Developmental mechanism of splenomegaly and portal hypertension in non-cirrhotic peri-portal fibrosis with splenomegaly (so-called Banti’s syndrome)

1973 ◽  
Vol 8 (2) ◽  
pp. 115-130 ◽  
Author(s):  
Toshio Sato ◽  
Kenji Koyama ◽  
Hidemi Yamauchi
Keyword(s):  
Portal Hypertension ◽  
Portal Fibrosis ◽  
Developmental Mechanism ◽  
Banti's Syndrome

scholarly journals CHARACTERIZATION OF PORTAL HYPERTENSION IN GEZIRASTATE (SUDAN) USING ULTRASOUND

2019 ◽  
Vol 7 (7) ◽  
pp. 30-38
Author(s):  
Abdal Gadir Yonis ◽  
Al Safi Ahmed Abdallash ◽  
Mona Ahmed ◽  
Ashraf Mustafa Mohammed Osman
Keyword(s):  
Portal Hypertension ◽  
Endemic Area ◽  
Imaging Modality ◽  
Frequency Range ◽  
Portal Fibrosis ◽  
Portable Ultrasound ◽  
Schistosomiasis Mansoni ◽  
High Incidence ◽  
A Prospective Study

Peri-sinusoidal portal hypertension with frequent episodes of upper gastro intestinal variceal bleeding are hallmarks of hepatic-splenic schistosomiasis (Mansoni or Japonicum). This a prospective study compromise of 306 consecutive patients at North Gezira State between 2016 to 2019, aimed to characterize the portal hypertension &to minimize potentiallysevere and deadly complications. Using  B-mode grayscale ultrasound, The images done by portable Sono- Scape- A6 machine using convex probe with frequency range from 3.5 to 5 MHz and the data analyzed by SPSS version 15.The result showed that the majority of patients were male and portal hypertension had high incidence associated with peri portal fibrosis(schistosomiasis), the result also showed that : out of 360 patients under study, there were 209(58.1%) had portal hypertension, 106(29.4%) had PPF, and 45(12.5%) were normal patients.  The study concluded that the portable ultrasound machine is the most frequently used imaging modality to assess patients for the presence of portal hypertension especially in the endemic area.

Non-cirrhotic portal fibrosis (idiopathic portal hypertension): Experience with 151 patients and a review of the literature

2002 ◽  
Vol 17 (1) ◽  
pp. 6-16 ◽  
Author(s):  
RADHA KRISHAN DHIMAN ◽  
YOGESH CHAWLA ◽  
RAKESH KUMAR VASISHTA ◽  
NANDITA KAKKAR ◽  
JANG BAHADUR DILAWARI ◽  
...  
Keyword(s):  
Portal Hypertension ◽  
Idiopathic Portal Hypertension ◽  
Review Of The Literature ◽  
Portal Fibrosis

scholarly journals Banti's Syndrome without Portal Hypertension

1966 ◽  
Vol 88 (2) ◽  
pp. 135-152 ◽  
Author(s):  
Toshio Sato ◽  
Yasuo Suda ◽  
Goro Kakizaki ◽  
Hidemi Yamauchi
Keyword(s):  
Portal Hypertension ◽  
Banti's Syndrome

Portal hemodynamics in idiopathic portal hypertension (Banti's syndrome)

1987 ◽  
Vol 92 (3) ◽  
pp. 751-758 ◽  
Author(s):  
Kunihiko Ohnishi ◽  
Masayuki Saito ◽  
Shinichi Sato ◽  
Hidetaka Terabayashi ◽  
Shinji Iida ◽  
...  
Keyword(s):  
Portal Hypertension ◽  
Idiopathic Portal Hypertension ◽  
Portal Hemodynamics ◽  
Banti's Syndrome

scholarly journals Non-cirrhotic portal hypertension: current concepts and modern management

2016 ◽  
Vol 43 (3) ◽  
pp. 170-176
Author(s):  
Md Ismail Patwary ◽  
Matiur Rahman ◽  
Kaushik Mojumder
Keyword(s):  
Portal Hypertension ◽  
Portal Vein ◽  
Variceal Bleeding ◽  
Gastric Varices ◽  
Idiopathic Portal Hypertension ◽  
Endoscopic Sclerotherapy ◽  
Cyanoacrylate Glue ◽  
Portal Fibrosis ◽  
Vascular Origin ◽  
Glue Injection

