Bilateral visual acuity reduction in a child with Marfan syndrome: Is there a pathogenetic role for optic nerve dural ectasia?

2021 ◽  
Author(s):  
Michele Trimboli ◽  
Maria Tagliente ◽  
Letizia Troisi ◽  
Sergio Manieri
Keyword(s):  
Visual Acuity ◽  
Optic Nerve ◽  
Marfan Syndrome ◽  
Pathogenetic Role ◽  
Dural Ectasia

Some aspects of diagnosis and treatment of a сircumscribed form of choroidal hemangioma complicated by macular edema

2021 ◽  
pp. 240-246
Author(s):  
J.A. Magaramov ◽  
◽  
R.A. Loginov ◽  
O.B. Klepinina ◽  
◽  
...  
Keyword(s):  
Visual Acuity ◽  
Optic Nerve ◽  
Macular Edema ◽  
Subretinal Fluid ◽  
Diagnostic Methods ◽  
Treatment Results ◽  
Transpupillary Thermotherapy ◽  
Choroidal Hemangioma ◽  
Nasal Side ◽  
Intraretinal Cysts

Introduction. The interest are rare cases of a сircumscribed choroidal hemangioma located juxtapapillary (JP) on the nasal side of the optic nerve disc (OND) and complicated by macular edema. Purpose. Studying the possibility of timely diagnosis and evaluating the effectiveness of treatment of a сircumscribed choroidal hemangioma complicated by macular edema. Material and methods. A retrospective analysis of the diagnostics and treatment results of 5 patients (5 eyes) with JP сircumscribed choroidal hemangioma, localized on the nasal side of the optic disc, complicated by macular edema, was carried out. Results. As a result, in all patients, already 1 month after the session of selective laser transpupillary thermotherapy (TTT), an increase in visual acuity and quality was observed, which was accompanied by pronounced resorption of intraretinal cysts and / or subretinal fluid in the macula. Conclusion. The purposeful use of modern diagnostic methods and the use of a sparing method of laser TTT makes it possible to identify and cure patients with CPCH complicated by macular edema without loss of visual functions. Key words: сircumscribed choroidal hemangioma, selective transpupillary thermotherapy, cystic macular edema.

Bilateral Optic Nerve Hypoplasia with Normal Visual Acuity

1978 ◽  
Vol 86 (4) ◽  
pp. 524-529 ◽  
Author(s):  
Ake Bjork ◽  
C.-G. Laureix ◽  
Ulla Laurell
Keyword(s):  
Visual Acuity ◽  
Optic Nerve ◽  
Optic Nerve Hypoplasia ◽  
Normal Visual Acuity

Sacral erosion and insufficiency fracture secondary to dural ectasia in patient with Marfan syndrome

2016 ◽  
Vol 16 (5) ◽  
pp. e301-e302
Author(s):  
Hossein Elgafy ◽  
Nicholas Peters ◽  
Robert M. Wetzel
Keyword(s):  
Marfan Syndrome ◽  
Insufficiency Fracture ◽  
Dural Ectasia

scholarly journals Transconjunctival Cryo-Assisted Extraction of Intraconal Cavernous Hemangioma

2019 ◽  
Author(s):  
Ayman E Abd El Ghafar ◽  
Sameh M Saleh ◽  
Ahmed S Elwehidy
Keyword(s):  
Visual Acuity ◽  
Optic Nerve ◽  
Postoperative Complications ◽  
Cavernous Hemangioma ◽  
Effective Technique ◽  
Safety And Efficacy ◽  
Transconjunctival Approach ◽  
Subconjunctival Hemorrhage ◽  
Assisted Extraction ◽  
Retrobulbar Hemorrhage

Abstract Background The aim of this study is to evaluate the safety and efficacy of transconjunctival cryo-assisted orbitotomy for extraction of intraconal cavernous hemangioma. Methods The study was performed at the Mansoura ophthalmic center, Mansoura University, Egypt from May 2015 to August 2018. It included 18 patients with orbital intraconal cavernous hemangioma. In all cases, preoperative orbital MRI with contrast was performed, transconjunctival approach was used and cryo-assisted extraction of the lesion was performed. Cases were followed for six months after surgery. Results This study included 18 patients with intraconal cavernous hemangioma, ten females (55.6%) and eight males (44.4%) with a mean age 35.6 years. All lesions were located in the intraconal space, eight cases (44.5%) were lateral to the optic nerve, four cases (22.2%) were above the optic nerve, and six cases (33.3%) were below the optic nerve. Postoperative complications included three cases (16.7%) that showed postoperative diplopia due to lateral rectus paresis that improved in all cases within six months, one case (5.6%) that showed postoperative retrobulbar hemorrhage and proptosis that resolved within two weeks without sequelae, and four cases (22.2%) that showed subconjunctival hemorrhage, which resolved within two weeks. Of the two cases with drop of visual acuity preoperative, one case (5.6%) showed improvement of visual acuity and one case (5.6%) did not improve. Conclusions Transconjunctival cryo-assisted extraction of intraconal cavernous hemangioma represents a safe more conservative and effective technique.

scholarly journals Recurrent Self-Induced Nontraumatic Orbital Emphysema Causing Orbital Compartment Syndrome with Optic Nerve Dysfunction

2021 ◽  
Vol 2021 ◽  
pp. 1-5
Author(s):  
S. Cutting ◽  
C. Davies-Husband ◽  
C. Poitelea
Keyword(s):  
Visual Acuity ◽  
Optic Nerve ◽  
Compartment Syndrome ◽  
Valsalva Manoeuvre ◽  
First Case ◽  
Orbital Emphysema ◽  
History Of ◽  
Nerve Dysfunction ◽  
The Right ◽  
Needle Decompression

