Auriculotemporal Neuralgia Secondary to TMJ Synovial Cyst: A Rare Presentation of a Rare Entity

2013 ◽  
Vol 53 (10) ◽  
pp. 1662-1665 ◽  
Author(s):  
Hossein Ansari ◽  
Carrie E. Robertson ◽  
John I. Lane ◽  
Christopher F. Viozzi ◽  
Ivan Garza
Keyword(s):  
Synovial Cyst ◽  
Rare Entity ◽  
Rare Presentation ◽  
Auriculotemporal Neuralgia

scholarly journals Multiple Koenen Tumors, a Rare Entity: Combination Treatment with 1% Topical Sirolimus Electrofulguration and Excision

2020 ◽  
Vol 7 (1) ◽  
pp. 66-70
Author(s):  
Vishalakshi Viswanath ◽  
Jay D. Gupte ◽  
Niharika Prabhu ◽  
Nilima L. Gour
Keyword(s):  
Tuberous Sclerosis ◽  
Combination Treatment ◽  
Tumor Regression ◽  
Surgical Excision ◽  
Tumor Formation ◽  
Rare Entity ◽  
Rare Presentation ◽  
Cutaneous Manifestations ◽  
Elderly Female

<b><i>Introduction:</i></b> Koenen tumors are benign, cutaneous manifestations of tuberous sclerosis. These are disfiguring, painful, and challenging to treat as they frequently recur. We report a case of long-standing, multiple Koenen tumors affecting all twenty nails in an elderly female who was successfully treated with a combination of topical sirolimus 1%, surgical excision, and electrofulguration. <b><i>Case Report:</i></b> A 57-year-old lady presented with multiple, asymptomatic periungual, and subungual tumors affecting all twenty nails since 27 years. Cutaneous examination revealed confetti macules, ash-leaf macule, and shagreen patch over trunk. Nail biopsy was compatible with Koenen’s tumor. Computerized tomography of brain showed diffuse patchy sclerosis. The tumors were treated with topical sirolimus 1% ointment for 10 months with excellent regression. Electro­fulguration for both great toenails and surgical excision of right thumbnail periungual fibroma was done. 1% sirolimus was advised after the surgical treatment. There were no adverse effects or recurrence of tumors over a 2-year follow-up. <b><i>Discussion:</i></b> Topical sirolimus 1% was effective in tumor regression and preventing new tumor formation. Larger tumors that interfered in daily chores were treated with excision and electrofulguration. Thus, a combination treatment for this rare presentation of tuberous sclerosis provided optimum results.

scholarly journals Carcinoma of Vagina in Utero-Vaginal Prolapse: A Rare Presentation

2012 ◽  
Vol 52 (186) ◽  
Author(s):  
S Acharya ◽  
DK Uprety
Keyword(s):  
Squamous Cell Carcinoma ◽  
Cell Carcinoma ◽  
Squamous Cell ◽  
Histopathological Examination ◽  
Large Cell ◽  
Uterovaginal Prolapse ◽  
Rare Entity ◽  
Rare Presentation ◽  
Vaginal Carcinoma ◽  
Keywords Squamous Cell Carcinoma

Primary vaginal carcinoma in uterovaginal prolapse is a rare entity. We report a case of an 84-years-old lady, who presented with long standing vaginal ulcer in association with third degree uterovaginal prolapse. Incisional biopsy was taken from the ulcer. Histopathological examination showed a large cell keratinizing squamous cell carcinoma. Keywords: Squamous cell carcinoma, uterovaginal prolapse, vaginal carcinoma.

scholarly journals Solitary Angiokeratoma of Oral Mucosa: A Rare Presentation

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Shilpa Kandalgaonkar ◽  
Suyog Tupsakhare ◽  
Ashok Patil ◽  
Gaurav Agrawal ◽  
Mahesh Gabhane ◽  
...  
Keyword(s):  
Oral Mucosa ◽  
Papillary Dermis ◽  
Common Denominator ◽  
Rare Entity ◽  
Epidermal Hyperplasia ◽  
Rare Presentation ◽  
Female Predominance ◽  
Mucosal Involvement ◽  
Chronic Irritation ◽  
Oral Involvement

Solitary angiokeratoma of oral mucosa is rare entity. The term Angiokeratoma is used to refer to several lesions, whose common denominator is the presence of dilated blood vessels in association with epidermal hyperplasia. Mucosal involvement, including oral cavity is occasionally found either as a component of the systemic variety, cutaneous involvement or isolated oral involvement. Clinically, the lesion is irregular, whitish to dark brown in color, with female predominance. The etiological factors include injury, trauma, or chronic irritation to the wall of a papillary dermis. Histologically, it is characterized by hyperkeratosis, acanthosis, and dilated vascular spaces with or without organizing thrombi in papillary dermis. The vascular spaces are partly or completely enclosed by elongated ret-ridges. Along with this reporting a case of solitary angiokeratoma affecting tongue in a 38-year-old male patient, along with the literature review is presented.

Adrenal pheochromocytoma with involvement of aorta and left renal artery: salvaged with adrenalectomy and nephrectomy

2021 ◽  
Vol 14 (9) ◽  
pp. e244297
Author(s):  
Shekhar Sathaye ◽  
Kalpesh Mahesh Parmar ◽  
Santosh Kumar ◽  
Pulkit Rastogi
Keyword(s):  
Renal Artery ◽  
Renal Involvement ◽  
Renal Tissue ◽  
Preoperative Imaging ◽  
Beta Blockade ◽  
Left Renal Artery ◽  
Rare Entity ◽  
Rare Presentation ◽  
Adrenal Pheochromocytoma

Large adrenal pheochromocytomas encasing the renal artery are a rare entity. The management of such challenging cases is surgical resection. The involvement of renal tissue and renal artery may necessitate meticulous dissection and concomitant nephrectomy. Here, we present a case of 41-year-old man diagnosed with left adrenal pheochromocytoma with complete encasement of left renal artery and partial encasement of aorta. Open left adrenalectomy and nephrectomy was performed after adequate preoperative optimisation. The patient is doing well at 6-month follow-up. Large adrenal pheochromocytoma with renal involvement is a rare presentation and requires optimal preoperative imaging, adequate preoperative alpha and beta blockade and meticulous surgical technique.

