Cathepsin K expression in a wide spectrum of perivascular epithelioid cell neoplasms (PEComas): a clinicopathological study emphasizing extrarenal PEComas

2013 ◽  
Vol 62 (4) ◽  
pp. 642-650 ◽  
Author(s):  
Qiu Rao ◽  
Liang Cheng ◽  
Qiu-yuan Xia ◽  
Biao Liu ◽  
Li Li ◽  
...  
Keyword(s):  
Wide Spectrum ◽  
Cathepsin K ◽  
Epithelioid Cell ◽  
Perivascular Epithelioid Cell Neoplasms ◽  
Perivascular Epithelioid Cell ◽  
Clinicopathological Study

scholarly journals Bladder perivascular epithelioid cell neoplasm: The importance of immunohistochemistry in the diagnosis of an unusual neoplasm

2021 ◽  
Vol 9 ◽  
pp. 2050313X2110008
Author(s):  
Solange De Noon ◽  
Benjamin Ayres ◽  
Uday Patel ◽  
Rami Issa ◽  
Colan Maxwell Ho-Yen
Keyword(s):  
Differential Diagnosis ◽  
Epithelioid Cell ◽  
Review Of The Literature ◽  
Histological Features ◽  
Perivascular Epithelioid Cell Neoplasms ◽  
Perivascular Epithelioid Cell ◽  
Organ Systems ◽  
Cell Neoplasm ◽  
Key Features ◽  
Mesenchymal Tumours

Perivascular epithelioid cell neoplasms represent a group of uncommon mesenchymal tumours with as yet undiscovered benign counterpart. Although perivascular epithelioid cell neoplasms have been described arising in most organ systems as well as in soft tissue and bone, only a small number of perivascular epithelioid cell neoplasms have been reported in the bladder. To date, there is no agreed system for predicting the behaviour of these tumours. We describe a case of a perivascular epithelioid cell neoplasm of the bladder arising in a 57-year-old male and initially diagnosed on biopsy and present a review of the literature focussing on the pathological differential diagnosis and the importance of key histological features in conjunction with a broad immunohistochemical panel. This case report highlights the key features of bladder perivascular epithelioid cell neoplasms that distinguishes these rare neoplasms from other bladder lesions.

scholarly journals Cathepsin K expression in the spectrum of perivascular epithelioid cell (PEC) lesions of the kidney

2011 ◽  
Vol 25 (1) ◽  
pp. 100-111 ◽  
Author(s):  
Guido Martignoni ◽  
Franco Bonetti ◽  
Marco Chilosi ◽  
Matteo Brunelli ◽  
Diego Segala ◽  
...  
Keyword(s):  
Cathepsin K ◽  
Epithelioid Cell ◽  
Perivascular Epithelioid Cell

Histopathologic Characterization of Bladder Perivascular Epithelioid Cell Neoplasms (PEComa)

2020 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Neil M. Neumann ◽  
Michael C. Haffner ◽  
Pedram Argani ◽  
Chia-Sui Kao ◽  
Jonathan I. Epstein
Keyword(s):  
Epithelioid Cell ◽  
Perivascular Epithelioid Cell Neoplasms ◽  
Perivascular Epithelioid Cell

scholarly journals A Primary Adrenal Epithelioid Angiomyolipoma (PEComa) in a Patient with Tuberous Sclerosis Complex: Report of a Case and Review of the Literature

2020 ◽  
Vol 2020 ◽  
pp. 1-4 ◽  
Author(s):  
Nancy Torres Luna ◽  
Jorge Esteban Mosquera ◽  
Isin Yagmur Comba ◽  
Mustafa Kinaan ◽  
Jorge Otoya
Keyword(s):  
Aggressive Behavior ◽  
Tuberous Sclerosis ◽  
Tuberous Sclerosis Complex ◽  
Present Report ◽  
Epithelioid Cell ◽  
Renal Tumors ◽  
Mesenchymal Tumors ◽  
Epithelioid Angiomyolipoma ◽  
Perivascular Epithelioid Cell Neoplasms ◽  
Perivascular Epithelioid Cell

Epithelioid angiomyolipomas (EAMLs) are mesenchymal tumors that are part of the family of the perivascular epithelioid cell neoplasms (PEComas). These tumors portray a potential aggressive behavior with metastatic lesions found in around 30% of reported cases. EAMLs might present sporadically or in association with the tuberous sclerosis complex (TSC). They typically involve the kidneys, liver, and lungs. It is extremely rare for these tumors to arise from other organs. The present report describes an unusual case of an adult patient with a history of TSC who developed EAML of the adrenal gland. Moreover, he presented with metastatic disease to the liver, a feature rarely described. The diagnosis of EAMLs can be challenging as they are hard to distinguish from other adrenal or renal tumors without a thorough histopathologic and immunohistochemical evaluation. Due to the potential aggressive behavior of these malignancies, timely diagnosis is extremely important and has significant therapeutic and prognostic implications.

Perivascular Epithelioid Cell Neoplasms of Soft Tissue and Gynecologic Origin

2005 ◽  
Vol 29 (12) ◽  
pp. 1558-1575 ◽  
Author(s):  
Andrew L Folpe ◽  
Thomas Mentzel ◽  
Hans-Anton Lehr ◽  
Cyril Fisher ◽  
Bonnie L Balzer ◽  
...  
Keyword(s):  
Soft Tissue ◽  
Epithelioid Cell ◽  
Perivascular Epithelioid Cell Neoplasms ◽  
Perivascular Epithelioid Cell

Perivascular Epithelioid Cell Neoplasms: A Systematic Review of Prognostic Factors

2009 ◽  
Vol 16 (5) ◽  
pp. 527-532 ◽  
Author(s):  
Nazila Zekry ◽  
Mark A. Rettenmaier ◽  
Lisa N. Abaid ◽  
Cameron R. John ◽  
John P. Micha ◽  
...  
Keyword(s):  
Systematic Review ◽  
Prognostic Factors ◽  
Epithelioid Cell ◽  
Perivascular Epithelioid Cell Neoplasms ◽  
Perivascular Epithelioid Cell
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