scholarly journals Surgical creation of aortopulmonary window in selected patients with pulmonary atresia with poorly developed aortopulmonary collaterals and hypoplastic pulmonary arteries

2002 ◽  
Vol 123 (6) ◽  
pp. 1147-1154 ◽  
Author(s):  
Mark D. Rodefeld ◽  
V.Mohan Reddy ◽  
Lenardo D. Thompson ◽  
Sam Suleman ◽  
Phillip C. Moore ◽  
...  
Keyword(s):  
Pulmonary Arteries ◽  
Pulmonary Atresia ◽  
Aortopulmonary Window ◽  
Aortopulmonary Collaterals

Tetralogy of Fallot with pulmonary atresia associated with aortopulmonary window and major aortopulmonary collaterals

1995 ◽  
Vol 5 (3) ◽  
pp. 289-290 ◽  
Author(s):  
A. R. Bhagwat ◽  
R. J. Pinto ◽  
Satyavan Sharma
Keyword(s):  
Tetralogy Of Fallot ◽  
Pulmonary Atresia ◽  
Postoperative Recovery ◽  
Aortopulmonary Window ◽  
Descending Thoracic Aorta ◽  
Additional Source ◽  
Collateral Arteries ◽  
Arterial Blood ◽  
Aortopulmonary Collaterals ◽  
Major Aortopulmonary Collaterals

SummaryWe report a patient with tetralogy of Fallot and pulmonary atresia in whom the predominant extracardiac supply of arterial blood was via an aortopulmonary window. Major aortopulmonary collateral arteries originating from the descending thoracic aorta provided an additional source of pulmonary blood flow. The patient underwent successful correction and the postoperative recovery was uneventful.

Pulmonary Atresia, VSD in Association with Coronary-Pulmonary Artery Fistula

2007 ◽  
Vol 15 (4) ◽  
pp. 335-338 ◽  
Author(s):  
Hani K Najm ◽  
Neerod K Jha ◽  
Michael Godman ◽  
Mansour Al Mutairi ◽  
Ahmed I Rezk ◽  
...  
Keyword(s):  
Ventricular Septal Defect ◽  
Pulmonary Artery ◽  
Septal Defect ◽  
Pulmonary Arteries ◽  
Pulmonary Atresia ◽  
Left Pulmonary Artery ◽  
Corrective Surgery ◽  
Aortopulmonary Collaterals ◽  
One Year ◽  
Pulmonary Artery Fistula

Congenital coronary-pulmonary artery fistula is rare in patients with pulmonary atresia and ventricular septal defect. The nomenclature, physiological, clinical, and surgical implications of these fistulas are yet to be defined. We report a one-year-old child with pulmonary atresia, ventricular septal defect, and a right coronary-pulmonary artery fistula who also had a diminutive, disconnected left pulmonary artery in addition to aortopulmonary collaterals. The patient underwent corrective surgery. However, the fate of diminutive pulmonary arteries is unknown. The literature was reviewed to explore the clinical or surgical implications of such fistulas for improved understanding and management in the future.

Prenatal identification of the pulmonary arterial supply in tetralogy of Fallot with pulmonary atresia

2009 ◽  
Vol 19 (2) ◽  
pp. 185-191 ◽  
Author(s):  
Anna N. Seale ◽  
Siew Y. Ho ◽  
Elliot A. Shinebourne ◽  
Julene S. Carvalho
Keyword(s):  
Tetralogy Of Fallot ◽  
Pulmonary Arteries ◽  
Pulmonary Atresia ◽  
Postmortem Examination ◽  
Aortopulmonary Window ◽  
Cardiac Defect ◽  
Pulmonary Flow ◽  
Collateral Arteries ◽  
Arterial Duct ◽  
Pulmonary Arterial

AbstractObjectiveTo define the patterns of flow of blood to the lungs in fetuses with tetralogy of Fallot and pulmonary atresia.BackgroundIn this condition, supply of blood to the lungs is provided via an arterial duct or systemic-to-pulmonary collateral arteries, or very rarely through other conduits such as coronary arterial fistulas or an aortopulmonary window. The intrapericardial pulmonary arteries vary in size, and may be absent. These variables influence the prognosis and management.MethodsWe carried out a retrospective review of cases from a tertiary service for fetal cardiology, identifying all cases of tetralogy of Fallot with pulmonary atresia diagnosed antenatally between January, 1997, and April, 2006. We established pre- and postnatal outcomes, and compared the prenatal diagnosis with postnatal or autopsy findings.ResultsOf 6587 fetuses scanned during this period, 11 were diagnosed as having tetralogy of Fallot with pulmonary atresia and no other cardiac defect. In 5, arterial flow to the lungs was via an arterial duct, and in the other 6, the main identified source of flow was systemic-to-pulmonary collateral arteries. Of the latter 6 pregnancies, 4 were terminated, along with 3 of the 5 with ductal supply. The presence of systemic-to-pulmonary collateral arteries was confirmed at postmortem examination in 3 instances, and in the two delivered neonates, in neither of whom was an infusion of prostaglandin commenced.ConclusionThe patterns of pulmonary flow can be identified prenatally in the setting of tetralogy with pulmonary atresia. Supply through systemic-to-pulmonary collateral arteries impacts on counselling, introducing uncertainty regarding postnatal surgical management.

