Neuroimaging in Sensory Neuronopathy

2015 ◽  
Vol 25 (5) ◽  
pp. 704-709 ◽  
Author(s):  
Raphael Fernandes Casseb ◽  
Alberto Rolim Muro Martinez ◽  
Jean Levi Ribeiro de Paiva ◽  
Marcondes Cavalcante França
Keyword(s):  
Sensory Neuronopathy

Benefit of IVIg for long-standing ataxic sensory neuronopathy with Sjogren's syndrome

Neurology ◽  
2003 ◽  
Vol 61 (6) ◽  
pp. 873-873 ◽  
Author(s):  
T. M. Burns ◽  
S. Quijano-Roy ◽  
H. R. Jones ◽  
G. I. Wolfe ◽  
S. P. Nations ◽  
...  
Keyword(s):  
Sjögren’S Syndrome ◽  
Sjögren's Syndrome ◽  
Sjogren’S Syndrome ◽  
Sjogren's Syndrome ◽  
Sensory Neuronopathy ◽  
Sjögren‘S Syndrome

scholarly journals Intravenous Immunoglobulin and Mycophenolate Mofetil for Long-Standing Sensory Neuronopathy in Sjögren's Syndrome

2012 ◽  
Vol 2012 ◽  
pp. 1-3 ◽  
Author(s):  
Maria Giovanna Danieli ◽  
Lucia Pettinari ◽  
Ramona Morariu ◽  
Fernando Monteforte ◽  
Francesco Logullo
Keyword(s):  
Mycophenolate Mofetil ◽  
Intravenous Immunoglobulin ◽  
Sjögren’S Syndrome ◽  
Sjögren's Syndrome ◽  
Sjogren’S Syndrome ◽  
Sjogren's Syndrome ◽  
Lower Limbs ◽  
High Dose ◽  
Sensory Neuronopathy ◽  
Sjögren‘S Syndrome

Sensory neuronopathy is described in association with the Sjögren's syndrome (SS). We studied a 55-year-old woman with a 4-year history of progressive asymmetric numbness, distal tingling, and burning sensation in upper and lower limbs. In a few months, she developed ataxia with increased hypoanaesthesia. Electrodiagnostic tests revealed undetectable distal and proximal sensory nerve action potential in upper and lower limbs. Cervical spine magnetic resonance showed a signal hyperintensity of posterior columns. Previous treatment with high-dose glucocorticoids and azathioprine was ineffective. A combined treatment with intravenous immunoglobulin and mycophenolate mofetil was followed by a progressive and persistent improvement. This case documented the efficacy and the safety of the coadministration of intravenous immunoglobulin and mycophenolate mofetil in sensory neuronopathy associated with SS refractory to conventional immunosuppressive therapy.

Acute Sensory Neuronopathy following Enterovirus Infection in a 3-Year-Old Girl

2017 ◽  
Vol 48 (03) ◽  
pp. 190-193 ◽  
Author(s):  
Chih-Chin Chiu ◽  
Chen-Ya Yang ◽  
Tsui-Fen Yang ◽  
Kon-Ping Lin ◽  
Shou-Hsien Huang ◽  
...  
Keyword(s):  
Sensory Nerve ◽  
Lower Limbs ◽  
Enterovirus Infection ◽  
Sensory Neuronopathy ◽  
System Disease ◽  
Sensory Axons ◽  
Comprehensive Knowledge ◽  
Sensory Nerve Action ◽  
Posterior Pharynx ◽  
Patient’S History

AbstractAcute sensory neuronopathy (SNN) is a rapidly developing peripheral nervous system disease that primarily affects sensory neurons in the dorsal root ganglion or trigeminal ganglion, leading to the impairment of sensory axons. SNN is notably uncommon in childhood; only three cases of childhood or adolescent SNN have been reported to date. Moreover, SSN has never been reported in association with enterovirus infection. Here, we report the case of a 3-year-old girl who was initially diagnosed with enterovirus infection based on the presentation of fevers, rashes on all extremities, and ulceration over the posterior pharynx. Nine days later, she presented with ataxic and wide-based gait and dysmetria affecting the extremities, with an absence of sensory nerve action potentials in the upper and lower limbs. The patient was diagnosed with acute SNN based on the criteria developed by Camdessanché et al in 2009. To our knowledge, this is the youngest case of SNN reported to date. In addition, this case reveals that enterovirus infection can be associated with acute SNN in children in rare cases. Accurate diagnosis relies on clinical suspicion, comprehensive knowledge of the patient's history, and careful characterization of abnormal findings in electrodiagnostic studies.

FGFR3 autoantibodies in sensory neuronopathy

2019 ◽  
Vol 91 (1) ◽  
pp. 8-8
Author(s):  
Norman Latov
Keyword(s):  
Clinical Practice ◽  
Sensory Neuropathy ◽  
Sensory Neuronopathy

FGFR3 antibodies have been associated with sensory neuropathy, but many questions remain regarding their use in clinical practice.

Sign in / Sign up

Export Citation Format

Share Document