Acute haemoperitoneum caused by ruptured extra‐adrenal paraganglioma

2020 ◽  
Author(s):  
Jae Im Lee ◽  
Su Lim Lee ◽  
Kyung Jin Seo
Keyword(s):  
Extra Adrenal Paraganglioma

Robotic-assisted interaortocaval dissection of an extra-adrenal paraganglioma in supine position via a trans-peritoneal approach

2019 ◽  
Author(s):  
Thierry Quackels ◽  
Simone Albisinni ◽  
Valerio Lucidi ◽  
Barbara Dessars ◽  
Natacha Driessens
Keyword(s):  
Supine Position ◽  
Robotic Assisted ◽  
Extra Adrenal Paraganglioma

scholarly journals Asymptomatic mediastinal extra-adrenal paraganglioma as a cause of sudden death: a case Report

2019 ◽  
Vol 14 (1) ◽  
pp. 564-567
Author(s):  
Qiancheng Xu ◽  
Yingya Cao ◽  
Hongzhen Yin ◽  
Rongrong Wu ◽  
Tao Yu ◽  
...  
Keyword(s):  
Blood Pressure ◽  
Case Report ◽  
Respiratory Failure ◽  
Pressure Drop ◽  
Thoracic Cavity ◽  
Severe Hypotension ◽  
Life Threatening ◽  
History Of ◽  
Posterior Mediastinal ◽  
Extra Adrenal Paraganglioma

AbstractA 23-year-old female patient was referred for treatment of a posterior mediastinal tumour. There was no history of hypertension or headache and no other complaints. The patient’s blood pressure increased to 210/125 mmHg after surgically manipulating the tumour, subsequently reversing to severe hypotension (25/15 mmHg) immediately after the tumour was removed. The life-threatening and irreversible blood pressure drop was difficult to treat with fluid and vasopressors, and the patient ultimately died of cardio-respiratory failure. Asymptomatic paraganglioma can be non-functional but can also be fatal. For any lump in the thoracic cavity, paraganglioma should be ruled out.

scholarly journals A First Case Report of Orbital Extra-Adrenal Paraganglioma in Cat

2021 ◽  
Vol 8 (5) ◽  
pp. 86
Author(s):  
Leonardo Leonardi ◽  
Raluca Ioana Rizac ◽  
Ilaria Pettinari ◽  
Luca Mechelli ◽  
Carlo De Feo
Keyword(s):  
Parasympathetic Nervous System ◽  
Neuron Specific Enolase ◽  
Final Diagnosis ◽  
Neuroendocrine Cells ◽  
Neuroendocrine Neoplasm ◽  
Glial Fibrillary Acid Protein ◽  
Veterinary Clinic ◽  
First Case ◽  
The Right ◽  
Extra Adrenal Paraganglioma

Paraganglioma is a rare neuroendocrine neoplasm originating from paraganglia and consisting of neuroendocrine cells of the sympathetic and parasympathetic nervous system. Extra-adrenal paraganglioma occurs with a low incidence in both humans and animals. This report presents the first case of paraganglioma in a cat with orbital primary location. An 18-year-old spayed female European domestic shorthair cat of 3.60 kg body weight was evaluated in a private veterinary clinic in Perugia, Italy, for a pronounced exophthalmos of the right eye. The cat underwent surgery for the enucleation of the right eye and of the mass. The biopsy samples of the removed tissue were fixed in 10% buffered neutral formalin for histological and immunohistochemical evaluations. Therefore, specific markers were used for immunohistochemical investigations, such as anti-neuron specific enolase (NSE), anti-synaptophysin, anti-glial fibrillary acid protein, anti-cytokeratin and anti-chromogranin. The results of these investigations allowed establishing the final diagnosis of ocular extra-adrenal paraganglioma of the cat.

A Case of Extra-Adrenal Paraganglioma Localized in Retroperitoneum Diagnosed With FDG-PET

2010 ◽  
Vol 20 (2) ◽  
pp. 60-62
Author(s):  
Banu Ozturk ◽  
Ugur Coskun ◽  
Emel Yaman ◽  
Ozgur Akdemir ◽  
Asli Cakir ◽  
...  
Keyword(s):  
Fdg Pet ◽  
Extra Adrenal Paraganglioma

Pheochromocytoma and Extra-adrenal Paraganglioma: Updates

2008 ◽  
Vol 132 (8) ◽  
pp. 1272-1284 ◽  
Author(s):  
Arthur S. Tischler
Keyword(s):  
World Health Organization ◽  
Medical Center ◽  
Genetic Defect ◽  
Tumor Location ◽  
Hereditary Disease ◽  
World Health ◽  
Adrenal Tumors ◽  
Endocrine Tumors ◽  
Health Organization ◽  
Extra Adrenal Paraganglioma

