Combined Heart Transplantation and Total Replacement of Thoracic Aorta in Marfan's Syndrome With Recurrent Aortic Dissection: A Case Report

2012 ◽  
Vol 44 (4) ◽  
pp. 1174-1175 ◽  
Author(s):  
J. Wei ◽  
S.H. Sue ◽  
Y.T. Lee ◽  
C.Y. Chang
Keyword(s):  
Case Report ◽  
Aortic Dissection ◽  
Heart Transplantation ◽  
Thoracic Aorta ◽  
Marfan’S Syndrome ◽  
Marfan's Syndrome ◽  
Total Replacement

Multiple Aneurysms and Aortic Dissection: An Unusual Manifestation of Marfan's Syndrome

1994 ◽  
Vol 8 (4) ◽  
pp. 383-386 ◽  
Author(s):  
Christian de Virgilio ◽  
Kenneth J. Cherry ◽  
Hartzell V. Schaff
Keyword(s):  
Aortic Dissection ◽  
Marfan’S Syndrome ◽  
Marfan's Syndrome ◽  
Unusual Manifestation ◽  
Multiple Aneurysms

scholarly journals Marfan’s syndrome and other aortopathies in pregnancy

2013 ◽  
Vol 6 (3) ◽  
pp. 112-119 ◽  
Author(s):  
Fiona M Stewart
Keyword(s):  
Aortic Valve ◽  
Aortic Aneurysm ◽  
Aortic Dissection ◽  
Bicuspid Aortic Valve ◽  
Marfan’S Syndrome ◽  
Marfan's Syndrome ◽  
Risk Of Death ◽  
Type Iv ◽  
In Pregnancy ◽  
Aortic Dimensions

Aortopathies, or disease affecting the aorta, are associated with a significant mortality risk for the mother and foetus during pregnancy because of an increased rate of aortic dissection. The hereditary aortopathies; Marfan’s syndrome, bicuspid aortic valve, Loeys–Dietz syndrome, Ehlers–Danlos (type IV) syndrome, Turner’s syndrome and nonsyndromic familial thoracic aortic aneurysm and dissection are all associated with an increased risk of aortic dissection particularly during the third trimester and early postpartum period. Maternal outcome in pregnancy depends on the underlying disorder and the aortic dimensions prior to pregnancy. The foetus has up to 50% chance of inheriting the underlying genetic defect. Vasculitis, particularly Takayasu’s arteritis may also be a problem in pregnancy and predispose to aortic dissection. Prepregnancy review, including careful assessment of the aorta and prophylactic aortic surgery for an aortic aneurysm may reduce the risk of aortic dissection in pregnancy for some of the aortopathies but for women with Marfan’s syndrome, Loeys–Dietz syndrome and Ehlers–Danlos (vascular type IV) who have had surgery, the risk of death remains high. A subgroup of women with Marfan’s syndrome or a bicuspid aortic valve and normal aortic dimensions prepregnancy should do well in a pregnancy. Multidisciplinary pregnancy care with agreement on pregnancy follow-up, delivery and postpartum care with a crisis plan for an aortic dissection can improve pregnancy outcome and ensure prompt management of an aortic dissection should it occur.

scholarly journals Aortic dissection without Marfan's syndrome in ankylosing spondylitis

2004 ◽  
Vol 127 (2) ◽  
pp. 600-602 ◽  
Author(s):  
Hisato Takagi ◽  
Takayoshi Kato ◽  
Yukihiro Matsuno ◽  
Yukio Umeda ◽  
Yukiomi Fukumoto ◽  
...  
Keyword(s):  
Ankylosing Spondylitis ◽  
Aortic Dissection ◽  
Marfan’S Syndrome ◽  
Marfan's Syndrome

Scaphotrapezial Arthritis after a Carpometacarpal Fusion in a Patient with Marfan’s Syndrome: Case Report

2008 ◽  
Vol 33 (6) ◽  
pp. 806-809
Author(s):  
R. M. SZABO ◽  
B. PETERSON
Keyword(s):  
Case Report ◽  
Marfan’S Syndrome ◽  
Marfan's Syndrome ◽  
Web Space

We report a case of scaphotrapezial arthritis that developed in a patient with Marfan’s syndrome many years after a carpometacarpal fusion, which placed the thumb metacarpal in adduction. This problem was effectively treated with an abduction/opposition osteotomy, which both increased the patient’s first web space and improved her arthritic symptoms.

The roving aorta of Marfan's syndrome: A case report

1981 ◽  
Vol 4 (4) ◽  
pp. 249-250
Author(s):  
Michael R. Paling ◽  
Thomas H. Shawker ◽  
Gary L. Peck
Keyword(s):  
Case Report ◽  
Marfan’S Syndrome ◽  
Marfan's Syndrome
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