Bickerstaff’s brainstem encephalitis with overlapping Guillain-Barré syndrome: Usefulness of sequential nerve conduction studies

2018 ◽  
Vol 40 (6) ◽  
pp. 507-511 ◽  
Author(s):  
Choong Yi Fong ◽  
Hnin Wint Wint Aung ◽  
Arie Khairani ◽  
Chin Seng Gan ◽  
Nortina Shahrizaila ◽  
...  
Keyword(s):  
Nerve Conduction ◽  
Nerve Conduction Studies ◽  
Guillain Barre Syndrome ◽  
Brainstem Encephalitis ◽  
Bickerstaff’S Brainstem Encephalitis ◽  
Guillain Barré Syndrome ◽  
Guillain Barré

SERIAL NERVE CONDUCTION STUDIES IN A GUILLAIN-BARRÉ SYNDROME VARIANT: THE EVOLUTION OF DEMYELINATING CHANGES

2015 ◽  
Vol 86 (11) ◽  
pp. e4.158-e4
Author(s):  
Catherine Morgan ◽  
Benjamin Wakerley ◽  
Geraint Fuller
Keyword(s):  
Nerve Conduction ◽  
Case Series ◽  
Pathological Process ◽  
Nerve Conduction Studies ◽  
Guillain Barre Syndrome ◽  
Facial Weakness ◽  
Guillain Barré Syndrome ◽  
Guillain Barré ◽  
Underlying Pathology ◽  
Serial Assessments

Guillain Barré syndrome (GBS) varies both in terms of clinical phenotype and underlying pathology. Serial assessments allow greater understanding of the pathophysiology. The evolution of neurophysiological changes is particularly helpful in distinguishing between demyelination and reversible axonal conduction failure.Bilateral facial weakness with distal paraesthesias is a rare subtype of GBS. In the largest case series 64% had abnormalities in motor and 27% in sensory conduction on single neurophysiological assessments; this was interpreted as a demyelinating neuropathy.We report an 18-year-old male with bilateral lower motor neurone facial weakness preceded by distal paraesthesias following a ‘flu-like illness. Examination of power and sensation was normal. Deep tendon reflexes were present. Cerebrospinal fluid showed albuminocytologic dissociation. By 6 weeks his facial weakness had almost completely resolved without treatment.Serial nerve conduction studies were performed. The first study (day 4) found prolonged distal motor latency and delayed F waves in posterior tibial and common peroneal nerves; normal sensory studies. Second study (day 18) found distal motor latencies and F waves had increased in upper and lower limb nerves. Third study (day 60) found improvement but abnormalities remained with changes similar to the first study.The neurophysiological changes became more marked while he improved clinically. These serial studies confirmed the primary pathological process of this GBS variant to be demyelination.

scholarly journals Misdiagnosed case of bicker staff brainstem encephalitis.

2019 ◽  
Vol 26 (08) ◽  
pp. 1386-1388
Author(s):  
Muhammad Haisum Maqsood ◽  
Kinza Rubab ◽  
Muhammad Zaigham Maqsood
Keyword(s):  
Informed Consent ◽  
Neurological Disease ◽  
Guillain Barre Syndrome ◽  
Brainstem Encephalitis ◽  
Atypical Case ◽  
Altered Sensorium ◽  
Bickerstaff’S Brainstem Encephalitis ◽  
Guillain Barré Syndrome ◽  
Guillain Barré

Bickerstaff’s brainstem encephalitis (BBE) is a rare neurological disease characterized by ophthalmoplegia, ataxia and altered sensorium.1 Its etiology is thought to be autoimmune in nature and sometimes certain infections precede illness.2-4 It is a spectrum of illnesses with Guillain-Barre Syndrome (GBS) and Miller Fischer Syndrome (MFS).5-6 We describe an atypical case of BBE which was initially misdiagnosed as meningo-encephalitis. As such, we report this case for its rarity. Informed consent was received from the patient before undertaking and reporting this study.

scholarly journals Guillain barre syndrome and its association with covid-19 infection – A clinical case series

2022 ◽  
Vol 7 (4) ◽  
pp. 326-333
Author(s):  
Madhavi Karri ◽  
Deepak Jacob ◽  
Balakrishnan Ramasamy ◽  
Santhosh Perumal
Keyword(s):  
Intravenous Immunoglobulin ◽  
Nerve Conduction ◽  
Cranial Nerves ◽  
Case Series ◽  
Nerve Conduction Studies ◽  
Guillain Barre Syndrome ◽  
Nasopharyngeal Swab ◽  
Neurological Manifestations ◽  
Guillain Barré Syndrome ◽  
Guillain Barré

A novel coronavirus (COVID-19) pandemic is caused by severe acute respiratory syndrome coronavirus 2 (SARs-CoV-2). This pandemic has been globally alarming in the current period. Several neurological manifestations are reported occurring with the infection. Guillain barre syndrome (GBS) or acute onset inflammatory polyradiculoneuropathy has been among the frequent manifestations observed among them. To know the pattern and outcome of GBS in COVID-19 affected individuals. We have taken six individuals admitted with flaccid quadriparesis in the last two months. All were affected recently by COVID 19 infection, which RT PCR of the nasopharyngeal swab confirmed. The study participants have undergone nerve conduction studies and have been diagnosed with Guillain Barre syndrome using Brighton criteria. We did cerebrospinal fluid (CSF) analysis after admission. We initiated all patients on Intravenous immunoglobulin according to body weight (2g/kg divided over five days). We used the Barthel index score to assess the outcome of the individuals. We observed a mean duration of 18.25 days between the COVID-19 infection and the onset of symptoms. Apart from motor quadriparesis and sensory symptoms being in common, we also noticed cranial nerves and autonomic involvement. We made the diagnosis using the nerve conduction studies and Brighton criteria. After initiating intravenous immunoglobulin, all patients had a good outcome, and quality of life was better after two months of follow up. Guillain Barre syndrome is one of the neurological manifestations of COVID-19 and has a dramatic response with intravenous immunoglobulin and better outcome with treatment.

Bickerstaff's brainstem encephalitis with monospecific anti-GT1a antibody: A subtype of Guillain–Barre syndrome

2021 ◽  
Vol 13 (1) ◽  
pp. 48-50
Author(s):  
Wan Yi Leong ◽  
Peck Kee Chia ◽  
Masita Arip ◽  
Liyana Najwa In Che Mat ◽  
Fan Kee Hoo ◽  
...  
Keyword(s):  
Guillain Barre Syndrome ◽  
Brainstem Encephalitis ◽  
Bickerstaff’S Brainstem Encephalitis ◽  
Guillain Barré Syndrome ◽  
Guillain Barré

scholarly journals Bickerstaff’s brainstem encephalitis: clinical features of 62 cases and a subgroup associated with Guillain–Barré syndrome

Brain ◽  
2003 ◽  
Vol 126 (10) ◽  
pp. 2279-2290 ◽  
Author(s):  
Masaaki Odaka ◽  
Nobuhiro Yuki ◽  
Mitsunori Yamada ◽  
Michiaki Koga ◽  
Toshihiko Takemi ◽  
...  
Keyword(s):  
Clinical Features ◽  
Guillain Barre Syndrome ◽  
Brainstem Encephalitis ◽  
Bickerstaff’S Brainstem Encephalitis ◽  
Guillain Barré Syndrome ◽  
Guillain Barré
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