Non-cirrhotic portal hypertension (NCPH) is a heterogeneous group of liver disorders of vascular origin, leading to portal hypertension (PHTN) in the absence of cirrhosis.The lesions are generallyvascular, either in the portal vein, its branches or in the peri-sinusoidal area. The majority of diseases included in the category of NCPH are well-characterized disease entities where PHTN is a late manifestation. Two diseases that present only with features of PHTN and are common in developing countries are non-cirrhotic portal fibrosis (NCPF) and extrahepatic portal vein obstruction (EHPVO). Non-cirrhotic portal fibrosis is a syndrome of obscure etiology, characterized by ‘obliterative-portovenopathy’ leading to PHT, massive splenomegaly and well-tolerated episodes of variceal bleeding in young adults from low socioeconomic backgrounds, having near normal hepatic functions. In some parts of the world, NCPFis called idiopathic portal hypertension in Japan or ‘hepatoportalsclerosis’in USA. Because 85–95% of patient with NCPF and EHPVO present with variceal bleeding, treatment involves management with endoscopic sclerotherapy (EST) or variceal ligation (EVL). These therapies are effective in approximately 90–95% of patients. Gastric varices are another common cause of upper gastrointestinal bleeding in these patients and these can be managed with cyanoacrylate glue injection or surgery. The prognosis of patients with NCPF is good and 5 years survival in patients in whom variceal bleeding can be controlled has been reported to be approximately 95–100%.Bangladesh Med J. 2014 Sep; 43 (3): 170-176

scholarly journals Ultrastructure of the liver in non-cirrhotic portal fibrosis with portal hypertension

Gut ◽  
1970 ◽  
Vol 11 (11) ◽  
pp. 905-910 ◽  
Author(s):  
B. N. Tandon ◽  
R. Lakshminarayanan ◽  
S. Bhargava ◽  
N. C. Nayak ◽  
S. K. Sama
Keyword(s):  
Portal Hypertension ◽  
Portal Fibrosis

scholarly journals Banti’s Syndrome Presenting as Hematemesis - A Case Report

2021 ◽  
Vol 10 (10) ◽  
pp. 749-751
Author(s):  
Aishwarya Ghule ◽  
Sourya Acharya ◽  
Samarth Shukla ◽  
Sunil Kumar ◽  
Parth Godhiwala
Keyword(s):  
Portal Hypertension ◽  
Portal Pressure ◽  
Normal Liver ◽  
Liver Function Tests ◽  
Massive Bleeding ◽  
Idiopathic Portal Hypertension ◽  
Hepatic Veins ◽  
Massive Splenomegaly ◽  
History Of ◽  
Banti's Syndrome

Massive splenomegaly presenting with hypersplenism, pancytopenia and portal hypertension, without any underlying known cause is known as Banti’s syndrome. There are various causes of splenomegaly. When all the known causes of portal hypertension are ruled out, it is termed as Banti’s syndrome. This syndrome was discovered by Guido Banti in 1882 and is named after him. Banti’s syndrome is also known as idiopathic portal hypertension or non-cirrhotic portal fibrosis.1 Banti’s syndrome is commonly found in India and Japan than in the West. 2 There is absence of any haematologic cause, primary hepatic cause or any tumour or mass lesion involving the spleen. Banti had stated that the primary organ involved was spleen and not the liver leading to secondary splenomegaly. Other features include normal liver function tests, varices seen in endoscopy, cytopenia of one or more cell lines, absence of cirrhosis, patent hepatic veins and elevated portal pressure with multiple collaterals. The complications include rupture of varices and massive bleeding. 3 We report a case of a 20-year-old male who presented to us with a history of fever for 7 days and one-episode of hematemesis on the day of admission. All known causes of hypersplenism were ruled out and he was diagnosed to have idiopathic massive splenomegaly with portal hypertension and hypersplenism.

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