A case report of right atrial epithelioid hemangioendothelioma with multiple pulmonary metastases

2019 ◽  
Vol 14 (2) ◽  
pp. 173-178
Author(s):  
Xiaoming Zhou ◽  
Peng Li ◽  
Xiu Gu ◽  
Fushuang Zheng ◽  
Jungang Zhao ◽  
...  
Author(s):  
Gerhard van Wyk ◽  
Hellmuth Weich ◽  
Zirkia Joubert ◽  
Louis Johann de Jager ◽  
Kevin McCree ◽  
...  

Abstract Background Malignant primary cardiac neoplasms are rare and primary cardiac angiosarcoma is the most common and aggressive subtype. It most commonly presents in middle-aged males and due to its non-specific clinical presentation, the diagnosis is often delayed until advanced disease is already present. Clinical presentation is determined by manifestations of local infiltration or metastatic disease and making an early diagnosis is extremely challenging. Case summary A 15-year-old previously healthy boy was admitted to the emergency department with a history of pathological weight loss and functional decline. The patient was found to have a left-sided pneumothorax as well as bilateral diffusely spread pulmonary nodules on plain chest radiograph. Computed tomography chest confirmed widespread pulmonary metastases and a right atrial filling defect. Echocardiography revealed a right atrial tumour and transvenous endomyocardial biopsy of the tumour was done under fluoroscopic and echocardiographic guidance. A diagnosis of primary cardiac angiosarcoma was made. The patient demised shortly after presentation. Discussion Primary cardiac angiosarcoma is rare and even more so in patients as young as the case described. The diagnostic process poses several challenges to the clinician, of which the obtaining of a histological sample is one. This case report demonstrates aspects both unique and typical of this rare disease. It also describes an effective option for obtaining tissue for a histological diagnosis in patients whose clinical condition may not allow biopsy under general anaesthesia.


2021 ◽  
Vol 7 (1) ◽  
Author(s):  
Satoshi Takamori ◽  
Hiroyuki Oizumi ◽  
Jun Suzuki ◽  
Katsuyuki Suzuki

Abstract Background Repeat pulmonary metastasectomy (PM) considerably improves the prognosis of patients with pulmonary metastases of osteosarcoma. Reports have demonstrated a significantly improved prognosis in patients who have undergone repeat metastasectomy for osteosarcoma; however, there have been no reports with more than six metastasectomies. Herein, we describe the long-term survival of a patient following resection of multiple tumors and other treatments for metastatic osteosarcoma. Case presentation A 28-year-old woman underwent extensive resection and postoperative adjuvant chemotherapy for right tibial sarcoma. Over the years, she developed repeated pulmonary metastases. First, 116 metastases were removed from the bilateral lungs. After that, multiple PMs of approximately 250 tumors and other treatments for deep metastatic lesions were performed. The patient died of the underlying disease 24 years after the primary surgery. Conclusions This case report demonstrates the long-term survival benefit of a multidisciplinary treatment centered on multiple metastasectomies.


2017 ◽  
Vol 3 (1) ◽  
Author(s):  
Mayu Ono ◽  
Yoshio Kasuga ◽  
Takeshi Uehara ◽  
Yoshinao Oda

2009 ◽  
Vol 27 (1) ◽  
pp. 130-133 ◽  
Author(s):  
Rui Niimi ◽  
Akihiko Matsumine ◽  
Katsuyuki Kusuzaki ◽  
Ken Shintani ◽  
Tomoki Nakamura ◽  
...  

2019 ◽  
Vol 52 (4) ◽  
pp. 260-264
Author(s):  
David A. Suarez-Zamora ◽  
Paula A. Rodriguez-Urrego ◽  
Jose A. Hakim-Tawil ◽  
Mauricio A. Palau-Lazaro

2013 ◽  
Vol 24 (2) ◽  
pp. 374-375
Author(s):  
Ali Deniz ◽  
Mehmet Kanadasi ◽  
Nazan Ozbarlas

AbstractThe development of an aorta–right atrial fistula is a very rare complication of aortic isthmic atresia. We described a case of aorta–right atrial communication associated with isthmic atresia.


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