scholarly journals AIRP Best Cases in Radiologic-Pathologic Correlation: Type 2 Congenital Cystic Adenomatoid Malformation (Type 2 Congenital Pulmonary Airway Malformation)

Radiographics ◽  
2011 ◽  
Vol 31 (3) ◽  
pp. 743-748 ◽  
Author(s):  
Sarah W. Kao ◽  
Craig W. Zuppan ◽  
Lionel W. Young
Keyword(s):  
Congenital Cystic Adenomatoid Malformation ◽  
Congenital Pulmonary Airway Malformation ◽  
Pathologic Correlation ◽  
Cystic Adenomatoid Malformation ◽  
Pulmonary Airway

Congenital Pulmonary Airway Malformation (Congenital Cystic Adenomatoid Malformation) with Multiple Extrapulmonary Anomalies: Autopsy Report of a Fetus at 19 Weeks of Gestation

2004 ◽  
Vol 7 (6) ◽  
pp. 661-666 ◽  
Author(s):  
Truc T. Pham ◽  
Kurt Benirschke ◽  
Eliezer Masliah ◽  
J. Thomas Stocker ◽  
Eunhee S. Yi
Keyword(s):  
Surfactant Protein ◽  
Maternal Serum ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Normal Female ◽  
Cytokeratin 20 ◽  
Congenital Pulmonary Airway Malformation ◽  
Thyroid Transcription Factor 1 ◽  
Cystic Adenomatoid Malformation ◽  
Estimated Risk ◽  
Pulmonary Airway

Congenital pulmonary airway malformation, or congenital cystic adenomatoid malformation, is postulated to be a disorder of pulmonary airway morphogenesis and encompasses 5 different types with distinct levels or stages of tracheobronchial development. We present a unique case of type 2 congenital pulmonary airway malformation with a previously undocumented combination of multiple extrapulmonary anomalies, featuring ipsilateral multicystic renal dysgenesis, contralateral renal agenesis, and ovarian germ cell hypoplasia, diagnosed in a 19-week gestational age fetus by autopsy. Epithelial cells comprising the pulmonary lesions were positive for thyroid transcription factor-1, surfactant protein-B, and cytokeratin-7 but negative for cytokeratin-20 immunostainings, with the pattern seen in normal terminal bronchioles. Chromosomal analysis showed a normal female karyotype, despite a high estimated risk for Down syndrome suggested by the low maternal serum α-fetoprotein level.

scholarly journals It is not pneumothorax: Multicystic lung lesion in a six-year-old child

2016 ◽  
Vol 26 (2) ◽  
pp. 121-124
Author(s):  
Eman Sobh ◽  
Amira Bahour ◽  
Shady Elia Anis
Keyword(s):  
Surgical Resection ◽  
Lung Development ◽  
Lung Lesion ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Congenital Pulmonary Airway Malformation ◽  
Cystic Lung ◽  
Cystic Adenomatoid Malformation ◽  
Pulmonary Airway ◽  
Cystic Lung Lesion

Congenital cystic adenomatoid malformation (CCAM) – recently reported as congenital pulmonary airway malformation – is a rare abnormality of lung development. We present a case of a six-year-old child having a cystic lung lesion that proved to be CCAM after surgical resection. The child is performing well on follow-up.

Prenatal Diagnosis and Postnatal Management of Congenital Pulmonary Airway Malformation

2017 ◽  
Vol 8 (2) ◽  
pp. 89-92
Author(s):  
Rema Nambiar ◽  
Dinesh Nayak ◽  
Krupa H Shah ◽  
Shashikala K Bhat
Keyword(s):  
Prenatal Diagnosis ◽  
Lung Lesion ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Congenital Pulmonary Airway Malformation ◽  
Diagnostic Features ◽  
Postnatal Management ◽  
Mediastinal Shift ◽  
Exact Etiology ◽  
Threatened Preterm Labor ◽  
Pulmonary Airway

ABSTRACT Congenital pulmonary airway malformation (CPAM) is a rare developmental lung abnormality. It is also referred as a congenital cystic adenomatoid malformation. The exact etiology is not known yet. The majority of cases are detected during targeted prenatal scan or within 2 years of the birth. Here, we report a case of CPAM type II diagnosed at 23 weeks of gestation, the key diagnostic features of which were mediastinal shift and lung lesion. The fetus had transient polyhydramnios and pericardial effusion. Glucocorticoids were administered for threatened preterm labor and CPAM. Healthy neonate was delivered at term without any immediate neonatal complications. How to cite this article Bhat SK, Nambiar R, Nayak D, Shah KH. Prenatal Diagnosis and Postnatal Management of Congenital Pulmonary Airway Malformation. Int J Infertil Fetal Med 2017;8(2):89-92.

scholarly journals Congenital Cystic Adenomatoid Malformation Of The Lung: A Case Report And Review Of The Literature

2015 ◽  
Vol 8 (2) ◽  
pp. 160-163
Author(s):  
Doroteya V. Malinova ◽  
Penka L. Kolova ◽  
Radoslav S. Radev
Keyword(s):  
Lung Development ◽  
Incidental Finding ◽  
Ct Scanning ◽  
Final Diagnosis ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Pulmonary Infections ◽  
Cystic Adenomatoid Malformation ◽  
Clinical Presentations ◽  
The Right

Summary Congenital cystic adenomatoid malformation (CCAM) is a rare abnormality of lung development. It was classified into 5 types by Stocker in 2002 and is also known under the name of congenital pulmonary airway malformation (CPAM). Cases are typically identified prenatally by routine ultrasonography screening. CCAM may present in the older child and adult as an incidental finding. The case presented is of a 21-year-old male patient who suffered from pulmonary infections with a recurrent productive cough 3-4 times the last 4 years. CT scanning of the thorax showed multiple cystic lesions in the right middle and lower lobes. The areas with the lesions were resected. The macroscopic and histological findings were typical for congenital cystic adenomatoid malformation type 2, which was the final diagnosis. Clinical presentations and prognosis depend on the type of lesion and its sequelae. The diagnosis is confirmed histologically.

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