scholarly journals Pulmonary artery aneurysm associated with a nonstenotic bicuspid pulmonic valve: A role for genetics?

2021 ◽  
Author(s):  
Sophia L. Alexis ◽  
Ismail El‐Hamamsy ◽  
Michael J. Robbins
Keyword(s):  
Pulmonary Artery ◽  
Artery Aneurysm ◽  
Pulmonary Artery Aneurysm ◽  
Pulmonic Valve

scholarly journals Pulmonary Artery Aneurysm Repair with Alpha-1 Anti-trypsin Deficiency

2021 ◽  
Author(s):  
Brett Starr ◽  
Caitlin Takahashi-Pipkin ◽  
Michael Bates ◽  
Shahab Akhter
Keyword(s):  
Pulmonary Hypertension ◽  
Pulmonary Artery ◽  
Artery Aneurysm ◽  
Pulmonary Artery Aneurysm ◽  
Pulmonic Valve ◽  
Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin Deficiency ◽  
Alpha 1 Antitrypsin ◽  
Aneurysm Repair ◽  
Work Up

A 62-year-old woman with pulmonary hypertension due to alpha-1 antitrypsin deficiency and known congenital pulmonic valve stenosis presented with palpitations, chest pressure and bradycardia and was found to have a 6 cm pulmonary artery aneurysm on work-up. The patient underwent surgical pulmonary artery aneurysm repair and recovered from operation without complications.

scholarly journals Asymptomatic Pulmonary Artery Aneurysm with a Bicuspid Pulmonic Valve

2018 ◽  
Vol 45 (3) ◽  
pp. 190-191
Author(s):  
Sahil Prasada ◽  
Olivia N. Gilbert ◽  
Sanjay K. Gandhi ◽  
Bharathi Upadhya ◽  
Richard Brandon Stacey
Keyword(s):  
Pulmonary Artery ◽  
Artery Aneurysm ◽  
Pulmonary Artery Aneurysm ◽  
Pulmonic Valve

scholarly journals Pulmonary artery aneurysm secondary to congenital pulmonic valve stenosis

2017 ◽  
Vol 5 (21) ◽  
pp. 32
Author(s):  
Audra Schwalk ◽  
Gilbert Berdine
Keyword(s):  
Pulmonary Artery ◽  
Standard Treatment ◽  
Artery Aneurysm ◽  
Close Monitoring ◽  
Pulmonary Artery Aneurysm ◽  
Pulmonic Valve ◽  
Pulmonary Artery Aneurysms ◽  
Work Up ◽  
Aorta Diameter ◽  
Pulmonary Artery Diameter

Pulmonary artery (PA) aneurysms are uncommon and often diagnosed post-mortem. Theyare characterized by a PA/aorta diameter ratio greater than 2 on transthoracic echocardiographyor a pulmonary artery diameter greater than 4 or 5 cm on computed tomography. The mostcommon conditions associated with pulmonary artery aneurysm are congenital heart defectswith left-to-right shunts and pulmonic valve abnormalities. There are also numerous causesof acquired pulmonary artery aneurysms, including infection, vasculitis, pulmonary arterialhypertension, trauma, neoplasm and pulmonary embolism. Symptoms of PA aneurysm areusually non-specific, and physical examination findings are variable depending on the underlyingcause. Work-up includes various imaging modalities, transthoracic echocardiography, and rightheart catheterization. The gold standard treatment is surgery, but in select patients, conservativemanagement with close monitoring can be pursued.

scholarly journals Pulmonary artery aneurysm associated with a non-stenotic bicuspid pulmonic valve: a role for genetics?

2021 ◽  
Author(s):  
Sophia Alexis ◽  
Ismail El-Hamamsy ◽  
Michael Robbins
Keyword(s):  
Pulmonary Artery ◽  
Artery Aneurysm ◽  
Vascular Wall ◽  
Aortic Aneurysms ◽  
Pulmonary Artery Aneurysm ◽  
Aortic Valves ◽  
Pulmonic Valve ◽  
Thoracic Aortic Aneurysms ◽  
Pulmonary Artery Aneurysms ◽  
The Relationship

Background Bicuspid pulmonic valves are quite uncommon, being described in only 0.1% of donor hearts, while pulmonary artery aneurysms are even more rare, having been found in 8 out of 109,571 autopsies. This rarity makes it difficult to characterize the relationship between them. Materials & Methods We describe the case of a 66-year-old female who was found to have a bicuspid pulmonic valve and pulmonary artery aneurysm (5.1cm) on imaging by her cardiologist. Discussion & Conclusion This case raises the question of whether the association between bicuspid semilunar valve disease and vascular wall anomalies are more genetic or hemodynamic. Even on the aortic side, despite the robust association between bicuspid aortic valves and thoracic aortic aneurysms, the mechanism still remains unclear. In our patient there was no significant gradient across the bicuspid pulmonic valve, suggesting that hemodynamics are not the primum mobile of this association.

Sign in / Sign up

Export Citation Format

Share Document