Demonstration of ascending aorta in hypoplastic left heart syndrome with aortic atresia by balloon occlusion aortography

1987 ◽  
Vol 17 (5) ◽  
pp. 370-372 ◽  
Author(s):  
R. N. S. Lo ◽  
M. P. Leung ◽  
K. C. Lau
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Balloon Occlusion ◽  
Ascending Aorta ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Aortic Atresia ◽  
Left Heart Syndrome

scholarly journals Assessment of Structural and Functional Abnormalities of the Myocardium and the Ascending Aorta in Fetus with Hypoplastic Left Heart Syndrome

2016 ◽  
Vol 2016 ◽  
pp. 1-9
Author(s):  
Yan Jiang ◽  
Yali Xu ◽  
Jinliang Tang ◽  
Hongmei Xia
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Left Ventricular ◽  
Ascending Aorta ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Histological Changes ◽  
Left Heart Syndrome ◽  
Rv Function ◽  
Normal Controls ◽  
Pulmonary Artery Diameter

Aims. To detect anatomical and intrinsic histopathological features of the ascending aorta and left ventricular (LV) myocardium and evaluate right ventricular (RV) function in fetuses with hypoplastic left heart syndrome (HLHS).Methods. Twenty-five fetuses diagnosed with HLHS were followed up in the antenatal and postpartum periods. 12 necropsy heart specimens were analyzed for morphological and histological changes.Results. Prenatal echocardiography and pathologic anatomy displayed the typical characteristics of HLHS as a severe underdevelopment of the LV in the form of mitral stenosis or atresia or as aortic atresia or stenosis, with a decreased ratio of aortic diameter to pulmonary artery diameter (median of 0.49 with a range of 0.24 to 0.69,p≤0.001) and a higher ratio of RV diameter to LV diameter (median of 2.44 with a range of 1.33 to 6.25,p≤0.001). The RV volume, stroke volume, and cardiac output in HLHS fetuses were increased compared with the gestational age-matched normal controls (p<0.01). Histological changes in the 12 HLHS specimens included LV myocardial fibrosis, aortic elastic fragmentation, and fibrosis.Conclusions. In addition to severe anatomical deformity, distinct histological abnormalities in the LV myocardium and aortic wall were identified in the fetuses with HLHS. RV function damage may be potentially exists.

Impact of Mitral Stenosis and Aortic Atresia on Survival in Hypoplastic Left Heart Syndrome

2008 ◽  
Vol 85 (6) ◽  
pp. 2057-2062 ◽  
Author(s):  
Jenifer A. Glatz ◽  
Raymond T. Fedderly ◽  
Nancy S. Ghanayem ◽  
James S. Tweddell
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Mitral Stenosis ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Aortic Atresia ◽  
Left Heart Syndrome

Mitral Stenosis and Aortic Atresia in Hypoplastic Left Heart Syndrome: Survival Analysis After Stage I Palliation

2010 ◽  
Vol 90 (5) ◽  
pp. 1599-1608 ◽  
Author(s):  
Shyam K. Sathanandam ◽  
Anastasios C. Polimenakos ◽  
David A. Roberson ◽  
Chawki F. elZein ◽  
Andrew Van Bergen ◽  
...  
Keyword(s):  
Survival Analysis ◽  
Hypoplastic Left Heart Syndrome ◽  
Mitral Stenosis ◽  
Stage I ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Aortic Atresia ◽  
Left Heart Syndrome

Acute ischaemic heart block in hypoplastic left heart syndrome

2014 ◽  
Vol 26 (1) ◽  
pp. 151-154
Author(s):  
Dale A. Burkett ◽  
Neil Wilson ◽  
Max B. Mitchell ◽  
Adel K. Younoszai
Keyword(s):  
Hypoplastic Left Heart Syndrome ◽  
Heart Block ◽  
Ascending Aorta ◽  
Left Heart ◽  
Hypoplastic Left Heart ◽  
Left Heart Syndrome ◽  
Complex Cases

AbstractIn hypoplastic left heart syndrome, thrombosis of the native ascending aorta is rare and often fatal; there are no previously reported cases presenting with acute heart block. We review a case of native ascending aorta thrombosis in a 2-year-old boy with hypoplastic left heart syndrome, presenting with acute heart block. This case highlights the benefit of multi-modality imaging in complex cases.

Sign in / Sign up

Export Citation Format

Share Document