Severe flucloxacillin-induced acute generalized exanthematous pustulosis (AGEP), with toxic epidermal necrolysis (TEN)-like features: does overlap between AGEP and TEN exist? Clinical report and review of the literature

2014 ◽  
Vol 171 (6) ◽  
pp. 1539-1545 ◽  
Author(s):  
S. van Hattem ◽  
G.I. Beerthuizen ◽  
S.H. Kardaun
Keyword(s):  
Toxic Epidermal Necrolysis ◽  
Clinical Report ◽  
Review Of The Literature ◽  
Acute Generalized Exanthematous Pustulosis ◽  
Exanthematous Pustulosis

scholarly journals First presentation of Sneddon-Wilkinson disease with unexpected immunoglobulin A gammopathy: A case report and review of the literature

2019 ◽  
Vol 7 ◽  
pp. 2050313X1982643
Author(s):  
Julia N Mayba ◽  
C Nicole Hawkins
Keyword(s):  
Clinical Presentation ◽  
Hematologic Malignancy ◽  
Topical Therapy ◽  
Immunoglobulin A ◽  
Lymphoproliferative Disorders ◽  
Review Of The Literature ◽  
First Line ◽  
Acute Generalized Exanthematous Pustulosis ◽  
Exanthematous Pustulosis ◽  
First Line Treatment

We present a case of Sneddon-Wilkinson disease in a 52-year-old female at her first presentation to dermatology. Outlined in the case are various investigations undertaken at this initial presentation, including rheumatologic and hematologic malignancy markers, which identified immunoglobulin A gammopathy. The systemic and topical therapies used to treat the patient’s condition are described, as well as her response to these treatments. In this discussion, we explain the epidemiology, pathophysiology, and clinical presentation of Sneddon-Wilkinson disease. Various medical conditions having known association with Sneddon-Wilkinson disease are discussed, including immunoglobulin A or immunoglobulin G monoclonal gammopathies and lymphoproliferative disorders. A comprehensive differential diagnosis for Sneddon-Wilkinson disease is provided, including immunoglobulin A pemphigus, acute generalized exanthematous pustulosis and pustular psoriasis, among others. We describe the systemic and topical therapy options for the treatment of Sneddon-Wilkinson disease, of which first line treatment is systemic dapsone. This patient serves as an excellent case of Sneddon-Wilkinson disease with unexpected immunoglobulin A gammopathy.

Acute generalized exanthematous pustulosis induced by hydroxychloroquine: Three cases and a review of the literature

2008 ◽  
Vol 30 (5) ◽  
pp. 930-940 ◽  
Author(s):  
Andrea Paradisi ◽  
Leonardo Bugatti ◽  
Teresa Sisto ◽  
Giorgio Filosa ◽  
Pier Luigi Amerio ◽  
...  
Keyword(s):  
Review Of The Literature ◽  
Acute Generalized Exanthematous Pustulosis ◽  
Exanthematous Pustulosis

Acute Generalized Exanthematous Pustulosis or Toxic Epidermal Necrolysis?

2010 ◽  
Vol 27 (5) ◽  
pp. 559-560
Author(s):  
OSCAR SUÁREZ-AMOR ◽  
MIGUEL CABANILLAS ◽  
BENIGNO MONTEAGUDO ◽  
AQUILINA RAMÍREZ-SANTOS ◽  
JAVIER PÉREZ-VALCÁRCEL ◽  
...  
Keyword(s):  
Toxic Epidermal Necrolysis ◽  
Acute Generalized Exanthematous Pustulosis ◽  
Exanthematous Pustulosis
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