scholarly journals Hereditary Gingival Fibromatosis: A Review and a Report of a Rare Case

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Hossein Aghili ◽  
Mahdjoube Goldani Moghadam
Keyword(s):  
Muscle Contraction ◽  
Female Patient ◽  
Orthognathic Surgery ◽  
Rare Case ◽  
Rare Condition ◽  
Chief Complaint ◽  
Growth Potential ◽  
Gingival Tissue ◽  
Growth Spurt ◽  
Gingival Fibromatosis

Hereditary gingival fibromatosis (HGF) is a rare condition which manifests itself by an enlarged gingival tissue covering teeth to various extents. The condition may occur isolated or as part of a syndrome. This paper presents a case of 9-year-old female patient suffering from HGF with chief complaint of mouth protrusion. Cephalometric findings showed severe mandibular deficiency and vertical maxillary excess. Patient exhibited perioral muscle contraction on mouth closing. After discussing the treatment possibilities with the patient and her parents, the decision was made to wait until growth potential decreases (following the adolescent growth spurt) and to correct the problem with orthognathic surgery.

scholarly journals The Autosomal Recessive Inheritance of Hereditary Gingival Fibromatosis

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Poulami Majumder ◽  
Vineet Nair ◽  
Malancha Mukherjee ◽  
Sujoy Ghosh ◽  
Subrata Kumar Dey
Keyword(s):  
Surgical Treatment ◽  
Medical History ◽  
Autosomal Recessive ◽  
Rare Condition ◽  
Autosomal Recessive Inheritance ◽  
Chief Complaint ◽  
Gingival Tissue ◽  
Recessive Inheritance ◽  
Inheritance Pattern ◽  
Gingival Fibromatosis

Hereditary gingival fibromatosis (HGF) is a rare condition which is marked by enlargement of gingival tissue that covers teeth to various extents leading to aesthetic disfigurement. This study presents a case of a 28-year-old female patient and 18-year-old male who belong to the same family suffering from HGF with chief complaint of overgrowing swelling gingiva. The presence of enlarged gingiva with the same eruption was found in their other family members with no concomitant drug or medical history, and the occurrence of HGF has been found in one generation of this family which may indicate the autosomal recessive inheritance pattern of HGF. Hereditary gingival fibromatosis is an idiopathic condition as its etiology is unknown and it was found to recur in some cases even after surgical treatment. Both patients underwent thorough oral prophylaxis and later surgical therapy to correct the deformity.

A Rare Case of Intra Mesenteric Dermoid Cyst

2021 ◽  
Vol 8 (05) ◽  
pp. 275-277
Author(s):  
Vikas Katiar ◽  
Kumar Vineet ◽  
Himanshu Singh ◽  
Sanjay Tripathi ◽  
Vikas Patel
Keyword(s):  
Case Report ◽  
Dermoid Cyst ◽  
Female Patient ◽  
Rare Case ◽  
Rare Condition ◽  
Epidermal Cells ◽  
Mild Pain ◽  
Glandular Cells

A dermoid cyst is a teratoma of a cystic nature which can occur wherever a teratoma can occur. Intra mesenteric dermoid cyst is rarest of rare case and even its incidence is not known. Here, we report a case of intra mesenteric dermoid cyst in 21 yr. old female patient who presented to us with complain of on & off mild pain in abdomen for last 2 years. Intra mesenteric dermoid cyst is a rare condition and when presented with symptoms, it should be operated upon for improving patient’s overall wellbeing. Dermoids belong to the group of congenital cystic tumours developing from an embryonic rest. Such tumours vary from those which contain only epidermal cells to those containing various dermal derivatives, such as glandular cells (sebaceous), and even hair and teeth. So, they vary from pure epidermoids to dermoids and then through the teratoid tumours to the teratomas. These tumours can arise wherever two ectodermal surfaces fuse together in the developing embryo when an ectodermal implant is retained deep in the surface.”1 Intra mesenteric dermoid is very rare and no previous case report regarding intra mesenteric dermoid was found.

scholarly journals Hereditary Gingival Fibromatosis with Distinctive Facies

2012 ◽  
Vol 13 (6) ◽  
pp. 892-896 ◽  
Author(s):  
Sunkara Shree Ramalinga Prasad ◽  
Chitturi Radharani ◽  
SV Kiran Kumar ◽  
Soumya Sinha
Keyword(s):  
Family History ◽  
Female Patient ◽  
Autosomal Dominant ◽  
Chief Complaint ◽  
Oral Manifestations ◽  
Autosomal Dominant Disorder ◽  
Rare Type ◽  
Gingival Enlargement ◽  
Gingival Fibromatosis ◽  
Maxilla And Mandible

