Dietary treatment and biochemical studies on a neonatal case of propionyl-CoA carboxylase deficiency

1982 ◽  
Vol 5 (2) ◽  
pp. 121-124 ◽  
Author(s):  
J. A. Del Valle ◽  
B. Merinero ◽  
A. Jiménez ◽  
M. J. García ◽  
M. Ugarte ◽  
...  
Keyword(s):  
Dietary Treatment ◽  
Biochemical Studies ◽  
Propionyl Coa Carboxylase Deficiency

ISOVALERIC ACIDEMIA: RESULTS OF FAMILY STUDY AND DIETARY TREATMENT

PEDIATRICS ◽  
1973 ◽  
Vol 52 (1) ◽  
pp. 83-94
Author(s):  
Harvey L. Levy ◽  
Arline M. Erickson ◽  
Ira T. Lott ◽  
Donald J. Kurtz
Keyword(s):  
Mental Retardation ◽  
Psychosocial Functioning ◽  
Family Study ◽  
Dietary Treatment ◽  
Isovaleric Acid ◽  
Dietary Therapy ◽  
Moderate Degree ◽  
Isovaleric Acidemia ◽  
Biochemical Studies ◽  
The Subject

Detailed clinical and biochemical studies are reported in two siblings with isovaleric acidemia ("sweaty feet syndrome"). The younger of these siblings was begun on treatment with a low-leucine diet at the age of 17 days and was the subject of a previous brief report (Pediatrics, 49: 616, 1972). Within one day of the beginning of treatment urinary isovaleric acid dropped from 1661.4µmoles/24 hr to 94.1µmoles/24 hr and urinary isovalerylglycine dropped from 480 mg/23 hr to 150 mg/24 hr. Until the age of 3 years he was maintained on this diet and had many less episodes of vomiting and acidosis than his affected but untreated sister had had at corresponding ages. Psychosocial functioning has been at low normal levels whereas the affected sister has a moderate degree of mental retardation. It is postulated that isovaleric acidemia may be added to the growing list of disorders that can cause mental retardation but that may be amenable to dietary therapy begun in early infancy.

Ruthenium Red Staining of Human Hard Keratin Fibers

1982 ◽  
Vol 40 ◽  
pp. 278-279
Author(s):  
M. C. Buhrer ◽  
R. A. Mathews
Keyword(s):  
Human Hair ◽  
Ruthenium Red ◽  
Acid Mucopolysaccharides ◽  
Biochemical Studies ◽  
Keratin Fibers ◽  
Ruthenium Red Staining ◽  
Extracellular Materials

Ruthenium red has been used as a stain to demonstrate a variety of extracellular materials, especially acid mucopolysaccharides. It also reacts with certain intracellular and extracellular lipids. Since biochemical studies in our laboratory demonstrated the presence of a variety of monosaccharides in human hair ruthenium red staining procedures were adopted in order to evaluate the presence and morphological location of acid oligosaccharides in the keratinized aspect of hair.

Effects of Hypophysectomy on the Fine Structure of Rat Liver Cells

1967 ◽  
Vol 25 ◽  
pp. 156-157
Author(s):  
Robert R. Cardell
Keyword(s):  
Electron Microscopy ◽  
Fine Structure ◽  
Rat Liver ◽  
Liver Cell ◽  
Anterior Pituitary ◽  
Liver Cells ◽  
Biochemical Studies ◽  
Liver Functions ◽  
Rat Liver Cells ◽  
And Control

Hypophysectomy of the rat renders this animal deficient in the hormones of the anterior pituitary gland, thus causing many primary and secondary hormonal effects on basic liver functions. Biochemical studies of these alterations in the rat liver cell are quite extensive; however, relatively few morphological observations on such cells have been recorded. Because the available biochemical information was derived mostly from disrupted and fractionated liver cells, it seemed desirable to examine the problem with the techniques of electron microscopy in order to see what changes are apparent in the intact liver cell after hypophysectomy. Accordingly, liver cells from rats which had been hypophysectomized 5-120 days before sacrifice were studied. Sham-operated rats served as controls and both hypophysectomized and control rats were fasted 15 hours before sacrifice.

Rhabdomyolysis in DOMS

1999 ◽  
Vol 38 (05) ◽  
pp. 164-168 ◽  
Author(s):  
Gloria Ruiz Hernandez ◽  
C. Sanchez Marchori ◽  
J. Munoz Moliner ◽  
C. Martinez Carsi
Keyword(s):  
Bone Scintigraphy ◽  
Previous History ◽  
Biochemical Studies ◽  
History Of ◽  
Increased Activity

SummaryA 26-year-old man with a previous history of external twin bursitis was remitted to our Department for a bone scintigraphy. Before the study, the patient performed an elevated number of intense sprints. Bone scintigraphy showed a bilaterally increased activity in both anterior rectum muscles suggesting rhabdomyolysis. Biochemical studies and MRT confirmed the diagnosis.

Nutritional Value Research of Spelt Pasta with Vegetable Additives

Food Industry ◽  
2020 ◽  
Vol 5 (2) ◽  
pp. 61-70
Author(s):  
Oliya Fazullina ◽  
Stanislav Smirnov
Keyword(s):  
Dietary Fiber ◽  
Nutritional Value ◽  
Raw Materials ◽  
Health Indicators ◽  
Dietary Treatment ◽  
Raw Material ◽  
Whole Wheat ◽  
Healthy Nutrition ◽  
Physiologically Active Substances ◽  
Simple Carbohydrates

Health indicators of the population depend significantly on the food quality and nutritional value. Simple carbohydrates excess of and lack of protein, dietary fiber, vitamins, minerals, antioxidants and other physiologically active substances increase the risk of socially significant disease progress. The development and production of mass-consumed products with high nutritional and biological value, including affordable non-traditional raw materials use, are promising areas of the food industry development aimed at improving the nutritional status of the population. The article presents the research results on the developed Noodle products recipes from non-traditional raw materials that meet modern healthy nutrition requirements, intended for dietary treatment and dietary prevention of people with overweight / obesity. The research aimed at expanding the range of macaroni products with these characteristics. As the main raw material, a man selected whole-wheat flour – new spelt flour, and as additional raw materials – buckwheat flour, broccoli and celery powders. The researchers found that the introduction of macaroni products from buckwheat spelt, broccoli and celery powders into the recipe had a multidirectional effect, reducing or increasing various indicators of its nutritional value. The changes range did not affect the overall characteristics. The satisfaction degree of the average daily need for food substances and energy when consuming a portion of 100 g for each sample of developed Noodle products allows them to be classified as functional products that are protein and dietary fiber sources, according to the requirements of the TR CU 022/2011.

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