Spontaneous Intracranial Hypotension Masquerading as Frontotemporal Dementia

2008 ◽  
Vol 22 (6) ◽  
pp. 1035-1053 ◽  
Author(s):  
L. Walker ◽  
C. DeMeulemeester
Keyword(s):  
Frontotemporal Dementia ◽  
Intracranial Hypotension ◽  
Spontaneous Intracranial Hypotension

Behavioral Variant Frontotemporal Dementia as a Serious Complication of Spontaneous Intracranial Hypotension

2018 ◽  
Vol 15 (5) ◽  
pp. 505-515 ◽  
Author(s):  
Wouter I Schievink ◽  
M Marcel Maya ◽  
Zachary R Barnard ◽  
Franklin G Moser ◽  
Stacey Jean-Pierre ◽  
...  
Keyword(s):  
Frontotemporal Dementia ◽  
Intracranial Hypotension ◽  
Spontaneous Intracranial Hypotension ◽  
Csf Leak ◽  
Behavioral Variant Frontotemporal Dementia ◽  
Clinical Criteria ◽  
Epidural Blood Patching ◽  
Early Onset Dementia ◽  
Percutaneous Procedures ◽  
Brain Sagging

Abstract BACKGROUND Behavioral variant frontotemporal dementia (bvFTD) is a devastating early onset dementia. Symptoms of bvFTD may be caused by spontaneous intracranial hypotension (SIH), a treatable disorder, but no comprehensive study of such patients has been reported. OBJECTIVE To describe detailed characteristics of a large cohort of patients with SIH and symptoms of bvFTD. METHODS We identified patients with SIH who met clinical criteria for bvFTD. Patients were compared to a cohort of SIH patients without bvFTD. RESULTS The mean age for the 21 men and 8 women was 52.9 yr (range, 37–65 yr). All 29 patients with bvFTD symptoms had hypersomnolence. Magnetic resonance imaging showed brain sagging in all patients, cerebrospinal fluid (CSF) opening pressure low in about half of patients, but a spinal CSF leak could not be detected in any patient. All patients underwent epidural blood patching, but 26 patients eventually underwent 1 or more surgical procedures. Overall, a good outcome was obtained in 21 patients (72%); 20 (91%) of 22 patients who had not undergone prior Chiari surgery compared to 1 (14%) of 7 patients who did undergo Chiari surgery (P < .003). Compared to SIH patients without symptoms of bvFTD (n = 547), those with bvFTD symptoms were older, more often male, less often demonstrated CSF leak on spinal imaging, and more often underwent surgery (P < .02). CONCLUSION bvFTD in SIH is rare and associated with brain sagging and hypersomnolence. Spinal CSF leaks are rarely detected. bvFTD symptoms are often refractory to the usual percutaneous procedures but most patients can be cured.

Spontaneous intracranial hypotension causing reversible frontotemporal dementia

Neurology ◽  
2002 ◽  
Vol 59 (5) ◽  
pp. 787-787 ◽  
Author(s):  
R. A. Fishman ◽  
W. P. Dillon ◽  
N.L. Foster ◽  
M. Hong ◽  
G.V. Shah ◽  
...  
Keyword(s):  
Frontotemporal Dementia ◽  
Intracranial Hypotension ◽  
Spontaneous Intracranial Hypotension

Spontaneous intracranial hypotension causing reversible frontotemporal dementia

Neurology ◽  
2002 ◽  
Vol 58 (8) ◽  
pp. 1285-1287 ◽  
Author(s):  
M. Hong ◽  
G. V. Shah ◽  
K. M. Adams ◽  
R. S. Turner ◽  
N. L. Foster
Keyword(s):  
Frontotemporal Dementia ◽  
Intracranial Hypotension ◽  
Spontaneous Intracranial Hypotension

Postural headache due to spontaneous intracranial hypotension in an adolescent

2013 ◽  
Vol 44 (02) ◽  
Author(s):  
J Schönberger ◽  
M Möhlenbruch ◽  
KS Kang ◽  
A Seitz ◽  
H Bächli ◽  
...  
Keyword(s):  
Intracranial Hypotension ◽  
Spontaneous Intracranial Hypotension ◽  
Postural Headache

Radiologic Assessment of Spinal CSF Leakage in Spontaneous Intracranial Hypotension

1999 ◽  
Vol 41 (6) ◽  
pp. 1091
Author(s):  
Chang Jin Han ◽  
Ji Hyung Kim ◽  
Jang Sung Kim ◽  
Sun Yong Kim ◽  
Jung Ho Suh
Keyword(s):  
Intracranial Hypotension ◽  
Spontaneous Intracranial Hypotension ◽  
Radiologic Assessment ◽  
Csf Leakage
Sign in / Sign up

Export Citation Format

Share Document