The Right Ventricular Infundibulum in Ebstein's Anomaly of the Tricuspid Valve

Radiology ◽  
1967 ◽  
Vol 89 (4) ◽  
pp. 694-700 ◽  
Author(s):  
Larry P. Elliott ◽  
Alexis F. Hartmann
Keyword(s):  
Right Ventricular ◽  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
The Right

Ebstein’s Anomaly

2007 ◽  
Vol 26 (3) ◽  
pp. 197-208 ◽  
Author(s):  
Sarah Pashia
Keyword(s):  
Heart Failure ◽  
Tricuspid Valve ◽  
Congenital Heart ◽  
Clinical Presentation ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Clinical Presentations ◽  
Wide Range ◽  
Pathologic Findings ◽  
The Right

EBSTEIN’S ANOMALY IS A RARE congenital heart defect characterized by displacement of the tricuspid valve leaflets into the right ventricle.1The defect was first described by Wilhelm Ebstein in 1866.2This anomaly of the tricuspid valve causes the right atrium to thin and become enlarged, resulting in a wide range of clinical presentations.3Clinical presentation depends on the severity of the pathologic findings, which vary considerably from patient to patient. Some infants may present with cyanosis, respiratory distress, heart failure, and even death, whereas others may not present with mild symptoms until adolescence or adulthood.

Cor triatriatum dexter masquerading as Ebstein's anomaly

2011 ◽  
Vol 21 (3) ◽  
pp. 354-356 ◽  
Author(s):  
Souheir Salam ◽  
David Gallacher ◽  
Orhan Uzun
Keyword(s):  
Tricuspid Valve ◽  
Transthoracic Echocardiography ◽  
Right Atrium ◽  
Cor Triatriatum ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Cor Triatriatum Dexter ◽  
The Right

AbstractWe report the case of a child with cor triatriatum dexter masquerading as Ebstein's anomaly on transthoracic echocardiography. This was attributed to a floppy membrane arising from the right atrium, protruding into the tricuspid valve and pushing the leaflets downwards, giving an impression of Ebstein's anomaly. The importance of recognising this pitfall will prevent misdiagnosis of Ebstein's anomaly.

Cone repair for Ebstein’s anomaly and atrial fibrillation ablation in an adult patient

2021 ◽  
Keyword(s):  
Atrial Fibrillation ◽  
Tricuspid Valve ◽  
Pulmonary Veins ◽  
Maze Procedure ◽  
Right Atrial ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Previously Treated ◽  
Cone Repair ◽  
The Right

We present a 52-year-old woman with Ebstein’s anomaly not previously treated. In this subset of patients, there are no clear guidelines regarding the best surgical strategy for treating the tricuspid valve: replace it or repair it. In this case, extensive repair of the tricuspid valve and the right ventricle is achieved using the cone repair technique popularized by Dr. José Pedro Da Silva. Because the patient also presented with symptomatic paroxysmal atrial fibrillation, a right atrial maze procedure combined with isolation of the pulmonary veins was performed using both radiofrequency and cryotherapy. At the last follow-up, 2 years after the repair, the patient is asymptomatic and maintains sinus rhythm. The last echocardiogram showed mild tricuspid regurgitation with normal right ventricular function.

scholarly journals Successful One and One-half Ventricular Circulation with Bioprosthetic Tricuspid Valve Replacement and Total Chordal Preservation in a Patient with Ebstein’s Anomaly: A Video Presentation

2021 ◽  
Vol 5 (02) ◽  
pp. 147-150
Author(s):  
Ujjwal K. Chowdhury ◽  
Sukhjeet Singh ◽  
Niwin George ◽  
Lakshmi Kumari Sankhyan ◽  
Sandeep Sharan ◽  
...  
Keyword(s):  
Right Ventricle ◽  
Tricuspid Valve ◽  
Ebstein’S Anomaly ◽  
Anterior Leaflet ◽  
Tricuspid Annulus ◽  
Tricuspid Valve Replacement ◽  
Rotational Displacement ◽  
Atrioventricular Junction ◽  
Ebstein's Anomaly ◽  
The Right

