scholarly journals Transitional care for patients with surgical pediatric hepatobiliary disease: Choledochal cysts and biliary atresia

2019 ◽  
Vol 34 (6) ◽  
pp. 966-974 ◽  
Author(s):  
Gudrun Aspelund ◽  
Elaa M Mahdi ◽  
David H Rothstein ◽  
Derek S Wakeman ◽  
PEDIATRICS ◽  
1992 ◽  
Vol 89 (2) ◽  
pp. 329-330
Author(s):  
PIETRO VAJRO ◽  
ANGIOLA FONTANELLA ◽  
EMILIA VUTTARIELLO ◽  
ANNA DE VINCENZO ◽  
GIULIANA FORTUNATO

For the practicing pediatrician, the most commonly encountered causes of neonatal cholestasis are idiopathic neonatal hepatitis (INH) and extrahepatic biliary atresia (EHBA). However, despite extensive research, little improvement in our understanding of the etiology of INH and EHBA has occurred.1 It has been proposed that both of them may be part of a continuum of hepatobiliary disease caused by a common insult with a different predominant injury site.2 In this respect, it is interesting that, up to the present, several cases of discordance for EHBA in twins of various zygosity have been reported,3-8 whereas no data are available about either concordance or discordance for INH both in monozygotic and dizygotic twins.


2017 ◽  
Vol 41 (3) ◽  
pp. 354-364 ◽  
Author(s):  
Inna N. Lobeck ◽  
Rachel Sheridan ◽  
Mark Lovell ◽  
Phylicia Dupree ◽  
Greg M. Tiao ◽  
...  

PEDIATRICS ◽  
1969 ◽  
Vol 43 (2) ◽  
pp. 273-276
Author(s):  
Jay Bernstein ◽  
Raul Braylan ◽  
A. Joseph Brough

Conjugated hyperbilirubinemia in the newborn period and early infancy can result from choledochal obstruction or hepatocellular damage. Examples of the former include biliary atresia, choledochal cyst, and choledochal bile plugs. The recognition of these conditions and their differentiation are of importance in determining the best and most effective course of therapy. Choledochal cysts and bile plugs can be corrected surgically, and the presence of these two conditions is best determined by surgical exploration and transcholecystic cholangiography. Previous liver biopsy is helpful in establishing the presence of an obstructive lesion; but, because of the similarity of histopathological effects on the liver, it will be of little help in differentiating the causes of obstruction.


PEDIATRICS ◽  
1972 ◽  
Vol 50 (5) ◽  
pp. 812-814
Author(s):  
C. Y. YEUNG

This study is in agreement with the observation that the serum 5’ nucleotidase level is related to the degree of bile duct proliferation in hepatobiliary disease. In infants with congenital extrahepatic biliary atresia, where ductal proliferation is a feature, the enzyme levels are markedly raised and are significantly different from those with neonatal hepatitis. Such finding is of diagnostic value in differentiating between the two conditions.


2021 ◽  
Author(s):  
Lizhu Chen ◽  
Fujiao He ◽  
Kaihui Zeng ◽  
Bing Wang ◽  
Jingyu Li ◽  
...  

Hepatology ◽  
1998 ◽  
Vol 27 (6) ◽  
pp. 1475-1482 ◽  
Author(s):  
Kenneth L. Tyler ◽  
Ronald J. Sokol ◽  
Stephanie M. Oberhaus ◽  
Mysan Le ◽  
Frederick M. Karrer ◽  
...  

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