scholarly journals Cochlear Implantation after Bacterial Meningitis in Infants Younger Than 9 Months

2011 ◽  
Vol 2011 ◽  
pp. 1-9 ◽  
Author(s):  
B. Y. Roukema ◽  
M. C. Van Loon ◽  
C. Smits ◽  
C. F. Smit ◽  
S. T. Goverts ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Bacterial Meningitis ◽  
Cochlear Implants ◽  
Cochlear Implantation ◽  
Speech Intelligibility ◽  
Pneumococcal Meningitis ◽  
Profound Hearing Loss ◽  
Young Infants ◽  
Key Points ◽  
Auditory Performance

Objective. To describe the audiological, anesthesiological, and surgical key points of cochlear implantation after bacterial meningitis in very young infants.Material and Methods. Between 2005 and 2010, 4 patients received 7 cochlear implants before the age of 9 months (range 4–8 months) because of profound hearing loss after pneumococcal meningitis.Results. Full electrode insertions were achieved in all operated ears. The audiological and linguistic outcome varied considerably, with categories of auditory performance (CAP) scores between 3 and 6, and speech intelligibility rating (SIR) scores between 0 and 5. The audiological, anesthesiological, and surgical issues that apply in this patient group are discussed.Conclusion. Cochlear implantation in very young postmeningitic infants is challenging due to their young age, sequelae of meningitis, and the risk of cochlear obliteration. A swift diagnostic workup is essential, specific audiological, anesthesiological, and surgical considerations apply, and the outcome is variable even in successful implantations.

Outcome of Cochlear Implantation in Postmeningitis Profound Sensorineural Hearing Loss at Rajavithi Hospital

2021 ◽  
Vol 104 (2) ◽  
pp. 260-263
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Cochlear Implantation ◽  
Sensorineural Hearing ◽  
Preoperative Imaging ◽  
Profound Hearing Loss ◽  
Language Status ◽  
Auditory Performance ◽  
Electrode Insertion ◽  
One Year

Background: Bacterial meningitis is one of the major factors in the etiology of acquired sensorineural hearing loss in children and adults. Cochlear implantation in these patients is challenging because of inner ear ossification and fibrosis, and this procedure sometimes achieves poorer outcomes in this scenario than with other causes of sensorineural hearing loss. There has been little research into the factors affecting the outcomes of this procedure. Objective: To evaluate the outcomes of cochlear implantation in patients with postmeningitis profound sensorineural hearing loss and to evaluate the factors that affect the results. Materials and Methods: A retrospective review was conducted of thirty patients who were diagnosed with post meningitis profound hearing loss and underwent cochlear implantation at Rajavithi Hospital between 2001 and 2016. Preoperative language status, duration of deafness, preoperative imaging, and degree of electrode insertion were recorded. Categories of auditory performance-II test (CAP-II) was evaluated in all cases, one year postoperative. Results: Thirty postmeningitis deafness patients underwent cochlear implantation. The median age at diagnosis of meningitis and age at implantation were 41 years (range 1 to 75) and 49.50 years (range 3 to 75), respectively. The median duration of deafness was 12 months (range 4 to 300), and the overall mean CAP-II at one year after surgery was 5.47±2.21. The postlinguistic group had a significantly higher CAP-II score than the prelinguistic one (p=0.006). Electrodes were successfully totally inserted in 19 patients (63.3%) and partially inserted in 11 (36.7%). The average CAP-II score in the group with fully-inserted electrodes was significantly higher than in the group with partially-inserted electrodes (p=0.045). There was no correlation between CAP-II score and age at meningitis diagnosis (p=0.069), age at time of surgery (p=0.105), duration of deafness (p=0.506), or preoperative CT (p=0.228) or MRI abnormality (p=0.078). Conclusion: Cochlear implantation in patients with postmeningitis profound hearing loss had high success rates and favorable outcomes. Preoperative language status and degree of electrode insertion were factors that affected auditory performance results. Keywords: Cochlear implantation, Postmeningitis hearing loss, Sensorineural hearing loss, Meningitis, Rajavithi Hospital