AbstractEbstein’s anomaly is a rare congenital malformation of the right ventricle and tricuspid valve which is characterized by several features that can exhibit an infinite spectrum of malformation.The abnormalities include: i) adherence of the tricuspid leaflets to the underlying myocardium (failure of delamination); ii) anterior and apical rotational displacement of the functional tricuspid annulus (septal > posterior > anterior leaflet); iii) dilatation of the right atrioventricular junction (the true tricuspid annulus) with variable degrees of hypertrophy and thinning of the wall; iv) dilatation of the “atrialized” portion of the right ventricle; and v) redundancy, fenestration, and tethering of the anterior leaflet.

scholarly journals Prenatal Sonographic Detection of Ebstein’s Anomaly

2017 ◽  
Vol 33 (3) ◽  
pp. 225-230
Author(s):  
Mariah C. Root ◽  
Kelsy L. Fisher
Keyword(s):  
Tricuspid Valve ◽  
Congenital Heart Defect ◽  
Congenital Heart ◽  
Ebstein’S Anomaly ◽  
Rare Type ◽  
Sonographic Appearance ◽  
Ebstein's Anomaly ◽  
Treatment Characteristic ◽  
The Right

Ebstein’s anomaly is a rare type of congenital heart defect characterized by a malformation of the tricuspid valve and the right side of the heart. This case study presents a well-documented case of Ebstein’s anomaly that was diagnosed prenatally using sonography. The ability of prenatal sonography to detect and accurately diagnosis this case allowed for a change in the management of the pregnancy to properly evaluate the condition and prepare for treatment. In addition, information regarding Ebstein’s anomaly is reviewed and specifically addresses etiology, symptoms, diagnosis, treatment, characteristic sonographic appearance, and common differential diagnoses.

scholarly journals Tricuspid valve dysplasia and Ebstein's anomaly in dogs: case report

2006 ◽  
Vol 58 (5) ◽  
pp. 762-767 ◽  
Author(s):  
M.G. Sousa ◽  
D.G. Gerardi ◽  
R.O. Alves ◽  
A.A. Camacho
Keyword(s):  
Heart Failure ◽  
Tricuspid Valve ◽  
Medical Therapy ◽  
Diagnostic Methods ◽  
The Other ◽  
Ebstein’S Anomaly ◽  
Post Mortem ◽  
Ebstein's Anomaly ◽  
Tricuspid Insufficiency ◽  
The Right

Two cases of tricuspid valve dysplasia are reported. Dogs were presented for evaluation of weakness and ascites. In both cases, echocardiography disclosed tricuspid insufficiency and, in one of them, tricuspid leaflets also were displaced down into the right ventricle, substantiating Ebstein's anomaly. Medical therapy for congestive heart failure was initiated. One of the dogs suddenly died shortly after diagnosis was established. Although the other dog recovered much better initially, sudden death also occurred. Post-mortem examinations showed right atrioventricular enlargement, and thickened tricuspid leaflets. Clinical features, diagnostic methods and medical therapy are discussed in this paper.

scholarly journals Ebstein's anomaly as a cause of paroxysmal atrial fibrillation

2008 ◽  
Vol 65 (11) ◽  
pp. 847-850
Author(s):  
Miodrag Damjanovic ◽  
Danijela Djordjevic-Radojkovic ◽  
Zoran Perisic ◽  
Svetlana Apostolovic ◽  
Goran Koracevic ◽  
...  
Keyword(s):  
Atrial Fibrillation ◽  
Right Ventricle ◽  
Tricuspid Valve ◽  
Paroxysmal Atrial Fibrillation ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Wpw Syndrome ◽  
Echocardiographic Examination ◽  
Electrophysiological Examination ◽  
The Right

Background. Ebstein's anomaly is characterized by a displacement of the tricuspid valve toward apex, because of anomalous attachment of the tricuspid leaflets. There are type B of Wolff-Parkinson-White (WPW) syndrome and paroxysmal arrhythmias in more than a half of all patients. Case report. We presented a female, 32-year old, with frequent paroxysms of atrial fibrillation. After conversion of rhythm an ECG showed WPW syndrome. Echocardiographic examination discovered normal size of the left cardiac chambers with paradoxical ventricular septal motion. The right ventricle was very small because of its atrialization. The origin of the tricuspid valve was 20 mm closer to apex of the right ventricle than the origin of the mitral valve. Electrophysiological examination showed a posterolateral right accesorial pathway. Atrial fibrillation was induced very easily in electrophysiological laboratory and a successful ablation of accessorial pathway was made. There were no WPW syndrome and paroxysms of atrial fibrillation after that. Conclusion. Ebstein's anomaly is one of the reasons of paroxysmal atrial fibrillation, especially in young persons with WPW syndrome.