scholarly journals Pulmonary atresia with a ventricular septal defect and left pulmonary artery discontinuity: a case report 

2021 ◽  
Vol 15 (1) ◽  
Author(s):  
Hyun-Hwa Cha ◽  
Hae Min Kim ◽  
Won Joon Seong
Keyword(s):  
Pulmonary Artery ◽  
Subclavian Artery ◽  
Septal Defect ◽  
Left Subclavian Artery ◽  
Ductus Arteriosus ◽  
Main Pulmonary Artery ◽  
Pulmonary Arteries ◽  
Pulmonary Atresia ◽  
Left Pulmonary Artery ◽  
Right Pulmonary Artery

Abstract Background Unilateral pulmonary artery discontinuity is a rare malformation that is associated with other intracardiac abnormalities. Cases accompanied by other cardiac abnormalities are often missed on prenatal echocardiography. The prenatal diagnosis of isolated unilateral pulmonary artery discontinuity can also be delayed. However, undiagnosed this malformation would have an effect on further prognosis. We report our case of a prenatal diagnosis of pulmonary atresia with ventricular septal defect and left pulmonary artery discontinuity. Case presentation A 33-year-old Asian woman visited our institution at 24 weeks of gestation because of suspected fetal congenital heart disease. Fetal echocardiography revealed a small atretic main pulmonary artery giving rise to the right pulmonary artery without bifurcation and the left pulmonary artery arising from the ductus arteriosus originating from the left subclavian artery. The neonate was delivered by cesarean section at 376/7 weeks of gestation. Postnatal echocardiography and multidetector computed tomography showed a right aortic arch, with the small right pulmonary artery originating from the atretic main pulmonary artery and the left pulmonary artery originating from the left subclavian artery. Patency of the ductus arteriosus from the left subclavian artery was maintained with prostaglandin E1. Right ventricular outflow tract reconstruction and pulmonary angioplasty with Gore-Tex graft patch was performed 25th day after birth. Unfortunately, the neonate died because of right heart failure 8 days postoperation. Conclusion There is a possibility that both pulmonary arteries do not arise from the same great artery (main pulmonary artery or common arterial trunk). Therefore, clinicians should check the origin of both pulmonary arteries.

Visualization of the Pulmonary Arteries in the Patients with Pulmonary Atresia or Hypoplasia by Pulmonary Vein Wedge Angiography

1986 ◽  
Vol 16 (1) ◽  
pp. 19
Author(s):  
Dong Soo Kim ◽  
Jun Hee Sul ◽  
Sung Kyu Lee ◽  
Dong Shik Chin ◽  
Kyu Ok Choi ◽  
...  
Keyword(s):  
Pulmonary Vein ◽  
Pulmonary Arteries ◽  
Pulmonary Atresia

Chromosome 22q11 deletion in a patient with pulmonary atresia, intact ventricular septum, and confluent branch pulmonary arteries

2017 ◽  
Vol 28 (3) ◽  
pp. 467-470 ◽  
Author(s):  
Varun Aggarwal ◽  
Michaki Imamura ◽  
Carlos Acuna ◽  
Antonio G. Cabrera
Keyword(s):  
Pulmonary Stenosis ◽  
Pulmonary Arteries ◽  
Pulmonary Atresia ◽  
22Q11.2 Deletion Syndrome ◽  
Ventricular Septum ◽  
Deletion Syndrome ◽  
Intact Ventricular Septum ◽  
Chromosome 22Q11 ◽  
Chromosome 22Q11.2 ◽  
22Q11.2 Microdeletion

AbstractIn this study, we report a patient with pulmonary atresia with intact ventricular septum (PA/IVS), confluent pulmonary arteries supplied by an arterial duct, and chromosome 22q11.2 microdeletion. The 22q11.2 deletion syndrome has been associated with anomalies of the outflow tracts, such as tetralogy of Fallot with either pulmonary stenosis or atresia, but we are aware of a solitary case described with pulmonary atresia when the ventricular septum is intact. The presence of genetic malformations can have long-term co-morbidities. By describing our patient, we aim to create awareness of this rare association.

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