Abstract Context.—Advances in genetics and gene expression profiling have led to new ways of thinking about the pathobiology of pheochromocytoma and extra-adrenal paraganglioma. These developments are concurrent with the publication and dissemination of the 2004 World Health Organization bluebook on pathology and genetics of endocrine tumors. Objective.—To summarize new information required by pathologists for effective participation in patient management and research. Data Sources.—Literature review and primary material from Tufts Medical Center. Conclusions.—The World Health Organization reserves the term pheochromocytoma for tumors arising from chromaffin cells in the adrenal medulla. Closely related tumors in extra-adrenal sympathetic and parasympathetic paraganglia are classified as extra-adrenal paragangliomas. A pheochromocytoma is an intra-adrenal sympathetic paraganglioma. Although arbitrary, this nomenclature emphasizes important distinctive properties of intra-adrenal tumors, including an often adrenergic phenotype, relatively low rate of malignancy, and predilection to occur in particular hereditary syndromes. Malignancy is defined by presence of metastases not local invasion. Occult germline mutations characteristic of familial syndromes are now found in more than 20% of patients with apparently sporadic tumors, bringing the percentage of tumors with a known genetic basis close to 30%. In addition, tumor location and risk of malignancy vary with the underlying genetic defect. The “10 percent rule” for pheochromocytoma/paraganglioma—10% familial, 10% malignant, 10% extra-adrenal—is therefore no longer tenable. Current roles of pathology are limited to diagnosing primary or metastatic tumors and identifying features suggestive of malignant potential or hereditary disease. Future roles may involve more definitive assessment of malignancy, genotype-phenotype correlation, and identification of targets for therapy.

Carney Triad

2010 ◽  
pp. 806-816
Author(s):  
Edward C. Rosenow
Keyword(s):  
Gastrointestinal Stromal Tumor ◽  
Stromal Tumor ◽  
Identical Twin ◽  
Carney Triad ◽  
Pulmonary Chondroma ◽  
Extra Adrenal Paraganglioma

1. Pulmonary chondroma 2. Gastrointestinal stromal tumor (GIST), formerly, gastric epithelioid leiomyosarcoma 3. Functioning extra-adrenal paraganglioma • Triad eventually present in more than half of patients • 〉90% of patients are female • Mean age: 17 years • Mechanism: unknown (disease absent in 1 identical twin)...

Multifocal Extra-Adrenal Paraganglioma – Case Report

2015 ◽  
Vol 87 (7) ◽  
Author(s):  
Łukasz Dobosz ◽  
Małgorzata Dobrzycka ◽  
Paula Franczak ◽  
Jagoda Wieczorek ◽  
Grażyna Kobierska-Gulida ◽  
...  
Keyword(s):  
Nervous System ◽  
Case Report ◽  
Female Patient ◽  
Parasympathetic Nervous System ◽  
Treatment Method ◽  
Complete Resection ◽  
Rare Neoplasm ◽  
Extra Adrenal Paraganglioma

AbstractParaganglioma is a rare neoplasm originating from extra-adrenal pheochromocytes of the sympathetic and parasympathetic nervous system. It is usually benign and the treatment method of choice is a complete resection of the tumour. The authors present a case of 66-year-old female patient with a multifocal benign retroperitoneal paraganglioma, which was completely removed during surgery.

Orbital paraganglioma in a dog

2018 ◽  
Vol 46 (06) ◽  
pp. 410-415 ◽  
Author(s):  
Olivier Taeymans ◽  
Paola Monti ◽  
Emma Scurrell ◽  
Lina Eddicks ◽  
Kaspar Matiasek ◽  
...  
Keyword(s):  
Optic Nerve ◽  
Neuroendocrine Tumour ◽  
Neuron Specific Enolase ◽  
Resonance Imaging ◽  
Fine Needle Aspirate ◽  
Complete Excision ◽  
Orbital Mass ◽  
Pupillary Light ◽  
Extradural Neoplasm ◽  
Extra Adrenal Paraganglioma

SummaryA 10-year-old Rottweiler presented with right-sided moderately painful exophthalmia, blindness, absence of dazzle and pupillary light reflexes, a swollen optic nerve head and ventrolateral indentation of the globe. On magnetic resonance imaging, a 3 x 2 x 2 cm mass with a fluid filled center and contrast-enhancing periphery was noted posteriolateral of the globe. Orbital ultrasound was used for a guided fine needle aspirate of the mass. Cytology revealed moderate numbers of polygonal cells with lightly basophilic cytoplasm. Several cells showed nuclear pseudoinclusions. Histopathology following exenteration of the orbit revealed an infiltrative, extradural neoplasm surrounding the optic nerve. Cells were arranged in packets. Neoplastic cells were immunopositive for neuron specific enolase, synaptophysin and chromogranin A and immunonegative for cytokeratin. Findings were consistent with an extra-adrenal paraganglioma (neuroendocrine tumour). Although complete excision could not be confirmed on histopathology, the owners reported no apparent tumour recurrence 25 months after surgery. In conclusion a paraganglioma should be considered as a differential diagnosis of an orbital mass.

Pathology of Pheochromocytoma and Extra-adrenal Paraganglioma

2006 ◽  
Vol 1073 (1) ◽  
pp. 557-570 ◽  
Author(s):  
A. S TISCHLER ◽  
N. KIMURA ◽  
A. M. MCNICOL
Keyword(s):  
Extra Adrenal Paraganglioma
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