Current Practices in Pediatric Cochlear Implantation

2009 ◽  
Vol 19 (1) ◽  
pp. 32-42 ◽  
Author(s):  
Tamala S. Bradham ◽  
Geneine Snell ◽  
David Haynes
Keyword(s):  
Hearing Loss ◽  
Cochlear Implants ◽  
Cochlear Implantation ◽  
Healthcare Providers ◽  
Interdisciplinary Teams ◽  
Profound Hearing Loss ◽  
Comprehensive Management ◽  
Technological Advances ◽  
Management Protocol ◽  
Professional Guidelines

Abstract Technological advances, specifically cochlear implants, have significantly impacted the treatment of children with severe to profound hearing loss. There are, however, very few professional guidelines or resources providing direction for hearing healthcare providers who are serving children with cochlear implants. The following article discusses a comprehensive management protocol for interdisciplinary teams providing cochlear implant services for children.

scholarly journals Factors affecting audiological performance and speech intelligibility in prelingually deaf children after cochlear implantation: a study

2019 ◽  
Vol 5 (4) ◽  
pp. 1035 ◽  
Author(s):  
Abhipsa Hota
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Cochlear Implantation ◽  
Speech Intelligibility ◽  
Deaf Children ◽  
Auditory Deprivation ◽  
Factors Affecting ◽  
Negative Relation ◽  
Auditory Performance ◽  
Prelingually Deaf

<p class="abstract"><strong>Background:</strong> The primary aim is to understand the factors affecting the audiological, speech and language outcome in prelingually deaf children, with bilateral severe to profound sensorineural hearing loss, who have undergone cochlear implantation.</p><p class="abstract"><strong>Methods:</strong> 40 prelingually deaf children, with bilateral severe to profound sensorineural hearing loss, who have undergone cochlear implantation were enrolled. Auditory performance and speech intelligibility was gauged by revised categories of auditory performance (CAP) score and speech intelligibility rating (SIR) respectively, preoperatively and at 3 months, 6 months and 1 year post cochlear implantation. These values were analysed using statistical package for social sciences with respect to duration of auditory deprivation, duration of use of hearing aid prior to cochlear implantation, duration of auditory verbal therapy prior to cochlear implantation and age of child at cochlear implantation.  </p><p class="abstract"><strong>Results:</strong> There is a negative relation between CAP and duration of auditory deprivation at 6 months and 1 year post cochlear implantation. Also, negative relation is seen between CAP and age of child at cochlear implantation at 6 months and 1 year post cochlear implantation. There is a negative relation between SIR and duration of auditory deprivation at 6 months and 1 year post cochlear implantation. Also, negative relation is seen between SIR score and age of child at cochlear implantation at 3 months, 6 months and 1 year post cochlear implantation.</p><p class="abstract"><strong>Conclusions:</strong> Lesser the auditory deprivation and younger the child at cochlear implantation, better is the audiological performance and speech intelligibility post cochlear implantation.</p><p> </p>

Contemporary Considerations for Cochlear Implantation for Children With Multiple Disabilities

2009 ◽  
Vol 19 (2) ◽  
pp. 69-74 ◽  
Author(s):  
Susan Waltzman
Keyword(s):  
Hearing Loss ◽  
Cochlear Implant ◽  
Cochlear Implants ◽  
Cochlear Implantation ◽  
Multiple Disabilities ◽  
Profound Hearing Loss ◽  
Contemporary Management

Abstract Due to advances in cochlear implant technology and the remarkable outcomes often achieved by persons with severe to profound hearing loss, cochlear implant candidacy criteria has expanded since the first children were implanted almost twenty years ago. Evidence of this can be seen in the increased willingness to provide cochlear implants for children with multiple disabilities. Over the last decade, several reports have appeared in the peer-reviewed literature describing cochlear implant outcomes of children with multiple disabilities. This paper will summarize those reports, discuss realistic expectations of implantation for children with multiple disabilities, and describe contemporary management protocols for the otologic, audiologic, and rehabilitative management of children with multiple disabilities.