ABSTRACT Hereditary gingival enlargement also known as gingivitis or familial elephantiasis is a rare type of gingival enlargement. It appears as an isolated autosomal dominant disorder or maybe associated with other conditions. Oral manifestations may vary from minimal involvement of only tuberosity area and the buccal gingiva around the lower molars to a generalized enlargement inhibiting eruption of the teeth. This paper discusses the case of a 13-year-old female patient with distinctive facial characteristics who presented to the department with a chief complaint of swollen gums since 1 year. She had severe diffuse gingival enlargement of the maxilla and mandible. Diagnosis was made based upon clinical examination and family history. Quadrant wise internal bevel gingivectomy procedure was done for the patient to restore her functional and esthetic needs. How to cite this article Prasad SSR, Radharani C, Sinha S, Kumar SVK. Hereditary Gingival Fibromatosis with Distinctive Facies. J Contemp Dent Pract 2012;13(6):892-896.

A Rare Case of non Syndromic Congenital Idiopathic Gingival Fibromatosis: Electrosurgical Management

2020 ◽  
Vol 44 (5) ◽  
pp. 352-355
Author(s):  
Parul Singhal ◽  
Ritu Namdev ◽  
Heena Sarangal ◽  
Saurabh Narang
Keyword(s):  
Case Report ◽  
Rare Case ◽  
Primary Teeth ◽  
Rare Condition ◽  
Permanent Dentition ◽  
Heterogeneous Condition ◽  
Hyperplastic Tissue ◽  
Gingival Fibromatosis ◽  
One Year ◽  
Excised Tissue

Idiopathic gingival fibromatosis (IGF) is a rare, genetically heterogeneous condition that is usually a part of syndrome or, rarely, an isolated disorder. It is characterized by a slowly progressive, non hemorrhagic, fibrous enlargement of keratinized gingiva which usually begins at the time of eruption of permanent dentition, however very few cases involving the primary teeth have been described in literature. Congenital gingival fibromatosis is very rare condition in which the gingival tissues become thickened and erupting teeth remain submerged beneath hyperplastic tissue masses. This case report discusses the rare case of congenital non syndromic idiopathic gingival fibromatosis in a two year old boy who reported with absence of teeth and incompetent lips. Gingivectomy was done using modified microdissection electrocautery needle to remove the excess gingival tissues. Excised tissue has been examined histologically. The patient was followed up for a period of one year and no recurrence was observed.

scholarly journals Conservative Treatment of Idiopathic Spontaneus Pneumoperitoneum

2021 ◽  
Vol 4 (7) ◽  
pp. 01-03
Author(s):  
Marina Gabrielle Epstein ◽  
Vladimir Schraibman ◽  
Luis Roberto Manzione Nadal ◽  
Gabriel Maccapani ◽  
Marília Fernandes ◽  
...  
Keyword(s):  
Conservative Treatment ◽  
Female Patient ◽  
Rare Case ◽  
Incidental Finding ◽  
Rare Condition

Pneumoperitoneum is often caused by perforation of hollow viscera, but when an etiology is not identified, it is said to be idiopathic. It is considered a rare condition, as in the last 30 years, just over 20 cases have been described. We present a rare case of an incidental finding of a pneumoperitoneum in a 36 years old female patient.

scholarly journals Unilateral Acquired Posterior Maxillary Mandibular Syngnathia

2016 ◽  
Vol 24 (3) ◽  
pp. 161-165
Author(s):  
Abhishek Vijay Sahu ◽  
Kamalika Purkayastha Roy ◽  
Niva Kashyap
Keyword(s):  
Case Report ◽  
Female Patient ◽  
Rare Case ◽  
Myositis Ossificans ◽  
Case Series ◽  
Rare Condition ◽  
International Literature ◽  
Bony Fusion ◽  
Maxilla And Mandible ◽  
Bony Ankylosis

Introduction: Congenital bony fusion of the maxilla and mandible, especially as an isolated occurrence, is a rare condition while acquired fusion being even rarer. Case report: A rare case of a 32 year old female patient with acquired unilateral bony fusion between the zygomatic arch of maxilla and ramus of mandible is reported. Discussion: Forty one cases of syngnathia has been reported in the international literature from 1936 to 2009, of which 39 cases are congenital and two were acquired, case 1 probably as a result of a fibrotic tubed pedicle and in case 2 from myositis ossificans. According to several case series, bony ankylosis of the mandible and maxilla has also been found to occur in 30%-43% of cases of NOMA.