The majority of cases of orbital emphysema are due to trauma. Complications are rare, and therefore, the need for surgical intervention is uncommon. We present the first case of which we are aware in which nontraumatic orbital emphysema led to orbital compartment syndrome and subsequent optic nerve dysfunction. The patient underwent emergency needle decompression. A 51-year-old man presented to the Emergency Department with right-sided unilateral proptosis, reduced visual acuity, and binocular diplopia. This occurred after performing a Valsalva manoeuvre with no history of head trauma. He also mentioned that over the past year he had experienced multiple episodes of transient proptosis occurring after Valsalva manoeuvres. Visual acuity in the right eye was reduced to 6/21. A relative afferent pupillary defect was present and intraocular pressure (IOP) was 12 mmHg. The CT scan showed significant orbital emphysema in the medial aspect of the right orbit. Needle decompression was performed resulting in immediate resolution of his symptoms. This case demonstrates that, in cases of orbital emphysema, a lack of a history of trauma and a normal IOP cannot always be used to rule out serious pathology.

scholarly journals SINDROM TOLOSA HUNT DENGAN KETERLIBATAN SARAF OPTIKUS

2019 ◽  
Vol 37 (1) ◽  
Author(s):  
Astra Dea Simanungkalit ◽  
Maria Larasati Susyono ◽  
Vivien Puspitasari
Keyword(s):  
Visual Acuity ◽  
Case Report ◽  
Optic Nerve ◽  
Pain Relief ◽  
Clinical Syndrome ◽  
Orbital Apex ◽  
Corticosteroid Administration ◽  
Hunt Syndrome ◽  
Nerve Dysfunction ◽  
Optic Nerve Involvement

TOLOSA HUNT SYNDROME WITH OPTIC NERVE INVOLVEMENTABSTRACTTolosa Hunt syndrome (THS) is a very rare clinical syndrome, which is characterized by unilateral headaches accompanied by dysfunction and painful ophthalmic nerves. In some cases, optic nerve involvement can be found due to inflammation at the orbital apex. Corticosteroid administration is a management of THS with pain relief generally occurring in the first 72 hours. However, corticosteroid administration is not significantly associated with nerve dysfunction or visual acuity improvement.This article is a case report of women with STH and optic nerve involvement.Keywords: Tolosa Hunt syndrome, painful ophtalmoplegia, orbital apex, superior orbital fissureABSTRAKSindrom Tolosa Hunt (STH) adalah sindrom klinik yang sangat jarang, yang ditandai oleh nyeri kepala unilateral disertai disfungsi dan nyeri saraf penggerak bola mata (painful ophtamloplegia). Pada beberapa kasus, dapat ditemukan keterlibatan saraf optikus akibat inflamasi pada apeks orbita. Pemberian kortikosteroid merupakan tatalaksana STH dengan perbaikan nyeri umumnya terjadi pada 72 jam pertama. Meskipun demikian pemberian kortikosteroid tidak berhubungan secara signifikan dengan perbaikan disfungsi saraf penggerak bola mata maupun tajam penglihatan. Artikel ini merupakan laporan kasus perempuan dengan STH dan keterlibatan saraf optikus.Kata kunci: Sindrom Tolosa Hunt, painful ophtalmoplegia, apeksorbita, fisura orbitalis superior

Outcomes of Steroid Therapy in Combination with Endoscopic Optic Nerve Decompression Surgery for Direct Traumatic Optic Neuropathy: A Case-Series

2021 ◽  
Vol 104 (7) ◽  
pp. 1166-1171
Keyword(s):  
Visual Acuity ◽  
Optic Nerve ◽  
Optic Neuropathy ◽  
Poor Prognosis ◽  
Combined Treatment ◽  
Treatment Protocol ◽  
Case Series ◽  
Light Perception ◽  
Traumatic Optic Neuropathy ◽  
Nerve Decompression

Background: Direct traumatic optic neuropathy (TON) carries a poor prognosis. However, the outcome of this injury is diverse and is related to time to treatment and treatment protocol. Objective: To evaluate the outcomes of the combined treatment protocol in patients with direct TON. Materials and Methods: The authors retrospectively reviewed the medical records of patients between January 2015 and August 2019. Main outcome was visual acuity (VA) improvement after the treatment. Results: Thirteen patients (15 eyes) were included. The mean age was 38.61 years with a range of 13 to 65 years. Initial VA varied from no light perception (NPL) in seven eyes of six patients, light perception (PL) in one eye, counting fingers in two eyes, 20/200 in three eyes, and 20/60 in two eyes. Average timing to treatment was 2.8 days (range 0 to 7 days). There were no side effects of high-dose corticosteroids treatment in all patients. During a follow-up period of three months, six of 13 patients (46.1%) had VA improvement. Conclusion: Despite poor prognosis of direct TON, the combined treatment protocol provides a favorable successful rate with most patients on having stable vision, and some having visual improvement from reducing intracanalicular pressure of the optic nerve. Keywords: Endoscopic optic nerve decompression; Traumatic optic neuropathy; Visual acuity; Case series

Predicting Visual Acuity in Children With Colobomas Involving the Optic Nerve

1996 ◽  
Vol 33 (1) ◽  
pp. 47-51
Author(s):  
Timothy W Olsen ◽  
C Gail Summers ◽  
William H Knobloch
Keyword(s):  
Visual Acuity ◽  
Optic Nerve
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