scholarly journals P16‐50: Clinical features of pleuroparenchymal fibroelastosis: Idiopathic versus secondary phenotype

Respirology ◽  
2021 ◽  
Vol 26 (S3) ◽  
pp. 469-469
Keyword(s):  
Clinical Features ◽  
Pleuroparenchymal Fibroelastosis ◽  
Secondary Phenotype

Heterogeneous clinical features in patients with pulmonary fibrosis showing histology of pleuroparenchymal fibroelastosis

2016 ◽  
Vol 54 (3) ◽  
pp. 162-169 ◽  
Author(s):  
Yuji Yoshida ◽  
Nobuhiko Nagata ◽  
Nobuko Tsuruta ◽  
Yasuhiko Kitasato ◽  
Kentaro Wakamatsu ◽  
...  
Keyword(s):  
Pulmonary Fibrosis ◽  
Clinical Features ◽  
Pleuroparenchymal Fibroelastosis

Pneumothorax in Patients with Idiopathic Pleuroparenchymal Fibroelastosis: Incidence, Clinical Features, and Risk Factors

Respiration ◽  
2021 ◽  
pp. 1-8
Author(s):  
Masato Kono ◽  
Yutaro Nakamura ◽  
Yasunori Enomoto ◽  
Hideki Yasui ◽  
Hironao Hozumi ◽  
...  
Keyword(s):  
Risk Factors ◽  
Clinical Features ◽  
Cumulative Incidence ◽  
Rank Test ◽  
Prior History ◽  
Pleuroparenchymal Fibroelastosis ◽  
History Of ◽  
Poor Outcomes ◽  
Persistent Air Leak ◽  
Retrospective Multicenter Study

<b><i>Background:</i></b> Idiopathic pleuroparenchymal fibroelastosis (PPFE) is a rare form of idiopathic interstitial pneumonia that is characterized by predominantly upper lobe pleural and subpleural lung parenchymal fibrosis. Pneumothorax is one of the major respiratory complications in PPFE patients; however, its clinical features are poorly understood. <b><i>Objective:</i></b> We aimed to investigate the complication of pneumothorax in patients with idiopathic PPFE. <b><i>Methods:</i></b> A retrospective multicenter study involving 89 patients who had been diagnosed with idiopathic PPFE was conducted. We investigated the cumulative incidence, clinical features, and risk factors of pneumothorax after the diagnosis of idiopathic PPFE. <b><i>Results:</i></b> Pneumothorax developed in 53 patients (59.6%) with 120 events during the observation period (41.8 ± 35.0 months). The cumulative incidence of pneumothorax was 24.8, 44.9, and 53.9% at 1, 2, and 3 years, respectively. Most events of pneumothorax were asymptomatic (<i>n</i> = 85; 70.8%) and small in size (<i>n</i> = 92; 76.7%); 30 patients (56.6%) had recurrent pneumothorax. Chest drainage was required in 23 pneumothorax events (19.2%), and a persistent air leak was observed in 13 (56.5%). Patients with pneumothorax were predominantly male and frequently had pathological diagnoses of PPFE and prior history of pneumothorax and corticosteroid use; they also had significantly poorer survival than those without pneumothorax (log-rank test; <i>p</i> = 0.001). Multivariate analysis revealed that a higher residual volume/total lung capacity ratio was significantly associated with the development of pneumothorax after the diagnosis. <b><i>Conclusion:</i></b> Pneumothorax is often asymptomatic and recurrent in patients with idiopathic PPFE, leading to poor outcomes in some cases.

Fibrosing cholestatic hepatitis: Clinical features, outcome and response to interferon and ribavirin

2001 ◽  
Vol 120 (5) ◽  
pp. A563-A564
Author(s):  
M ISMAIL ◽  
I DABOUL ◽  
B WATERS ◽  
J FLECKENSTEIN ◽  
S VERA ◽  
...  
Keyword(s):  
Clinical Features ◽  
Cholestatic Hepatitis

Abstract #873: Association of Patterns in the Oral Glucose Tolerance Test and Different Clinical Features in Patients with Insulinoma

2005 ◽  
Vol 11 ◽  
pp. 28
Author(s):  
Fanny Rodriguez Vallejo ◽  
Juan Manuel Rios Torres ◽  
Francisco J. Gomez-Pérez ◽  
Juan A. Rull Rodrigo ◽  
Bernardo Pérez Enriquez
Keyword(s):  
Glucose Tolerance ◽  
Oral Glucose Tolerance Test ◽  
Clinical Features ◽  
Glucose Tolerance Test ◽  
Tolerance Test ◽  
Oral Glucose ◽  
Oral Glucose Tolerance
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