scholarly journals Effect of age at cochlear implantation on speech and auditory performance

2021 ◽  
Vol 7 (2) ◽  
pp. 229
Author(s):  
Mohammed Iftekharul Alam ◽  
A. K. M. Asaduzzaman ◽  
Mohammad K. Hossain ◽  
M. Belal Hossain ◽  
Tasnia Mahmud
Keyword(s):  
Hearing Loss ◽  
Language Impairment ◽  
Cochlear Implantation ◽  
Speech Intelligibility ◽  
Neck Surgery ◽  
Military Hospital ◽  
Retrospective Clinical Study ◽  
Auditory Performance ◽  
The Mean

<p class="abstract"><strong>Background:</strong> Cochlear implants (CI) are currently widely accepted as treatment for patients with severe bilateral hearing loss. The outcomes of cochlear implantation among post lingual and crossover patients measuring surgical and functional outcomes and identifying areas which require further attention or improvement.</p><p class="abstract"><strong>Methods:</strong> This is retrospective clinical study was performed in a total of 80 children purposively screened from the patients who attended the outpatient clinic with complaints of hearing, speech or language impairment. The study group consisted those children who fit into the candidacy norms for cochlear implantation at the Department of ENT and Head-Neck Surgery, Combined Military Hospital, Dhaka from January 2017 to June 2019. Children with bilateral severe to profound sensori-neural hearing loss, age less than 5 years and prelingual deafness was included in this study.  </p><p class="abstract"><strong>Results:</strong> Mean categorical auditory performance (CAP) and speech intelligibility rating (SIR) at 6 month and 12 month were statistically significant (p&lt;0.05) compare with at 3 month. The mean post-operative CAP score was found significantly increased at 6, 12 and 24 month follow up age ≤3 years than &gt;3 years (p&lt;0.05). The mean post-operative SIR score was found significantly increased at 6, 12 and 24 month follow up in children age ≤3 years than &gt;3 years (p&lt;0.05).</p><p class="abstract"><strong>Conclusions:</strong> The majority of implanted have significantly gained auditory improvement as shown by the CAP and SIR scores in both group. Comparison between age group CAP and SIR score was significantly increased when children age &lt;3 years than &gt;3 years.</p>

scholarly journals Expansion of indications for cochlear implantation in the Russian Federation

2020 ◽  
Vol 19 (6) ◽  
pp. 72-77
Author(s):  
Ya. L. Shcherbakova ◽  
◽  
S. M. Megrelishvili ◽  
V. E. Kuzovkov ◽  
S. A. Karpishchenko ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Speech Intelligibility ◽  
Binaural Hearing ◽  
Profound Hearing Loss ◽  
Special Groups ◽  
Patient Groups ◽  
The Moment ◽  
Special Patient

Profound hearing loss makes it difficult for a person to fully integrate into society. Cochlear implantation is rightfully considered a universal and an effective method of rehabilitation of patients with severe and profound hearing loss. The advantages of binaural hearing are well known; the advantages of bilateral cochlear implantation over monolateral implantation are undeniable, due to the restoration of all binaural hearing effects. At the moment, the relevance of simultaneous cochlear implantation, especially among children, and its benefits compared with sequential implantation are being discussed. It is known that there are special groups of patients among patients with hearing loss; they are either unrehabilitated at all or rehabilitation measures for which are ineffective. Special patient groups include patients with unilateral acquired or congenital deafness, asymmetric and residual hearing loss. Patients in these groups often complain of poor speech intelligibility, especially against a background of noise, inability to localize the source of sound, one-sided or two-sided tinnitus, and, as a result, a deterioration in the quality of life. All abovementioned makes us think about the need to revise the indications for cochlear implantation and study this issue in detail.

scholarly journals Detailed clinical features and genotype–phenotype correlation in an OTOF-related hearing loss cohort in Japan

