Two staged Starnes operation for Ebstein’s anomaly with pulmonary atresia in early infancy —A report of a successful case—

1998 ◽  
Vol 46 (11) ◽  
pp. 1200-1205 ◽  
Author(s):  
Masanobu Maeda ◽  
Noboru Sai ◽  
Ken Miyahara ◽  
Hajime Sakurai ◽  
Masato Nakayama ◽  
...  
Keyword(s):  
Pulmonary Atresia ◽  
Early Infancy ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Successful Case

Point ablation for macro-reentrant ventricular tachycardia associated with Ebstein’s anomaly and pulmonary atresia: a case report

2020 ◽  
pp. 1-3
Author(s):  
Keiko Toyohara ◽  
Yasuko Tomizawa ◽  
Morio Shoda
Keyword(s):  
Ventricular Tachycardia ◽  
Case Report ◽  
Catheter Ablation ◽  
Right Ventricle ◽  
Low Voltage ◽  
Pulmonary Atresia ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Slow Conduction ◽  
Hypoplastic Right Ventricle

Abstract We report a case with Ebstein’s anomaly and pulmonary atresia with sustained monomorphic ventricular tachycardia in a patient without a ventriculotomy history. In the low voltage area between the atrialised right ventricle and hypoplastic right ventricle, there was a ventricular tachycardia substrate and slow conduction. The tachycardia circuit was eliminated by a point catheter ablation at the area with diastolic fractionated potentials.

Surgical management of symptomatic neonates with Ebstein’s anomaly: choice of operation

2014 ◽  
Vol 25 (6) ◽  
pp. 1119-1123 ◽  
Author(s):  
Christopher J. Knott-Craig ◽  
Thittamaranahalli Kariyappa S. Kumar ◽  
Alejandro R. Arevalo ◽  
Vijaya M. Joshi
Keyword(s):  
Pulmonary Artery ◽  
Right Ventricle ◽  
Surgical Management ◽  
Single Ventricle ◽  
Pulmonary Atresia ◽  
Early Mortality ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly ◽  
Single Ventricle Palliation ◽  
Artery Conduit

AbstractObjective:Symptomatic neonates with Ebstein’s anomaly pose significant challenge. Within this cohort, neonates with associated anatomical pulmonary atresia have higher mortality. We review our experience with this difficult subset.Methods:A total of 32 consecutive symptomatic neonates with Ebstein’s anomaly underwent surgical intervention between 1994 and 2013. Of them, 20 neonates (62%, 20/32) had associated pulmonary atresia. Patients’ weights ranged from 1.9 to 3.4 kg. All patients without pulmonary atresia had two-ventricle repair. Of the 20 neonates, 16 (80%, 16/20) with Ebstein’s anomaly and pulmonary atresia had two-ventricle repair and 4 had single-ventricle palliation, of which 2 underwent Starnes’ palliation and 2 Blalock–Taussig shunts. Six recent patients with Ebstein’s anomaly and pulmonary atresia had right ventricle to pulmonary artery valved conduit as part of their two-ventricle repair.Results:Overall early mortality was 28% (9/32). For those without pulmonary atresia, mortality was 8.3% (1/12). For the entire cohort of neonates with Ebstein’s anomaly and pulmonary atresia, mortality was 40% (8/20; p=0.05). Mortality for neonates with Ebstein’s anomaly and pulmonary atresia having two-ventricle repair was 44% (7/16). Mortality for neonates with Ebstein’s anomaly and pulmonary atresia having two-ventricle repair utilising right ventricle to pulmonary artery conduit was 16% (1/6). For those having one-ventricle repair, the mortality was 25% (1/4).Conclusions:Surgical management of neonates with Ebstein’s anomaly remains challenging. For neonates with Ebstein’s anomaly and anatomical pulmonary atresia, single-ventricle palliation is associated with lower early mortality compared with two-ventricle repair. This outcome advantage is negated by inclusion of right ventricle to pulmonary artery conduit as part of the two-ventricle repair.

scholarly journals Ebstein’s anomaly with ‘reversible’ functional pulmonary atresia

2019 ◽  
Vol 12 (12) ◽  
pp. e229809
Author(s):  
João Rato ◽  
Ana R Sousa ◽  
Ana Teixeira ◽  
Rui Anjos
Keyword(s):  
Pulmonary Valve ◽  
Ductus Arteriosus ◽  
Pulmonary Atresia ◽  
Ebstein’S Anomaly ◽  
Peripheral Oxygen Saturation ◽  
Pulmonic Valve ◽  
Ebstein's Anomaly ◽  
Chest X Ray ◽  
Team Decision

We present the case of an infant with prenatal diagnosis, at 32 weeks gestation, of Ebstein’s anomaly without anterograde flow from right ventricular to pulmonary atresia (PA)—functional PA with flow reversal in the ductus arteriosus. Prostaglandin E1 was started after birth. Chest X-ray showed severe cardiomegaly and echocardiogram confirmed Ebstein’s anomaly with a thickened non-opening pulmonary valve without anterograde flow but with mild regurgitation. Multidisciplinary team decision was to progressively reduce prostaglandins and have an expectant attitude. Peripheral oxygen saturation above 85% was maintained and serial echocardiograms documented progressive reduction of the ductus arteriosus and the opening of the pulmonic valve cusps, with the development of anterograde flow. The newborn was discharged at day 19 of life without the need for any intervention, and at last follow-up remains asymptomatic, with anterograde normal flow in the pulmonary valve.

Biventricular Repair of Ebstein's Anomaly With Pulmonary Atresia in a Low Birth Weight Neonate

2006 ◽  
Vol 21 (4) ◽  
pp. 421-422 ◽  
Author(s):  
Yuji Hiramatsu ◽  
Mio Noma ◽  
Hitoshi Horigome ◽  
Miho Takahashi-Igari ◽  
Yuzuru Sakakibara
Keyword(s):  
Birth Weight ◽  
Low Birth Weight ◽  
Pulmonary Atresia ◽  
Ebstein’S Anomaly ◽  
Biventricular Repair ◽  
Ebstein's Anomaly ◽  
Birth Weight Neonate

Prenatal echocardiographic diagnosis of Ebstein's anomaly with pulmonary atresia

1983 ◽  
Vol 147 (3) ◽  
pp. 300-303 ◽  
Author(s):  
Mordechai Sharf ◽  
Edward G. Abinader ◽  
Israel Shapiro ◽  
Tiberiu Rosenfeld ◽  
Izu Eibschitz
Keyword(s):  
Pulmonary Atresia ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly

Ebstein's Anomaly With or Without Pulmonary Atresia: Differential Diagnosis by Fetal Echocardiography

1989 ◽  
Vol 6 (6) ◽  
pp. 509-515 ◽  
Author(s):  
GENGI SATOMI ◽  
SUSUMU KANDA ◽  
HIROSHI KATAYAMA ◽  
SATOSHI YASUKOHCHI ◽  
KENJI NAKAMURA ◽  
...  
Keyword(s):  
Differential Diagnosis ◽  
Fetal Echocardiography ◽  
Pulmonary Atresia ◽  
Ebstein’S Anomaly ◽  
Ebstein's Anomaly
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