.

scholarly journals Association of increased erythrocyte osmotic resistance with haematological and histopathological findings in dogs with a congenital extrahepatic portosystemic shunt

2013 ◽  
Vol 82 (4) ◽  
pp. 393-398
Author(s):  
Kristína Řeháková ◽  
Ivana Uhríková ◽  
Leona Raušerová-Lexmaulová ◽  
Jana Lorenzová ◽  
Ladislav Stehlík ◽  
...  
Keyword(s):  
Osmotic Fragility ◽  
Portosystemic Shunt ◽  
Osmotic Resistance ◽  
Test Results ◽  
Cell Deformability ◽  
Histological Changes ◽  
Congenital Portosystemic Shunt ◽  
Congenital Extrahepatic Portosystemic Shunt ◽  
Healthy Dogs ◽  
Complete Blood Counts

The aim of the study was to investigate changes in erythrocyte osmotic resistance in relation to haematological and histological changes in dogs with a congenital portosystemic shunt. Osmotic fragility tests with complete blood counts and liver histological examinations were performed in 12 dogs with single extrahepatic portosystemic shunt confirmed by surgical exploration. Laboratory results were compared with those from 30 healthy dogs. Dogs with portosystemic shunt had a significantly increased erythrocyte osmotic resistance (P < 0.01) with 5%, 50% and 90% haemolysis corresponding to 0.45%, 0.35% and 0.30% NaCl solution, respectively. Statistical analyses revealed no correlation between haematological indicators and the osmotic fragility test results. Increased osmotic resistance was significantly associated with hepatic lipogranulomas. Based on these results, dogs with a congenital portosystemic shunt have a significantly increased erythrocyte osmotic resistance suggesting impaired red blood cell deformability. Osmotic resistance test that until now was not studied in canine hepatopathies seems to be independent of routinely performed haematological tests.

scholarly journals Born Again: Recurrent Hepatic Encephalopathy in an Adult without Cirrhosis

2019 ◽  
Vol 02 (01) ◽  
pp. 039-040
Author(s):  
Tom George ◽  
Sasidharan Rajesh ◽  
Cyriac Abby Philips
Keyword(s):  
Hepatic Encephalopathy ◽  
Systemic Circulation ◽  
Portosystemic Shunt ◽  
Type Ii ◽  
Adult Onset ◽  
Significant Clinical Improvement ◽  
Congenital Extrahepatic Portosystemic Shunt ◽  
Born Again

AbstractCongenital extrahepatic portosystemic shunt (CEPS) develops between the por-to-mesenteric and systemic veins. The splanchnic venous system drains directly to systemic circulation in this condition. We present a case of an adult onset Type II CEPS presenting with hepatic encephalopathy. The patient underwent PARTO (plug-assisted retrograde transvenous obliteration) and had a significant clinical improvement on subsequent follow-up. Our case highlights the importance of imaging and the role of an interventional radiologist in the management of the condition.

scholarly journals Congenital extrahepatic portosystemic shunt type II occluded with cardiac closure device

2021 ◽  
Vol 16 (12) ◽  
pp. 3802-3806
Author(s):  
Gisela Andrade ◽  
João Facas ◽  
Pedro Marques ◽  
Ana Nassauer Mónica ◽  
Paulo Donato
Keyword(s):  
Portosystemic Shunt ◽  
Closure Device ◽  
Type Ii ◽  
Congenital Extrahepatic Portosystemic Shunt
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