Hepatology: “Central dot sign” of Caroli syndrome

2015 ◽  
Vol 30 (2) ◽  
pp. 234-234 ◽  
Author(s):  
G Perricone ◽  
A Vanzulli
Keyword(s):  
Caroli Syndrome

10. Caroli syndrome–A case report

2018 ◽  
Vol 8 ◽  
pp. S105-S106 ◽  
Author(s):  
Jyoti Kadian ◽  
Tarana Gupta ◽  
Nitin Yadav ◽  
Hari Kishan Aggarwal
Keyword(s):  
Case Report ◽  
Caroli Syndrome

Giant choledochal cyst and infantile polycystic kidneys as prenatal sonographic features of Caroli syndrome

2019 ◽  
Vol 48 (1) ◽  
pp. 45-47
Author(s):  
Kuntharee Traisrisilp ◽  
Fuanglada Tongprasert ◽  
Komson Wannasai ◽  
Theera Tongsong
Keyword(s):  
Choledochal Cyst ◽  
Polycystic Kidneys ◽  
Caroli Syndrome

scholarly journals Hepatobiliary and Pancreatic: Caroli syndrome: Egg‐like sign on CT

2019 ◽  
Vol 35 (2) ◽  
pp. 180-180
Author(s):  
Y Zhong ◽  
S Peng ◽  
Y Yang
Keyword(s):  
Caroli Syndrome

scholarly journals Revisiting Caroli Syndrome in a Tanzanian Patient

Cureus ◽  
2020 ◽  
Author(s):  
Casmir Wambura ◽  
Munish Sharma ◽  
Salim Surani
Keyword(s):  
Caroli Syndrome

scholarly journals Factors contributing to diagnostic delay of Caroli syndrome: a single-center, retrospective study

2020 ◽  
Vol 20 (1) ◽  
Author(s):  
Wen Shi ◽  
Xiao-ming Huang ◽  
Yun-lu Feng ◽  
Feng-dan Wang ◽  
Xiao-xing Gao ◽  
...  
Keyword(s):  
Risk Factors ◽  
Clinical Symptoms ◽  
Medical Center ◽  
Diagnostic Delay ◽  
Mainland China ◽  
Magnetic Resonance Cholangiopancreatography ◽  
Laboratory Findings ◽  
Hepatic Cysts ◽  
Initial Symptoms ◽  
Caroli Syndrome

Abstract Background Caroli syndrome (CS) is a rare congenital disorder without pathognomonic clinical symptoms or laboratory findings; therefore, the diagnosis is often delayed. The objective of this study was to investigate the diagnostic delay and associated risk factors in CS patients. Methods This was a retrospective analysis of 16 CS patients admitted to a single tertiary medical center on mainland China. The diagnostic timelines of CS patients were reviewed to demonstrate the initial findings of CS at diagnosis, the risk factors associated with diagnostic delay, and potential clues leading to early diagnosis. Results The median diagnostic delay was 1.75 years (range: 1 month to 29 years, interquartile range: 6.2 years) in 16 enrolled CS patients. Sex, age, and initial symptoms were not associated with diagnostic delay. 87.5% of CS patients were diagnosed by imaging, and the accuracies of ultrasonography, computed tomography (CT), and magnetic resonance cholangiopancreatography were 25, 69.2, and 83.3%, respectively. The median diagnostic delays for patients with or without CT performed at the first hospital visited according to physician and radiologist suspicion of the diagnosis were 7.4 months and 6 years, respectively (p = 0.021). Hepatic cysts with splenomegaly were detected by ultrasound in over half of CS patients. Conclusions The majority of CS patients were not diagnosed until complications of portal hypertension had already developed. Recognition and early suspicion of the disease were important factors influencing diagnostic delay of CS. Hepatic cysts plus splenomegaly detected by US might raise the clinical suspicion to include CS in the differential diagnosis.

Caroli syndrome: a clinical case

2020 ◽  
pp. 42-47
Author(s):  
T. Shindina ◽  
E. Aleksandrova ◽  
O. Minushkin ◽  
O. Kropova ◽  
Maksim Maksimov
Keyword(s):  
Patient Care ◽  
Rare Diseases ◽  
Clinical Case ◽  
The State ◽  
State Program ◽  
Caroli Syndrome

This article covers a case of the rare, hereditarily caused disease, "Caroli Syndrome". The publication of this case is important because it shows that rare diseases occur, should be diagnosed and treated at all stages of patient care. It is important to know that this pathology is diagnosed and treated according to the state program — "Rare diseases".

scholarly journals Re-resection of remnant Caroli syndrome six years after the first resection (case report)

2016 ◽  
Vol 3 ◽  
pp. 8-10
Author(s):  
Ahmed Zidan ◽  
Astride Bauschke ◽  
Hubert Scheuerlein ◽  
Utz Settmacher ◽  
Falk Rauchfuss
Keyword(s):  
Case Report ◽  
Caroli Syndrome
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