Impact of prenatal haemodynamic and functional abnormalities in Ebstein’s anomaly on survival

2014 ◽  
Vol 24 (6) ◽  
pp. 1049-1056 ◽  
Author(s):  
Grace Freire ◽  
Thieu Nguyen ◽  
Priya Sekar ◽  
Marilyn Wilhm ◽  
Kathy Arnold ◽  
...  
Keyword(s):  
Right Ventricular ◽  
Tricuspid Valve ◽  
Tricuspid Regurgitation ◽  
Prognostic Significance ◽  
Ebstein’S Anomaly ◽  
Cardiothoracic Ratio ◽  
Ebstein's Anomaly ◽  
Functional Parameters ◽  
Profile Score ◽  
Cardiovascular Profile

AbstractPredicting outcomes of foetuses with Ebstein’s anomaly and tricuspid valve dysplasia continues to be challenging. Limited data exist on the prognostic significance of prenatal haemodynamic and functional parameters in this population. Our aim was to investigate the prognostic significance of haemodynamic and ventricular functional parameters in addition to associated morphometric parameters in patients with Ebstein’s anomaly. We reviewed medical records of foetuses with Ebstein’s anomaly and tricuspid valve dysplasia at All Children’s Hospital Johns Hopkins Medicine and Johns Hopkins University between 2005 and 2012. The main outcome was survival past 30 days from birth; participants who died in utero or <30 days after birth were considered non-survivors. There were 13 survivors and seven non-survivors. We found that participants with abnormal right ventricular function predicted by low tricuspid regurgitation velocity (<2.3 m/second) (p=0.012) and low estimated right ventricular pressure (<24 mmHg) (p=0.029), a low (<7) cardiovascular profile score (p=0.029) and high (>0.53) cardiothoracic ratio (p=0.008) at the first foetal echocardiogram were less likely to survive. In addition, participants with a fossa ovalis/atrial septal length ratio <0.36 at the last foetal echocardiogram (p=0.051) were more likely to die, albeit of borderline statistical significance. Low tricuspid regurgitation velocity and low right ventricular estimated pressure, or a low cardiovascular profile score could be potential prognostic factors for Ebstein’s anomaly and tricuspid valve dysplasia. However, future larger prospective studies are needed to confirm these initial findings.

scholarly journals A Rare Manifestation of Asymptomatic Ebstein’s Anomaly with Tricuspid Valve Endocarditis

2017 ◽  
Vol 2017 ◽  
pp. 1-4
Author(s):  
Carmel Moazez ◽  
Vicken Zeitjian ◽  
Christian Breburda ◽  
Ranjini Roy
Keyword(s):  
Tricuspid Valve ◽  
Wide Spectrum ◽  
Left Ventricular ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Normal Left Ventricular ◽  
The Right ◽  
New Diagnosis ◽  
Apical Displacement ◽  
Tricuspid Valve Endocarditis

Ebstein’s anomaly is a rare congenital heart disease that presents with apical displacement of the septal and posterior leaflets of the tricuspid valve. It has a wide spectrum of clinical presentations and has been shown to manifest itself any time from birth to adulthood. Our patient is a 43-year-old male with a history of intravenous heroin abuse who presented to the emergency department with worsening shortness of breath and lower extremity edema. He denied any prior cardiac history. A transthoracic echo showed normal left ventricular function, but a large 2.2 × 2.1 cm echodensity on the septal leaflet of the tricuspid valve consistent with vegetation with severe tricuspid regurgitation and probable leaflet perforation. It also demonstrated severe right heart enlargement with atrialization of the right ventricle and apical displacement of the tricuspid valve consistent with Ebstein’s anomaly. This is a rare case of an adult who presented with asymptomatic Ebstein’s anomaly. There have been few reports of tricuspid valve endocarditis with Ebstein’s anomaly in the literature. To our knowledge, this represents the fifth reported case of a new diagnosis of Ebstein’s anomaly in the setting of endocarditis and the second case of Ebstein’s anomaly and endocarditis in an intravenous drug abuser.

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