2021 ◽  
Author(s):  
Yoh-ichiro Iwasa ◽  
Shin-ya Nishio ◽  
Hidekane Yoishimura ◽  
Akiko Sugaya ◽  
Yuko Kataoka ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Clinical Characteristics ◽  
Clinical Information ◽  
Auditory Neuropathy ◽  
Hearing Level ◽  
Phenotype Correlation ◽  
Profound Hearing Loss ◽  
Genotype Phenotype Correlation ◽  
Auditory Performance

AbstractMutations in the OTOF gene are a common cause of hereditary hearing loss and the main cause of auditory neuropathy spectrum disorder (ANSD). Although it is reported that most of the patients with OTOF mutations have stable, congenital or prelingual onset severe-to-profound hearing loss, some patients show atypical clinical phenotypes, and the genotype–phenotype correlation in patients with OTOF mutations is not yet fully understood. In this study, we aimed to reveal detailed clinical characteristics of OTOF-related hearing loss patients and the genotype–phenotype correlation. Detailed clinical information was available for 64 patients in our database who were diagnosed with OTOF-related hearing loss. As reported previously, most of the patients (90.6%) showed a “typical” phenotype; prelingual and severe-to-profound hearing loss. Forty-seven patients (73.4%) underwent cochlear implantation surgery and showed successful outcomes; approximately 85–90% of the patients showed a hearing level of 20–39 dB with cochlear implant and a Categories of Auditory Performance (CAP) scale level 6 or better. Although truncating mutations and p.Arg1939Gln were clearly related to severe phenotype, almost half of the patients with one or more non-truncating mutations showed mild-to-moderate hearing loss. Notably, patients with p.His513Arg, p.Ile1573Thr and p.Glu1910Lys showed “true” auditory neuropathy-like clinical characteristics. In this study, we have clarified genotype–phenotype correlation and efficacy of cochlear implantation for OTOF-related hearing loss patients in the biggest cohort studied to date. We believe that the clinical characteristics and genotype–phenotype correlation found in this study will support preoperative counseling and appropriate intervention for OTOF-related hearing loss patients.

Detailed Clinical Features and Genotype-Phenotype Correlation in an OTOF-Related Hearing Loss Cohort in Japan

2021 ◽  
Author(s):  
Yoh-ichiro Iwasa ◽  
Shin-ya Nishio ◽  
Hidekane Yoishimura ◽  
Akiko Sugaya ◽  
Yuko Kataoka ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Clinical Characteristics ◽  
Clinical Information ◽  
Auditory Neuropathy ◽  
Hearing Level ◽  
Phenotype Correlation ◽  
Profound Hearing Loss ◽  
Genotype Phenotype Correlation ◽  
Auditory Performance

Abstract OTOF is one of the most frequent causes of hereditary hearing loss and a main cause of auditory neuropathy spectrum disorder (ANSD). Although it is reported that most of the patients with OTOF mutations have stable, congenital or prelingual onset severe-to-profound hearing loss, some patients show atypical clinical phenotypes, and the genotype-phenotype correlation in the patients with OTOF mutations is not yet fully understood. In this study, we aimed to reveal detailed clinical characteristics of OTOF-related hearing loss patients and the genotype-phenotype correlation. Detailed clinical information was available for 65 patients in our database who were diagnosed with OTOF-related hearing loss. As reported previously, most of the patients (90.8%) showed a “typical” phenotype, prelingual and severe-to-profound hearing loss. Forty-seven patients (72.3%) underwent cochlear implantation surgery and showed successful outcomes; approximately 85-90% of the patients showed a hearing level of 20-39dB with cochlear implant and a CAP scale (Categories of Auditory Performance) level 6 or better. Although truncating mutations and p.R1939Q were clearly related to severe phenotype, almost half of patients with one or more non-truncating mutations showed mild-to-moderate hearing loss. Notably, patients with p.H513R, p.I1573T and p.E1910K showed “true” auditory neuropathy-like clinical characteristics. In this study, we have clarified genotype-phenotype correlation and efficacy of cochlear implantation for OTOF-related hearing loss patients in the biggest cohort studied to date. We believe that the clinical characteristics and genotype-phenotype correlation found in this study will support preoperative counseling and appropriate intervention for OTOF-related hearing loss patients.

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