Long‐term walking ability and patient satisfaction after lower limb functional surgery in patients affected by Charcot‐Marie‐Tooth disease: A retrospective study

2020 ◽  
Vol 25 (3) ◽  
pp. 297-302
Author(s):  
Irene Carantini ◽  
Andrea Merlo ◽  
Donatella Esposito ◽  
Paolo Zerbinati ◽  
Luca Gaiani ◽  
...  
Keyword(s):  
Patient Satisfaction ◽  
Retrospective Study ◽  
Lower Limb ◽  
Walking Ability ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
Functional Surgery ◽  
Tooth Disease

Biomechanical effects of sensorimotor orthoses in adults with Charcot–Marie–Tooth disease

2015 ◽  
Vol 40 (4) ◽  
pp. 436-446 ◽  
Author(s):  
Caleb Wegener ◽  
Katrin Wegener ◽  
Richard Smith ◽  
Karl-Heinz Schott ◽  
Joshua Burns
Keyword(s):  
Lower Limb ◽  
Repeated Measures ◽  
Three Dimensional ◽  
Walking Ability ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
Inherited Neuropathy ◽  
Custom Made ◽  
Patient Reported ◽  
Tooth Disease

Background: Charcot–Marie–Tooth disease is an inherited neuropathy causing progressive weakness, foot deformity and difficulty walking. Clinical anecdotes suggest orthoses designed on the ‘sensorimotor’ paradigm are beneficial for improving gait in Charcot–Marie–Tooth disease. Objectives: Investigate the effect of sensorimotor orthoses on in-shoe and lower limb biomechanics in adults with Charcot–Marie–Tooth disease. Study design: Randomised, repeated-measures, exploratory study. Methods: Eight males and two females with Charcot–Marie–Tooth disease aged 31–68 years fitted with pedorthic shoes and custom-made sensorimotor orthoses were randomly tested at baseline and after 4 weeks of adaptation. In-shoe three-dimensional multi-segment foot and lower limb kinematics and kinetics were collected as were plantar pressures, electromyography and self-reported comfort, stability, cushioning and preference. Results: Compared to the shoe only condition, sensorimotor orthoses increased midfoot eversion and plantarflexion, increased ankle eversion and produced small but significant changes at the knee and hip indicating increased internal rotation. The orthoses increased medial ground reaction forces and increased pressure at the heel, midfoot and toes. There were minimal effects on electromyography. The sensorimotor orthoses were rated higher for comfort, cushioning, stability and preference. Conclusion: Sensorimotor orthoses produced changes in kinematic, kinetic and pressure variables in adults with Charcot–Marie–Tooth disease and were regarded as more comfortable, cushioned and stable during walking. Clinical relevance In this study, the walking ability of patients with Charcot–Marie–Tooth disease improved with the use of foot orthoses designed according to the sensorimotor paradigm. However, the mechanism of action appears to be primarily mechanical in origin. Randomised controlled trials are necessary to evaluate the long-term patient-reported outcomes of sensorimotor orthoses.

Long term results of the revisited Meary closing wedge tarsectomy for the treatment of the fixed cavo-varus foot in adolescent with Charcot-Marie-Tooth disease

2019 ◽  
Vol 25 (6) ◽  
pp. 834-841 ◽  
Author(s):  
Anne-Laure Simon ◽  
Raphaël Seringe ◽  
Alina Badina ◽  
Nejib Khouri ◽  
Christophe Glorion ◽  
...  
Keyword(s):  
Long Term Results ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
Closing Wedge ◽  
Tooth Disease

Long-Term Effective Thalamic Deep Brain Stimulation for Neuropathic Tremor in Two Patients with Charcot-Marie-Tooth Disease

2017 ◽  
Vol 95 (2) ◽  
pp. 102-106 ◽  
Author(s):  
Lidia Cabañes-Martínez ◽  
Marta Del Álamo de Pedro ◽  
Gema de Blas Beorlegui ◽  
Ignacio Regidor Bailly-Bailliere
Keyword(s):  
Deep Brain Stimulation ◽  
Brain Stimulation ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
Tooth Disease ◽  
Deep Brain

Proximal Lower-Limb Weakness in Charcot-Marie-Tooth Disease—Reply

2013 ◽  
Vol 70 (12) ◽  
pp. 1587
Author(s):  
Ki Wha Chung ◽  
Sang Soo Lee ◽  
Young Bin Hong ◽  
Jeong Hyun Yoo ◽  
Byung-Ok Choi
Keyword(s):  
Lower Limb ◽  
Limb Weakness ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
Lower Limb Weakness ◽  
Proximal Lower Limb ◽  
Tooth Disease

scholarly journals Long-Term Results of Reconstruction for Treatment of a Flexible Cavovarus Foot in Charcot-Marie-Tooth Disease

2008 ◽  
Vol 90 (12) ◽  
pp. 2631-2642 ◽  
Author(s):  
Christina M Ward ◽  
Lori A Dolan ◽  
D Lee Bennett ◽  
Jose A Morcuende ◽  
Reginald R Cooper
Keyword(s):  
Long Term Results ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
Tooth Disease

scholarly journals A Case Report of a Patient with Charcot-Marie-Tooth Disease Complaining about Lower Limb Pain

2018 ◽  
Vol 39 (6) ◽  
pp. 1321-1328
Author(s):  
Hee-young Moon ◽  
Gwang-hyun Ryu ◽  
Won-jung Choo ◽  
Yo-sup Choi ◽  
Ji-won Park ◽  
...  
Keyword(s):  
Case Report ◽  
Lower Limb ◽  
Limb Pain ◽  
Charcot Marie Tooth ◽  
Charcot Marie Tooth Disease ◽  
Lower Limb Pain ◽  
Tooth Disease
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