scholarly journals Can Dynamic MRI Depict Change in Thoracic Function after Operation for Thoracic Insufficiency Syndrome?

Radiology ◽  
2019 ◽  
Vol 292 (1) ◽  
pp. 214-215
Author(s):  
Harriet J. Paltiel
Keyword(s):  
Dynamic Mri ◽  
Thoracic Insufficiency Syndrome ◽  
Insufficiency Syndrome

Assessing Regional Ventilatory Function in Thoracic Insufficiency Syndrome Patients via Dynamic MRI

2021 ◽  
Author(s):  
Yubing Tong ◽  
Jayaram K. Udupa ◽  
Joseph M. McDonough ◽  
Caiyun Wu ◽  
Changjian Sun ◽  
...  
Keyword(s):  
Dynamic Mri ◽  
Ventilatory Function ◽  
Thoracic Insufficiency Syndrome ◽  
Insufficiency Syndrome

The Effect of Opening Wedge Thoracostomy on Thoracic Insufficiency Syndrome Associated with Fused Ribs and Congenital Scoliosis

2004 ◽  
Vol 86 (8) ◽  
pp. 1659-1674 ◽  
Author(s):  
Robert M. Campbell ◽  
Melvin D. Smith ◽  
Thomas C. Mayes ◽  
John A. Mangos ◽  
Donna B. Willey-Courand ◽  
...  
Keyword(s):  
Congenital Scoliosis ◽  
Opening Wedge ◽  
Thoracic Insufficiency Syndrome ◽  
Insufficiency Syndrome

Effects on Lung Function of Multiple Expansion Thoracoplasty in Children With Thoracic Insufficiency Syndrome: A Longitudinal Study

Spine ◽  
2006 ◽  
Vol 31 (3) ◽  
pp. 284-290 ◽  
Author(s):  
Etsuro K. Motoyama ◽  
Vincent F. Deeney ◽  
Gavin F. Fine ◽  
Charles I. Yang ◽  
Rebecca L. Mutich ◽  
...  
Keyword(s):  
Longitudinal Study ◽  
Lung Function ◽  
Thoracic Insufficiency Syndrome ◽  
Expansion Thoracoplasty ◽  
Insufficiency Syndrome

Neurosurgical management of symptomatic thoracic spinal ossification in a patient with fibrodysplasia ossificans progressiva

2012 ◽  
Vol 16 (3) ◽  
pp. 285-288 ◽  
Author(s):  
Bartosz T. Grobelny ◽  
David Rubin ◽  
Peter Fleischut ◽  
Elayna Rubens ◽  
Patricia Fogarty Mack ◽  
...  
Keyword(s):  
Soft Tissues ◽  
Genetic Disorder ◽  
Fibrodysplasia Ossificans Progressiva ◽  
Anesthetic Technique ◽  
Minor Trauma ◽  
Thoracic Insufficiency Syndrome ◽  
Canal Stenosis ◽  
Thoracic Spinal ◽  
Muscle Tissues ◽  
Insufficiency Syndrome

Fibrodysplasia ossificans progressiva (FOP) is a rare genetic disorder characterized by heterotopic ossification of soft connective and muscle tissues, often as the result of minor trauma. The sequelae include joint fusion, accumulation of calcified foci within soft tissues, thoracic insufficiency syndrome, and progressive immobility. The authors report on a patient with FOP who developed severe spinal canal stenosis in the thoracic spine causing substantial myelopathy. He underwent a thoracic laminectomy and resection of a large posterior osteophyte. Unique considerations are required in treating patients with FOP, including steroid administration to prevent ossification and anesthetic technique. The nuances of neurosurgical and medical management as they pertain to this disease are discussed.

Sign in / Sign up

Export Citation Format

Share Document