scholarly journals Surgical management of the scimitar syndrome

2021 ◽  
Author(s):  
Ujjwal K. Chowdhury ◽  
Robert H. Anderson ◽  
Lakshmi K. Sankhyan ◽  
Niwin George ◽  
Niraj N. Pandey ◽  
...  
Keyword(s):  
Surgical Management ◽  
Scimitar Syndrome

Surgical management of scimitar syndrome: an alternative approach

2008 ◽  
Vol 78 (5) ◽  
pp. 419-420 ◽  
Author(s):  
Ahmad Rajaii-Khorasani ◽  
Mahdi Kahrom ◽  
Hassan Mottaghi ◽  
Hadi Kahrom
Keyword(s):  
Surgical Management ◽  
Scimitar Syndrome ◽  
Alternative Approach

scholarly journals Pericardial tunnel technique in the surgical management of the vertical form of scimitar syndrome

2018 ◽  
Vol 27 (3) ◽  
pp. 387-393 ◽  
Author(s):  
Yanjun Sun ◽  
Haibo Zhang ◽  
Jinfen Liu ◽  
Zhiwei Xu ◽  
Shunmin Wang ◽  
...  
Keyword(s):  
Surgical Management ◽  
Scimitar Syndrome ◽  
Tunnel Technique

scholarly journals Surgical Management of the Scimitar Syndrome

2021 ◽  
Author(s):  
Ujjwal Chowdhury ◽  
Robert Anderson ◽  
Lakshmi Sankhyan ◽  
Niwin George ◽  
Niraj Pandey ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Surgical Management ◽  
Surgical Intervention ◽  
Respiratory Infections ◽  
Computed Tomographic Angiography ◽  
Scimitar Syndrome ◽  
Surgical Approaches ◽  
Radiographic Findings ◽  
Computed Tomographic ◽  
Clinical Presentations

The morphology variations of the so-called scimitar vein are many and varied. We present a synthesis of 92 published investigations of the overall scimitar syndrome. We reviewed the clinical presentations, diagnostic modalities, surgical approaches, and outcomes. Diagnostic information was provided by clinical presentations, radiographic findings, transthoracic and transesophageal echocardiography, computed-tomographic angiography, magnetic resonance imaging, angiocardiography, and ventilation/perfusion scans. These investigations served to elucidate the origin, course, and termination of the scimitar vein, the intracardiac anatomy, the presence of associated defects, and the patterns of any accompanying pulmonary lesions. In short, they defined the disease prior to surgical intervention. Of the patients described, up to four-fifths presented during infancy, with cardiac failure, increased pulmonary flow, and pulmonary hypertension. Associated cardiac and extracardiac defects, particularly hypoplasia of the right lung, are present in up to three-quarters of cases. Overall operative mortality has been cited between 4.8% and 5.9%. Mortality was highest in patients with preoperative pulmonary hypertension, and those undergoing surgery in infancy. Despite timely surgical intervention, post-repair obstruction of the scimitar vein, intra-atrial baffle obstruction, or stenosis of the inferior caval vein were reported in up to two-thirds of cases. The venous obstruction could not be related to any particular surgical technique. On long term follow-up, one sixth of patients reported persistent dyspnoea and recurrent respiratory infections. Any infants presenting with heart failure, right-sided heart, and hypoplastic right lung should be evaluated to exclude the syndrome. An increased appreciation of variables will contribute to improved surgical management.

scholarly journals Scimitar syndrome: report of a case and its surgical management

2009 ◽  
Vol 29 (1) ◽  
pp. 50-52 ◽  
Author(s):  
Ahmad Rajaii-Khorasani ◽  
Mahdi Kahrom ◽  
Hassan Mottaghi ◽  
Hadi Kahrom
Keyword(s):  
Surgical Management ◽  
Scimitar Syndrome ◽  
Syndrome Report

scholarly journals Surgical management of scimitar syndrome: An alternative approach

2003 ◽  
Vol 125 (2) ◽  
pp. 238-245 ◽  
Author(s):  
John W. Brown ◽  
Mark Ruzmetov ◽  
Douglas J. Minnich ◽  
Palaniswamy Vijay ◽  
Christopher A. Edwards ◽  
...  
Keyword(s):  
Surgical Management ◽  
Scimitar Syndrome ◽  
Alternative Approach

Surgical Management of Patients With 22q11.2 Deletion Syndrome

2019 ◽  
Vol 4 (5) ◽  
pp. 857-869
Author(s):  
Oksana A. Jackson ◽  
Alison E. Kaye
Keyword(s):  
Surgical Management ◽  
Preoperative Evaluation ◽  
Preoperative Assessment ◽  
22Q11.2 Deletion Syndrome ◽  
Deletion Syndrome ◽  
22Q11.2 Deletion ◽  
Surgical Decision ◽  
Obstructive Sleep ◽  
Spine Abnormalities ◽  
Speech Assessment

Purpose The purpose of this tutorial was to describe the surgical management of palate-related abnormalities associated with 22q11.2 deletion syndrome. Craniofacial differences in 22q11.2 deletion syndrome may include overt or occult clefting of the palate and/or lip along with oropharyngeal variances that may lead to velopharyngeal dysfunction. This chapter will describe these circumstances, including incidence, diagnosis, and indications for surgical intervention. Speech assessment and imaging of the velopharyngeal system will be discussed as it relates to preoperative evaluation and surgical decision making. Important for patients with 22q11.2 deletion syndrome is appropriate preoperative screening to assess for internal carotid artery positioning, cervical spine abnormalities, and obstructive sleep apnea. Timing of surgery as well as different techniques, common complications, and outcomes will also be discussed. Conclusion Management of velopharyngeal dysfunction in patients with 22q11.2 deletion syndrome is challenging and requires thoughtful preoperative assessment and planning as well as a careful surgical technique.

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