scholarly journals Pediatric Synovial Sarcoma in the Retropharyngeal Space: A Rare and Unusual Presentation

2015 ◽  
Vol 2015 ◽  
pp. 1-4
Author(s):  
Sanjay Vaid ◽  
Neelam Vaid ◽  
Sanjay Desai ◽  
Varada Vaze

Synovial sarcomas in the head and neck are extremely rare tumors, especially in the pediatric population. 3–5% of synovial sarcomas occur in the head and neck region displaying varied imaging and histopathological features resulting in frequent misdiagnosis. These tumors have a poor prognosis; hence early diagnosis and accurate classification based on imaging, histopathology, and immunohistochemistry are critical for prompt treatment. To the best of our knowledge, imaging findings of pediatric retropharyngeal lipomatous synovial sarcoma have not been reported to date in English medical literature. We report, for the first time, a rare case of retropharyngeal lipomatous synovial sarcoma in a ten-year-old child and discuss the case-specific imaging findings in our patient using magnetic resonance imaging and computed tomography.

2021 ◽  
Vol 11 (44) ◽  
pp. 174-180
Author(s):  
Ionut Tanase ◽  
Mihaela Neagu ◽  
George Dascalescu

Abstract BACKGROUND. Synovial sarcomas of the soft tissue are a particular type of sarcomas that rarely appear in the head and neck region. CASE REPORT AND COMMENTS. We present the case of a 27-year-old patient diagnosed in 2017 with soft palate biphasic synovial sarcoma who presented with recurrent microepistaxis, nasal obstruction, left cephalalgia and aural fullness in the left ear. The clinical examination showed a tumor with approximately 4/6 cm in diameter, covered with sero-sanguinolent secretions, pulsating in nature, completely obstructing the left choana. The surgical treatment consisted of complete removal of the tumor under endoscopic guidance with electrocauterization of the insertion area, without further postoperative radiotherapy. The histopathological aspect was suggestive for pleomorphic sarcoma, poorly differentiated, confirming the local recurrence of the tumor. The patient also presented lung metastasis from undifferentiated malignant tumor. CONCLUSION. The particularity of this case is represented by the extremely rare occurrence of synovial sarcoma in the head and neck region, especially at the level of the soft palate. Complete resection of the tumor with negative margins represent the mainstay of treatment, associated with adjuvant radiotherapy, with an important role in improving disease-specific survival.


2019 ◽  
Vol 52 (4) ◽  
pp. 268-271
Author(s):  
Pinar Gulmez Cakmak ◽  
Gülsüm Akgün Çağlayan ◽  
Furkan Ufuk

Abstract Primary extranodal lymphoma is defined as a lymphoma at a solitary extranodal site, with or without involvement of the lymph nodes. The clinical and radiological features of extranodal lymphoma have been documented in recent studies. In this pictorial essay, we reviewed imaging findings of extranodal lymphoma in the head and neck region.


2013 ◽  
Vol 4 (2) ◽  
pp. 86-88 ◽  
Author(s):  
Raza Hussain ◽  
Asif Loya ◽  
Arif Jamshed ◽  
Adeel Haider Tirmazi

ABSTRACT Synovial sarcomas of head and neck are very rare and account for only 3% of all sarcomas. Approximately 5% of synovial sarcomas arise in the head and neck region and hypopharynx and larynx are the most and least often affected anatomic sites respectively. We describe a rare case of primary hypopharyngeal synovial sarcoma in a young adult. How to cite this article Jamshed A, Loya A, Tirmazi AH, Hussain R. Synovial Cell Sarcoma of the Hypopharynx. Int J Head Neck Surg 2013;4(2):86-88.


2005 ◽  
Vol 103 (6) ◽  
pp. 1077-1080 ◽  
Author(s):  
Gary L. Gallia ◽  
Daniel M. Sciubba ◽  
Christine L. Hann ◽  
Siva P. Raman ◽  
William H. Westra ◽  
...  

✓ Synovial sarcoma is a soft-tissue lesion occurring predominantly in the extremities of young adults. Although the head and neck region is the second most common site of involvement, synovial sarcoma has rarely been reported in the paranasal sinus. The authors present a case of synovial sarcoma arising from the frontal sinus and review the literature of synovial sarcomas arising from the paranasal sinuses.


2015 ◽  
Vol 06 (04) ◽  
pp. 237-241
Author(s):  
Deepshikha Khanna ◽  
Virad Kumar ◽  
Vineet Narula ◽  
Ravi Meher ◽  
Nita Khurana ◽  
...  

2019 ◽  
Vol 11 (2) ◽  
pp. 116-117
Author(s):  
Anass Chaouki ◽  
Merzouqui B ◽  
Zouhair N ◽  
Beghdad M ◽  
Abada R ◽  
...  

Synovial sarcoma (SS) is a malignant neoplasm that arises from primitive pluripotential mesenchymal cells . It is a high-grade histological variety of sarcoma and it accounts for 7-10% of all soft tissue sarcomas. Head and neck locations represent only 0.7% to 10% of all cases. Primary parapharyngeal synovial sarcoma (PPSS) is rare representing only 0.5% of all tumors of the head and neck region. We describe through a clinical case the clinical, radiological and histological features of PPSS and we discuss its therapeutic management.


2021 ◽  
Vol 07 (03) ◽  
pp. e195-e198
Author(s):  
Sapna Dhiman ◽  
Sarita Negi ◽  
Sandeep Moudgil ◽  
Jagdeep S. Thakur ◽  
Ramesh K. Azad

Abstract Background Synovial sarcoma is an aggressive soft tissue cancer of extremities mainly and rare in head and neck region, whereas rarest in ethmoidal sinus as only three cases have been reported till date. Case Reports We managed two cases of synovial sarcoma who presented with nasal obstruction, epistaxis, and swelling around the nasofacial region. Endoscopic nasal biopsy and immunohistochemistry markers confirmed synovial sarcoma in both the cases. While one case was managed by surgery and chemoradiation, the second patient received two cycles of ifosfamide-based chemotherapy and succumbed after 6 weeks of diagnosis. Conclusion Head and neck sarcomas are aggressive and carry a poor prognosis. Surgical resection with postoperative radiotherapy is the standard treatment. However, they have a high risk of recurrence and hence aggressive management and close follow-up is warranted for the optimal outcome.


2005 ◽  
Vol 84 (5) ◽  
pp. 302-306 ◽  
Author(s):  
Frank O. Agada ◽  
Justin Murphy ◽  
Ravi Sharma ◽  
Laszlo Karsai ◽  
Nick D. Stafford

Synovial sarcoma is not common in the head and neck region. Because its histopathologic features are many and varied, it is often misdiagnosed. We report a case of biphasic synovial sarcoma of the posterior pharyngeal wall, and we discuss the clinical and pathologic features of this case.


2002 ◽  
Vol 81 (1) ◽  
pp. 36-39 ◽  
Author(s):  
Levent Saydam ◽  
Ahmet Kizilay ◽  
M. Tayyar Kalcioglu ◽  
Bulent Mizrak ◽  
Fatih Bulut

Synovial sarcoma is a malignancy not usually encountered in the head and neck region. We describe a case of synovial sarcoma of the posterior pharyngeal wall in a 14-year-old girl. The mass was completely excised via the transoral route. Postoperatively, the patient received irradiation to 60 Gy. At 40 months of follow-up, the patient remains disease-free.


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