scholarly journals A rare case of eight multiple primary malignant neoplasms in a female patient: A case report and review of the literature

2014 ◽  
Vol 9 (2) ◽  
pp. 587-590 ◽  
Author(s):  
JIEMIN ZHAO ◽  
YAN TAN ◽  
YUGANG WU ◽  
WEI ZHAO ◽  
JUN WU ◽  
...  
Keyword(s):  
Case Report ◽  
Female Patient ◽  
Rare Case ◽  
Malignant Neoplasms ◽  
Review Of The Literature ◽  
Multiple Primary

scholarly journals Refractory Dry Eye Syndrome after Transconjunctival Excision of the Palpebral Lobe of the Lacrimal Gland

Medicina ◽  
2021 ◽  
Vol 57 (6) ◽  
pp. 608
Author(s):  
Yong-Jae Lee ◽  
Han-Sol Choi ◽  
Seong-Jun Park ◽  
Hae-Jung Sun ◽  
Sun-Young Jang
Keyword(s):  
Female Patient ◽  
Dry Eye ◽  
Lacrimal Gland ◽  
Medical Center ◽  
Chief Complaint ◽  
Incisional Biopsy ◽  
Lacrimal Glands ◽  
Palpable Mass ◽  
Tear Secretion ◽  
Palpebral Lobe

The aim of the present study was to report two cases of refractory dry eye syndrome (DES) after transconjunctival excision of the palpebral lobe of the lacrimal gland. A 25-year-old female patient with a chief complaint of a palpable mass in both upper eyelids visited our medical center. Preoperative orbital computer tomography showed high-attenuation lesions in both lacrimal glands. Incisional biopsy of the lacrimal gland palpebral lobe via transconjunctival incision was performed in January 2019. At 1 month after the biopsy, a lack of tears and persistent corneal erosions were found in both eyes. Artificial tears, punctal occlusion, autologous serum eye drops, and therapeutic contact lenses were applied in an attempt to control the dry eye symptoms. The patient continues to suffer from intractable DES at 2.5 years after the procedure. The second case involved a 52-year-old female patient who visited our medical center with a chief complaint of a palpable mass in both upper eyelids. Bilateral orbital tumors were diagnosed with preoperative magnetic resonance imaging. An incisional biopsy of the lacrimal gland was performed. Immunoglobulin G4-related dacryoadenitis was confirmed through lacrimal palpebral lobe incisional biopsy. Intractable DES and corneal erosion of her left eye persisted thereafter. A transconjunctival incision is an effective approach for minimizing postoperative scars and is suitable for the biopsy of tumors that are visible through the conjunctiva. After a biopsy of the palpebral lobe of the main lacrimal glands, the secretion of reflex tears decreases due to damage to the secreting ducts of the main lacrimal glands. However, total tear secretion can be maintained by basal tear secretion from the accessory lacrimal glands. In this report, we describe two cases of refractory DES due to decreased total tear secretion, although only the palpebral lobes of the main lacrimal glands were biopsied.

scholarly journals Hypertrophy of the abductor hallucis muscle: A case report and review of the literature

2017 ◽  
Vol 5 ◽  
pp. 2050313X1772763 ◽  
Author(s):  
Toshinori Kurashige
Keyword(s):  
Rare Case ◽  
Muscle Hypertrophy ◽  
Pathological Condition ◽  
Rare Condition ◽  
Review Of The Literature ◽  
Resonance Imaging ◽  
Abductor Hallucis ◽  
Medial Plantar Nerve ◽  
Abductor Hallucis Muscle ◽  
Entrapment Syndromes

Objectives: Muscle hypertrophy is a relatively rare condition that may cause nerve entrapment syndromes. We report the case of a 14-year-old girl with unilateral hypertrophy of the abductor hallucis muscle with entrapment of the medial plantar nerve and review the literature. Methods: Computed tomography and magnetic resonance imaging revealed unilateral hypertrophy of the abductor hallucis muscle. Results: Two injections of steroid and lidocaine at the point of tenderness resulted in resolution of the pain. Conclusions: We report a rare case of hypertrophy of the abductor hallucis muscle considered with entrapment of the medial plantar nerve. Treatment of this condition should be selected according to the pathological condition of each patient.

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