Atypical teratoid rhabdoid tumour of the leptomeninges in an adult: case report and literature review

Pathology ◽  
2017 ◽  
Vol 49 ◽  
pp. S132
Author(s):  
Sophie Corbett-Burns ◽  
Tamadur Mahasneh ◽  
Benjamin Jonker ◽  
Michael Edward Buckland
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Adult Case ◽  
Rhabdoid Tumour ◽  
Atypical Teratoid ◽  
Atypical Teratoid Rhabdoid Tumour

scholarly journals Intraventricular atypical teratoid rhabdoid tumour in an adult: a case report and literature review

2019 ◽  
Vol 57 (3) ◽  
pp. 295-300
Author(s):  
Vivien Chan ◽  
Alessandro Marro ◽  
Jonathan Chainey ◽  
Laura Schmitt ◽  
Sumit Das
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Rhabdoid Tumour ◽  
Atypical Teratoid ◽  
Atypical Teratoid Rhabdoid Tumour

Atypical teratoid rhabdoid tumour of the spine: report of a case and literature review

2014 ◽  
Vol 24 (S4) ◽  
pp. 472-484 ◽  
Author(s):  
Priyank Sinha ◽  
Maleeha Ahmad ◽  
Ann Varghese ◽  
Tejal Parekh ◽  
Azzam Ismail ◽  
...  
Keyword(s):  
Literature Review ◽  
Rhabdoid Tumour ◽  
Atypical Teratoid ◽  
Atypical Teratoid Rhabdoid Tumour

Primary spinal atypical teratoid/rhabdoid tumour presenting with hematomyelia and subarachnoid haemorrhage—a case report

2019 ◽  
Vol 36 (3) ◽  
pp. 655-659
Author(s):  
Rajesh Kumar Meena ◽  
Ramesh S. Doddamani ◽  
Harshad Chipde ◽  
Swati Mahajan ◽  
Sarat P. Chandra ◽  
...  
Keyword(s):  
Case Report ◽  
Subarachnoid Haemorrhage ◽  
Rhabdoid Tumour ◽  
Atypical Teratoid ◽  
Atypical Teratoid Rhabdoid Tumour

Atypical Teratoid/Rhabdoid Tumor of the Cerebellum in an Adult: Case Report and Literature Review

2021 ◽  
Vol 145 ◽  
pp. 57-63 ◽  
Author(s):  
Garret P. Greeneway ◽  
Paul S. Page ◽  
Viharkumar Patel ◽  
Azam S. Ahmed
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Rhabdoid Tumor ◽  
Atypical Teratoid Rhabdoid Tumor ◽  
Adult Case ◽  
Atypical Teratoid

Successful Multimodality Management of Atypical Teratoid/Rhabdoid Tumour of the Lower Dorsal Spine with Spinal Drop Metastasis: Illustrated Review

2021 ◽  
pp. 1-13
Author(s):  
Ahitagni Biswas ◽  
Umesh Velu ◽  
Seema Sharma ◽  
Kalpana Kumari ◽  
Mehar Chand Sharma ◽  
...  
Keyword(s):  
Smooth Muscle Actin ◽  
Primary Tumour ◽  
Complete Response ◽  
Malignant Cell ◽  
Conus Medullaris ◽  
Successful Outcome ◽  
Rhabdoid Tumour ◽  
Drop Metastasis ◽  
Atypical Teratoid ◽  
Atypical Teratoid Rhabdoid Tumour

<b><i>Introduction:</i></b> Spinal atypical teratoid/rhabdoid tumour (AT/RT) is exquisitely rare and constitutes 2% of all AT/RTs. <b><i>Case Presentation:</i></b> A 6-year-old boy presented with low backache for the last 5 months. MRI of the spine showed a 1.5 × 1.5 × 4.7 cm intradural extramedullary mass extending from D10 to D12, causing compression of the conus medullaris. With a preoperative diagnosis of ependymoma, a gross total resection (GTR) of tumour was performed. Post-operative histopathology showed AT/RT. The tumour cells were immunopositive for cytokeratin, epithelial membrane antigen, smooth muscle actin, and p53 and immunonegative for MIC2, desmin, glial fibrillary acidic protein, and INI1. Post-operative neuraxis MRI revealed post-operative changes (D10–D12) with a 9 mm enhancing lesion at L5-S1 junction suggesting drop metastasis. There was no lesion in brain. Cerebrospinal fluid cytology did not show any malignant cell. The metastatic work-up was normal. He received 3 cycles of chemotherapy with ICE regimen (ifosfamide, carboplatin, and etoposide). Subsequently, he received craniospinal irradiation (CSI)-36 Gy/20 fractions/4 weeks followed by focal boost to primary tumour bed and spinal drop metastasis-14.4 Gy/8 fractions/1.5 weeks. Thereafter, he received 3 more cycles of ICE regimen. End-of-treatment MRI spine showed post-op changes (D10–D12) and 38.9% reduction of the L5-S1 lesion suggesting partial response. Six monthly spinal MRI showed serial reduction of the metastatic lesion leading to complete response (CR) 1 year after completion of treatment. On last follow-up (30 months from the initial diagnosis), he was neurologically intact and in CR. <b><i>Conclusion:</i></b> Multimodality management comprising GTR of tumour, CSI followed by focal boost, and multiagent chemotherapy (ICE) can lead to successful outcome in patients with this rare and aggressive spinal tumour.

scholarly journals AT-17EPIDEMIOLOGY, MANAGEMENT AND OUTCOME OF CHILDHOOD ATYPICAL TERATOID/RHABDOID TUMOUR (ATRT) OF CENTRAL NERVOUS SYSTEM

2016 ◽  
Vol 18 (suppl 3) ◽  
pp. iii5.1-iii5
Author(s):  
Dennis Tak-Loi Ku ◽  
Matthew Ming-kong Shing ◽  
Kai-on Chang ◽  
Anthony Pak-yin Liu ◽  
Siu-keung Ling ◽  
...  
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Rhabdoid Tumour ◽  
Atypical Teratoid ◽  
Atypical Teratoid Rhabdoid Tumour
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