An unusual case of median arcuate ligament syndrome with inferior mesenteric artery supply to supra-mesocolic organs: A challenge in liver transplantation

Author(s):  
Giovanni Vennarecci ◽  
Daniele Ferraro ◽  
Luca Vaccaro ◽  
Giuseppe Maria Ettorre
Diagnostics ◽  
2020 ◽  
Vol 10 (2) ◽  
pp. 76
Author(s):  
Ryan P. Dyches ◽  
Kelsey J. Eaton ◽  
Heather F. Smith

Median arcuate ligament syndrome (MALS) is a rarely diagnosed condition resulting from compression of the celiac trunk (CT) by the median arcuate ligament (MAL) of the diaphragm. Ischemia due to reduced blood flow through the CT and/or neuropathic pain resulting from celiac ganglion compression may result in a range of gastrointestinal symptoms, including nausea, postprandial discomfort, and weight loss. However, the mechanism of compression and its anatomical correlates have been incompletely delineated. It has been hypothesized that CT angle of origination may be more acute in individuals with MALS. Here, frequency of anatomical variation in the MAL and CT were assessed in 35 cadaveric subjects (17M/18F), including the vertebral level of origin of CT and superior mesenteric artery (SMA), the distance between CT and MAL and SMA, the angles of origination of CT and SMA, the diameter at the CT base, and MAL/CT overlap. Females exhibited significantly higher rates of inferred MAL/CT overlap than males. Significant correlations were revealed between MAL/CT overlap and angles of origination of the CT and SMA. Vertebral level of origin of the CT in individuals with MAL/CT overlap was not significantly more superior than in those without. This study also revealed a significant relationship between MAL/CT overlap and angle of origination of the CT, which has clinical implications for understanding the anatomy associated with MALS.


2015 ◽  
Vol 38 (3) ◽  
pp. 379-382 ◽  
Author(s):  
Agata Arazińska ◽  
Michał Polguj ◽  
Andrzej Wojciechowski ◽  
Łukasz Trębiński ◽  
Ludomir Stefańczyk

Author(s):  
Maitane I Orue-Echebarria ◽  
◽  
Elena Sagarra ◽  
Sergio Carrasco ◽  
Benjamín Díaz-Zorita ◽  
...  

Arcuate ligament syndrome results from the compression of the celiac artery by the diaphragmatic fibers. It is asymptomatic in most cases and has an incidence of 2 to 24% of the population. In liver transplantation, it has great relevance, since it can be related to various postoperative complications. Case presentation


2016 ◽  
Vol 49 (4) ◽  
pp. 257-263 ◽  
Author(s):  
Leandro Cardarelli-Leite ◽  
Fernanda Garozzo Velloni ◽  
Priscila Silveira Salvadori ◽  
Marcelo Delboni Lemos ◽  
Giuseppe D'Ippolito

Abstract Abdominal vascular syndromes are rare diseases. Although such syndromes vary widely in terms of symptoms and etiologies, certain imaging findings are characteristic. Depending on their etiology, they can be categorized as congenital-including blue rubber bleb nevus syndrome, Klippel-Trenaunay syndrome, and hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber syndrome)-or compressive-including "nutcracker" syndrome, median arcuate ligament syndrome, Cockett syndrome (also known as May-Thurner syndrome), and superior mesenteric artery syndrome. In this article, we aimed to illustrate imaging findings that are characteristic of these syndromes, through studies conducted at our institution, as well as to perform a brief review of the literature on this topic.


2019 ◽  
Vol 5 (1) ◽  
Author(s):  
Haruhiko Okada ◽  
Kazuhisa Ehara ◽  
Hisashi Ro ◽  
Masaki Yamada ◽  
Tetsuya Saito ◽  
...  

Abstract Background Median arcuate ligament syndrome (MALS) is a rare clinical entity caused mainly by extrinsic compression of the celiac axis by the median arcuate ligament (MAL). Severe celiac artery stenosis can lead to the development of collateral circulation, aneurysms, and, rarely, superior mesenteric artery (SMA) dissection. The treatment of MALS involves the surgical release of the MAL. However, a standard procedure with the use of laparoscopy has not been established, and intraoperative complications can lead to severe vascular injury. Case presentation The patient was a 43-year-old man with MALS identified at the onset of SMA dissection. After treatment for the SMA dissection, he underwent laparoscopic MAL release. Using the technique of laparoscopic gastrectomy within the surgical field, we performed laparoscopic MAL release and ganglionectomy safely with a good view. Immediate symptomatic improvement was acquired, and no recurrence was observed at the 20-month follow-up. Conclusion We reported a rare case of MALS and SMA dissection. A horizontal 3D laparoscopic approach of the celiac axis allows for safe, meticulous, and radical MAL release and ganglionectomy.


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