scholarly journals Type 1 Autoimmune Pancreatitis and IgG4-Related Sclerosing Cholangitis Is Associated With Extrapancreatic Organ Failure, Malignancy, and Mortality in a Prospective UK Cohort

2014 ◽  
Vol 109 (10) ◽  
pp. 1675-1683 ◽  
Author(s):  
Matthew T Huggett ◽  
E L Culver ◽  
M Kumar ◽  
J M Hurst ◽  
M Rodriguez-Justo ◽  
...  
2015 ◽  
Vol 2015 ◽  
pp. 1-6
Author(s):  
Allon Kahn ◽  
Anitha D. Yadav ◽  
M. Edwyn Harrison

IgG4-related disease is a relatively novel clinical entity whose gastrointestinal manifestations include type 1 autoimmune pancreatitis (AIP) and IgG4-associated sclerosing cholangitis. The presence of elevated serum IgG4 is suggestive but not essential for the diagnosis of type 1 AIP and is a pervasive feature of the proposed diagnostic criteria. The differential diagnosis of type 1 AIP includes malignant conditions, emphasizing the importance of a deliberate, comprehensive evaluation. Management of patients with a suggestive clinical presentation, but without serum IgG4 elevation, is difficult. Here we present three cases of IgG4-seronegative AIP and sclerosing cholangitis that responded to empiric steroid therapy and discuss approach considerations. These cases demonstrate the value of meticulous application of existing diagnostic algorithms to achieve a clinical diagnosis and avoid surgical intervention.


2018 ◽  
Vol 12 (3) ◽  
pp. 232-238 ◽  
Author(s):  
Yuichi Takano ◽  
Takahiro Kobayashi ◽  
Fumitaka Niiya ◽  
Eiichi Yamamura ◽  
Naotaka Maruoka ◽  
...  

2011 ◽  
Vol 6 (1) ◽  
pp. 82 ◽  
Author(s):  
Yoh Zen ◽  
Dimitrios P Bogdanos ◽  
Shigeyuki Kawa

Pancreas ◽  
2013 ◽  
Vol 42 (8) ◽  
pp. 1238-1244 ◽  
Author(s):  
Itaru Naitoh ◽  
Takahiro Nakazawa ◽  
Kazuki Hayashi ◽  
Katsuyuki Miyabe ◽  
Shuya Shimizu ◽  
...  

Pancreatology ◽  
2020 ◽  
Vol 20 (3) ◽  
pp. 318-324
Author(s):  
Koh Nakamaru ◽  
Takashi Tomiyama ◽  
Sanshiro Kobayashi ◽  
Manami Ikemune ◽  
Satoshi Tsukuda ◽  
...  

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