Protein-Losing Enteropathy After the Modified Fontan Operation: Oral Prednisone Treatment with Biopsy and Laboratory Proved Improvement

1996 ◽  
Vol 17 (2) ◽  
pp. 115-117 ◽  
Author(s):  
T.M. Zellers ◽  
K. Brown
Keyword(s):  
Fontan Operation ◽  
Oral Prednisone ◽  
Protein Losing Enteropathy ◽  
Prednisone Treatment ◽  
Modified Fontan Operation

Conversion of the modified Fontan operation to total cavopulmonary connection: a treatment for protein-losing enteropathy

1997 ◽  
Vol 7 (3) ◽  
pp. 344-346 ◽  
Author(s):  
Gerd Stafanger ◽  
Gösta Pettersson ◽  
Joes Ramsøe Jacobsen
Keyword(s):  
Fontan Operation ◽  
Tricuspid Atresia ◽  
Total Cavopulmonary Connection ◽  
Protein Losing Enteropathy ◽  
Cavopulmonary Connection ◽  
Modified Fontan Operation

AbstractWe describe a patient with tricuspid atresia who, after a Fontan operation three years earlier, presented with severe protein-losing enteropathy. After conversion to a cavopulmonary connection, the symptoms regressed and substitution with albumin and immunoglobulin was no longer required.

scholarly journals Pathological and Immunological Approaches for a Patient Complicated with Protein-losing Enteropathy Following the Fontan Operation

2012 ◽  
Vol 28 (4) ◽  
pp. 224-229
Author(s):  
Kentaro Ueno ◽  
Hideaki Nakamura ◽  
Ryohei Gatayama ◽  
Sadamitsu Yanagi ◽  
Hideaki Ueda ◽  
...  
Keyword(s):  
Fontan Operation ◽  
Protein Losing Enteropathy

scholarly journals Protein-Losing Enteropathy and Plastic Bronchitis After the Fontan Operation

2018 ◽  
Vol 38 (6) ◽  
pp. e5-e12 ◽  
Author(s):  
Christine Peyton
Keyword(s):  
Heart Failure ◽  
Congestive Heart Failure ◽  
Complex Disease ◽  
Fontan Procedure ◽  
Fontan Operation ◽  
Venous Pressure ◽  
Venous Hypertension ◽  
Plastic Bronchitis ◽  
Protein Losing Enteropathy ◽  
Fontan Physiology

Protein-losing enteropathy and plastic bronchitis remain challenging to treat despite recent treatment advances. Protein-losing enteropathy and plastic bronchitis have been diagnosed in patients with cardiomyopathy, constrictive pericarditis, and congestive heart failure. This article focuses on patients with protein-losing enteropathy or plastic bronchitis following the Fontan procedure. Patients with single-ventricle physiology who have undergone the Fontan procedure are at risk for these conditions. Fontan physiology predisposes patients to chronically low cardiac output, increased central venous pressure, and congestive heart failure. These altered hemodynamics lead to increased mesenteric vascular resistance, resulting in venous hypertension and congestion in protein-losing enteropathy. Plastic bronchitis is a complex disease in which chronic high lymphatic pressures from Fontan physiology cause acellular bronchial casts to develop. These entities may also occur in patients with normal Fontan hemodynamics. This article also covers medical and surgical interventions for protein-losing enteropathy and plastic bronchitis. (Critical Care Nurse. 2018;38[6]:e5–e12)

scholarly journals Atrial pacing: An alternative treatment for protein-losing enteropathy after the Fontan operation

2001 ◽  
Vol 121 (3) ◽  
pp. 582-583 ◽  
Author(s):  
Mitchell I. Cohen ◽  
Larry A. Rhodes ◽  
Gil Wernovsky ◽  
J.William Gaynor ◽  
Thomas L. Spray ◽  
...  
Keyword(s):  
Alternative Treatment ◽  
Fontan Operation ◽  
Atrial Pacing ◽  
Protein Losing Enteropathy

Current treatment options for the Failing Fontan Circulation

2022 ◽  
Vol 18 ◽  
Author(s):  
Bart. W. Driesen ◽  
Michiel Voskuil ◽  
Heynric B. Grotenhuis
Keyword(s):  
Myocardial Dysfunction ◽  
Fontan Procedure ◽  
Treatment Options ◽  
Fontan Operation ◽  
Current Treatment ◽  
Fontan Circulation ◽  
Protein Losing Enteropathy ◽  
Resistance Protein ◽  
Failing Fontan

Abstract: The Fontan operation was introduced in 1968. For congenital malformations where biventricular repair is not suitable, the Fontan procedure has provided a long-term palliation strategy with improved outcome compared to the initially developed procedures. Despite these improvements, several complications merely as a result of a failing Fontan circulation (including myocardial dysfunction, arrhythmias, increased pulmonary vascular resistance, protein losing enteropathy, hepatic dysfunction, plastic bronchitis and thrombo-embolism) will limit life-expectancy in this patient cohort. This review provides an overview of the most common complications of the Fontan circulation and the currently available treatment options.

scholarly journals Contractility–Afterload Mismatch in Patients With Protein-Losing Enteropathy After the Fontan Operation

2014 ◽  
Vol 35 (7) ◽  
pp. 1225-1231 ◽  
Author(s):  
Hideto Ozawa ◽  
Takayoshi Ueno ◽  
Shigemitsu Iwai ◽  
Hiroaki Kawata ◽  
Kyouichi Nishigaki ◽  
...  
Keyword(s):  
Fontan Operation ◽  
Protein Losing Enteropathy
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