Pancreatic Carcinosarcoma with a Rare Presentation

2021 ◽  
Vol 156 (Supplement_1) ◽  
pp. S65-S66
Author(s):  
J Khan ◽  
S Guo
Keyword(s):  
Spindle Cell ◽  
Sarcomatoid Carcinoma ◽  
World Health ◽  
Rare Entity ◽  
Cell Component ◽  
Rare Presentation ◽  
Term Survival ◽  
Cytoplasmic Staining ◽  
Spindle Cell Component ◽  
Head Of The Pancreas

Abstract Introduction/Objective Carcino-sarcoma of the pancreas is a rare tumor and very limited clinical and pathologic data have been reported in the literature. As per World Health Organization (WHO) classification of tumors of the digestive system, the carcinosarcoma of the pancreas is classified together with sarcomatoid carcinoma and anaplastic giant cell carcinomas in undifferentiated carcinoma of pancreas. Carcinosarcoma is a rare entity with very poor prognosis. Methods/Case Report Here we report a rare case of pancreatic carcinosarcoma in a 68 year old male patient who underwent a pancreatoduodenectomy for unilocular cystic mass in the head of the pancreas. The mass grossly replaces the whole head of the pancreas. Histologically, the lesion showed a high-grade spindle cell component and adjacent moderately differentiated adenocarcinoma. On immunohistochemical examination, the carcinomatous component was positive for epithelial markers, and the sarcomatous component was positive for DOG1 and had a focal cytoplasmic staining for S-100. The diagnosis of pancreatic carcinosarcoma was rendered. Treatment options are same as of pancreatic carcinoma. Surgical resection is the best option available for patients. Systemic chemotherapy is indicated for patients with distant metastasis or patients with other contraindications. Despite surgery and adjuvant chemotherapy, recurrence rates are high, and prognosis is poor. However, there are no relevant standard chemotherapies available. Based on the limited number of reported cases, the prognosis of carcinosarcoma of the pancreas appears to be poor. But some cases with long term survival have been reported. There are very few primary pancreatic neoplasms with carcinomatous and sarcomatous components reported in the current literature. Results (if a Case Study enter NA) NA Conclusion This case highlights the importance of familiarity with histopathology of this rare entity, and to order proper immunohistochemical and molecular work-up when there is a suspicious abnormal spindle cell component.

scholarly journals Giant Synovial Cyst of Thigh: A Rare Entity

2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Kushagra Sinha ◽  
Rajesh Maheshwari ◽  
Atul Agrawal
Keyword(s):  
Knee Joint ◽  
Surgical Excision ◽  
Inflammatory Cells ◽  
Synovial Cyst ◽  
Rare Entity ◽  
The Past ◽  
Inflammatory Conditions ◽  
Precise Diagnosis ◽  
Synovial Cysts ◽  
Laboratory Investigations

Synovial cyst occurs secondary to traumatic, degenerative, or inflammatory conditions. Synovial cysts represent abnormal distension of bursae, which communicate with the joint. Giant synovial cysts are typically due to rheumatoid arthritis, other causes being trauma and synovial pseudoarthrosis. A 33-year-old male presented to an outpatient clinic with a massive swelling on his posterolateral aspect of right thigh extending from upper one-third to the knee joint which had been increasing in size over the past six months. This was associated with dull aching pain. All laboratory investigations were within normal parameters. Even FNAC was inconclusive. With time, swelling was increasing in size. Ultrasound revealed the cystic nature of swelling. MRI showed large cystic lesion 24 × 10 × 12 cm in posterolateral aspect of thigh extending up to knee joint. Following the MRI, an excision was planned. After excision, histological examination confirmed the synovial nature of the cyst, which had a collagenous wall and dense chronic inflammatory cells. As the disease is extremely rare and asymptomatic, precise diagnosis is difficult and often delayed. We consider that open surgical excision should be reserved for cases of large synovial cysts because it can provide a complete resection of the lesion and minimize the risk of recurrence.

scholarly journals Rare Presentation of Congenital Cystic Adenomatoid Malformation of the Lung

2016 ◽  
Vol 36 (1) ◽  
pp. 91-93
Author(s):  
Anubha Sharma ◽  
MS Pannu ◽  
Neeraj Lata ◽  
SPS Dhillon ◽  
Narinder Singh ◽  
...  
Keyword(s):  
Spontaneous Pneumothorax ◽  
Failure To Thrive ◽  
Congenital Cystic Adenomatoid Malformation ◽  
Rare Entity ◽  
Pectus Carinatum ◽  
Rare Presentation ◽  
Respiratory Difficulty ◽  
Cystic Adenomatoid Malformation

Congenital cystic adenomatoid malformation is a rare entity presenting with respiratory difficulty in newborns and even later in infancy. Various cases have been reported but recurrent spontaneous pneumothorax in an infant with failure to thrive and pectus carinatum since birth(with uneventful antenatal history and asymptomatic course in the first seven months of life) is an extremely rare presentation of this congenital lung condition.J Nepal Paediatr Soc 2016;36(1):91-93.

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