scholarly journals H10: Scleroderma or scleroedema? The complex classification of systemic sclerosis

2021 ◽  
Vol 185 (S1) ◽  
pp. 165-165
Keyword(s):  
2016 ◽  
Vol 27 (4) ◽  
pp. 614-617 ◽  
Author(s):  
Yuka Ikawa ◽  
Yasuhito Hamaguchi ◽  
Naoki Mugii ◽  
Takashi Matsushita ◽  
Kazuhiko Takehara

2018 ◽  
Vol 4 (1) ◽  
pp. 77-78
Author(s):  
Timothy Beukelman ◽  
Fenglong Xie ◽  
Ivan Foeldvari

Juvenile localised scleroderma is believed an orphan autoimmune disease, which occurs 10 times more often than systemic sclerosis in childhood and is believed to have a prevalence of 1 per 100,000 children. To gain data regarding the prevalence of juvenile localised scleroderma, we assessed the administrative claims data in the United States using the International Classification of Diseases, Ninth Revision diagnosis codes. We found an estimated prevalence in each year ranging from 3.2 to 3.6 per 10,000 children. This estimate is significantly higher as found in previous studies.


2016 ◽  
Vol 49 (5) ◽  
pp. 316-321 ◽  
Author(s):  
Andréa de Lima Bastos ◽  
Ricardo de Amorim Corrêa ◽  
Gilda Aparecida Ferreira

Abstract Currently, lung impairment is the leading factor responsible for the morbidity and mortality associated with systemic sclerosis. Therefore, the recognition of the various tomography patterns becomes decisive in the clinical management of these patients. In high-resolution computed tomography studies, the most common pattern is that of nonspecific interstitial pneumonia. However, there are other forms of lung involvement that must also be recognized. The aim of this study was to review the literature on the main changes resulting from pulmonary involvement in systemic sclerosis and the corresponding radiological findings, considering the current classification of interstitial diseases. We searched the Medline (PubMed), Lilacs, and SciELO databases in order to select articles related to pulmonary changes in systemic sclerosis and published in English between 2000 and 2015. The pulmonary changes seen on computed tomography in systemic sclerosis are varied and are divided into three main categories: interstitial, alveolar, and vascular. Interstitial changes constitute the most common type of pulmonary involvement in systemic sclerosis. However, alveolar and vascular manifestations must also be recognized and considered in the presence of atypical clinical presentations and inadequate treatment responses.


2011 ◽  
Vol 70 (6) ◽  
pp. 1074-1079 ◽  
Author(s):  
Tanja A Stamm ◽  
Malin Mattsson ◽  
Carina Mihai ◽  
Juliane Stöcker ◽  
Alexa Binder ◽  
...  

ObjectiveTo describe the experiences of people with systemic sclerosis (SSc) in different European countries of functioning and health and to link these experiences to the WHO International Classification of Functioning, Disability and Health (ICF) to develop a common understanding from a bio-psycho-social perspective.MethodA qualitative multicentre study with focus-group interviews was performed in four European countries: Austria, Romania, Sweden and Switzerland. The qualitative data analysis followed a modified form of ‘meaning condensation’ and the concepts that emerged in the analysis were linked to the ICF.Results63 people with SSc participated in 13 focus groups. In total, 86 concepts were identified. 32 (37%) of these were linked to the ICF component body functions and structures, 21 (24%) to activities and participation, 26 (30%) to environmental factors, 6 (7%) to personal factors and 1 (1%) to the health condition itself. 19 concepts (22%) were identified in all four countries and included impaired hand function, household activities, paid work, drugs, climate and coldness, support from others and experiences with healthcare institutions, non-pharmacological treatment, social security and benefits.ConclusionConcepts identified in all four countries could be used for guiding clinical assessment, as well as interdisciplinary team care and rheumatological rehabilitation for patients with SSc. For a full understanding of the aspects of the disease that were most relevant to people with SSc, people with SSc from multiple countries needed to be involved.


Author(s):  
Metin Akay ◽  
Yong Du ◽  
Cheryl L. Sershen ◽  
Minghua Wu ◽  
Ting Y. Chen ◽  
...  

2013 ◽  
Vol 33 (2) ◽  
pp. 207-214 ◽  
Author(s):  
Murray Baron ◽  
Lorinda Chung ◽  
Geneviève Gyger ◽  
Laura Hummers ◽  
Dinesh Khanna ◽  
...  

2004 ◽  
Vol 14 (3) ◽  
pp. 216-221 ◽  
Author(s):  
Emi Nishimagi ◽  
Yasushi Kawaguchi ◽  
Eiichi Tanaka ◽  
Masako Hara ◽  
Naoyuki Kamatani

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