Tetralogy of Fallot, right aortic arch with isolated left subclavian artery: Rare synchronous triple occurrence!!!

2020 ◽  
Vol 35 (10) ◽  
pp. 2804-2805
Author(s):  
Rishabh Khurana ◽  
Arun Sharma ◽  
Sheragaru Hanumanthappa Chandrashekhara ◽  
Amit Ajit Deshpande
Keyword(s):  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Subclavian Artery ◽  
Left Subclavian Artery ◽  
Right Aortic Arch

scholarly journals Importance of Absent Ductus Arteriosus in Tetralogy of Fallot with Absent Pulmonary Valve Syndrome

2014 ◽  
Vol 41 (6) ◽  
pp. 664-667 ◽  
Author(s):  
Muhammad Yasir Qureshi ◽  
Harold M. Burkhart ◽  
Paul Julsrud ◽  
Frank Cetta
Keyword(s):  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Subclavian Artery ◽  
Pulmonary Valve ◽  
Left Subclavian Artery ◽  
Ductus Arteriosus ◽  
Vascular Ring ◽  
Right Aortic Arch ◽  
Absent Pulmonary Valve ◽  
Absent Pulmonary Valve Syndrome

Tetralogy of Fallot without pulmonary valve syndrome is almost always associated with an absent ductus arteriosus. Patients with right aortic arch and retroesophageal left subclavian artery have a vascular ring if the left ductus arteriosus or its remnant and the Kommerell diverticulum are present. We report the cases of 2 infants in whom the role of an absent ductus arteriosus or its remnant is noteworthy. Both patients had a combination of tetralogy of Fallot with absent pulmonary valve syndrome and right aortic arch with retroesophageal left subclavian artery without a vascular ring. The absence of the ductus arteriosus has a role in the pathogenesis of tetralogy of Fallot with absent pulmonary valve syndrome. The absence of a ductus arteriosus in the right aortic arch with retroesophageal left subclavian artery precludes a vascular ring.

Tetralogy of Fallot with coarctation of the aorta: a newly recognised developmental and anatomic syndrome

2014 ◽  
Vol 24 (4) ◽  
pp. 714-720 ◽  
Author(s):  
Elodie Perdreau ◽  
Lucile Houyel ◽  
Alban-Elouen Baruteau
Keyword(s):  
Aortic Arch ◽  
Tetralogy Of Fallot ◽  
Subclavian Artery ◽  
Left Subclavian Artery ◽  
Pulmonary Atresia ◽  
Coarctation Of The Aorta ◽  
Mirror Image ◽  
Right Aortic Arch ◽  
Initial Assessment ◽  
The Right

AbstractTetralogy of Fallot and coarctation of the aorta is an exceptional association. We report here four cases of infants referred for tetralogy of Fallot with or without pulmonary atresia associated with aortic coarctation from 1974 to 2013. All had a right aortic arch, and the coarctation was abnormally situated between the right common carotid and the right subclavian arteries. In all, two infants had an abnormal left subclavian artery and one child had DiGeorge syndrome. All underwent staged surgical repair of the left and right-sided obstructions. A review of the literature shows two types of coarctation in this context. In left aortic arch, coarctation is situated distal to the left subclavian artery. In right aortic arch, coarctation is distal to the right common carotid artery, mirror-image of interrupted left aortic arch type B, associated with anomalies of the branches of the aorta, and should be considered a complex anomaly of aortic arches in the setting of an outflow tract defect due to abnormal migration of cardiac neural crest cells. Screening for this unusual association is critical in the initial assessment of all patients with tetralogy of Fallot.

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