Long‐term liver transplant outcomes for progressive familial intrahepatic cholestasis type 1: The Pittsburgh experience

Pediatric Transplantation ◽

10.1111/petr.14108 ◽

2021 ◽

Author(s):

Sarah A.F. Henkel ◽

Claudia M. Salgado ◽

Miguel Reyes‐Mugica ◽

Kyle A. Soltys ◽

Kevin Strauss ◽

...

Keyword(s):

Liver Transplant ◽

Intrahepatic Cholestasis ◽

Progressive Familial Intrahepatic Cholestasis ◽

Transplant Outcomes

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Long-Term Outcomes of Living-Donor Liver Transplantation for Progressive Familial Intrahepatic Cholestasis Type 1

Journal of Pediatric Gastroenterology and Nutrition ◽

10.1097/mpg.0000000000002983 ◽

2020 ◽

Vol Publish Ahead of Print ◽

Author(s):

Tatsuya Okamoto ◽

Mari Sonoda ◽

Eri Ogawa ◽

Shogo Ito ◽

Takao Togawa ◽

...

Keyword(s):

Liver Transplantation ◽

Intrahepatic Cholestasis ◽

Living Donor ◽

Living Donor Liver Transplantation ◽

Long Term Outcomes ◽

Donor Liver ◽

Progressive Familial Intrahepatic Cholestasis ◽

Donor Liver Transplantation

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Progressive familial intrahepatic cholestasis type 1 and extrahepatic features: no catch-up of stature growth, exacerbation of diarrhea, and appearance of liver steatosis after liver transplantation

Journal of Hepatology ◽

10.1016/s0168-8278(03)00286-1 ◽

2003 ◽

Vol 39 (3) ◽

pp. 447-452 ◽

Cited By ~ 119

Author(s):

Panayotis Lykavieris ◽

Saskia van Mil ◽

Danièle Cresteil ◽

Monique Fabre ◽

Michelle Hadchouel ◽

...

Keyword(s):

Liver Transplantation ◽

Intrahepatic Cholestasis ◽

Liver Steatosis ◽

Progressive Familial Intrahepatic Cholestasis ◽

Catch Up

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Total internal biliary diversion during liver transplantation for type 1 progressive familial intrahepatic cholestasis: a novel approach

Pediatric Transplantation ◽

10.1111/petr.12782 ◽

2016 ◽

Vol 20 (7) ◽

pp. 981-986 ◽

Cited By ~ 11

Author(s):

V. P. Mali ◽

A. Fukuda ◽

T. Shigeta ◽

H. Uchida ◽

Y. Hirata ◽

...

Keyword(s):

Liver Transplantation ◽

Intrahepatic Cholestasis ◽

Progressive Familial Intrahepatic Cholestasis ◽

Novel Approach ◽

Biliary Diversion

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Serum bile acid control in long-term maralixibat-treated patients is associated with native liver survival in children with progressive familial intrahepatic cholestasis due to bile salt export pump deficiency

Journal of Hepatology ◽

10.1016/s0168-8278(20)30757-1 ◽

2020 ◽

Vol 73 ◽

pp. S120

Author(s):

Richard Thompson ◽

Deirdre Kelly ◽

Alexander Miethke ◽

Sanjay Rajwal ◽

Nisreen Soufi ◽

...

Keyword(s):

Bile Acid ◽

Bile Salt ◽

Intrahepatic Cholestasis ◽

Serum Bile Acid ◽

Bile Salt Export Pump ◽

Progressive Familial Intrahepatic Cholestasis ◽

Acid Control ◽

Native Liver ◽

Native Liver Survival

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O136 A NOVEL, HYBRID RECOMBINANT AAV-piggyBac TRANSPOSON VECTOR PERMITS ROBUST LONG-TERM PHENOTYPE CORRECTION OF THE PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS TYPE 3 MOUSE MODEL IN VIVO

Journal of Hepatology ◽

10.1016/s0168-8278(14)60138-0 ◽

2014 ◽

Vol 60 (1) ◽

pp. S57-S58

Author(s):

S.M. Siew ◽

S.C. Cunningham ◽

I.E. Alexander

Keyword(s):

Mouse Model ◽

Intrahepatic Cholestasis ◽

Piggybac Transposon ◽

Progressive Familial Intrahepatic Cholestasis ◽

Type 3

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Cholecysto-appendicostomy as partial internal biliary drainage in Progressive Familial Intrahepatic Cholestasis Type 1: A case report and review of literature

Journal of Pediatric Surgery Case Reports ◽

10.1016/j.epsc.2015.11.009 ◽

2016 ◽

Vol 4 ◽

pp. 17-21 ◽

Cited By ~ 1

Author(s):

Yee Ian Yik ◽

Mohd Yusran Othman ◽

Ruey Terng Ng ◽

Way Seah Lee

Keyword(s):

Case Report ◽

Intrahepatic Cholestasis ◽

Biliary Drainage ◽

Review Of Literature ◽

Progressive Familial Intrahepatic Cholestasis

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Novel splice-site mutation inATP8B1results in atypical Progressive Familial Intrahepatic Cholestasis Type 1

Journal of Gastroenterology and Hepatology ◽

10.1111/j.1440-1746.2012.07290.x ◽

2013 ◽

Vol 28 (3) ◽

pp. 560-564 ◽

Cited By ~ 4

Author(s):

Emily Copeland ◽

Nisa Renault ◽

Marc Renault ◽

Sarah Dyack ◽

Dennis E Bulman ◽

...

Keyword(s):

Splice Site ◽

Intrahepatic Cholestasis ◽

Splice Site Mutation ◽

Site Mutation ◽

Progressive Familial Intrahepatic Cholestasis

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P0033 PP REDUCED EXPRESSION OF FARNESOID X RECEPTOR IN PATIENTS WITH PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS TYPE 1

Journal of Pediatric Gastroenterology and Nutrition ◽

10.1097/00005176-200406001-00157 ◽

2004 ◽

Vol 39 (Supplement 1) ◽

pp. S68-S69

Author(s):

L. Alvarez ◽

P. Jara ◽

E. L??pez-Collazo ◽

M. C. D??az ◽

L. Hierro ◽

...

Keyword(s):

Intrahepatic Cholestasis ◽

Farnesoid X Receptor ◽

Progressive Familial Intrahepatic Cholestasis

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O137 4-PHENYLBUTYLATE AMELIORATES LIVER FIBROSIS IN PATIENTS WITH PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS (PFIC) TYPE 2 AND PRURITUS IN PATIENTS WITH PFIC TYPE 1

Journal of Hepatology ◽

10.1016/s0168-8278(14)60139-2 ◽

2014 ◽

Vol 60 (1) ◽

pp. S58

Author(s):

Y. Hasegawa ◽

H. Kondou ◽

S. Naoi ◽

K. Bessho ◽

M. Ukitsu ◽

...

Keyword(s):

Liver Fibrosis ◽

Intrahepatic Cholestasis ◽

Progressive Familial Intrahepatic Cholestasis

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Partial internal biliary diversion: A solution for intractable pruritus in progressive familial intrahepatic cholestasis type 1

Saudi Journal of Gastroenterology ◽

10.4103/1319-3767.80387 ◽

2011 ◽

Vol 17 (3) ◽

pp. 212 ◽

Cited By ~ 12

Author(s):

Ramaswamy Ganesh ◽

Natarajan Suresh ◽

Malathi Sathiyasekeran ◽

Priya Ramachandran

Keyword(s):

Intrahepatic Cholestasis ◽

Progressive Familial Intrahepatic Cholestasis ◽

Biliary Diversion

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