Impaired peroxisomal fatty acid oxidation in human skin fibroblasts with a mitochondrial acylcarnitine/carnitine translocase deficiency

B. S. Jakobs; R. J. A. Wanders

doi:10.1007/bf01799425

Impaired peroxisomal fatty acid oxidation in human skin fibroblasts with a mitochondrial acylcarnitine/carnitine translocase deficiency

Journal of Inherited Metabolic Disease ◽

10.1007/bf01799425 ◽

1996 ◽

Vol 19 (2) ◽

pp. 185-187 ◽

Cited By ~ 3

Author(s):

B. S. Jakobs ◽

R. J. A. Wanders

Keyword(s):

Fatty Acid ◽

Fatty Acid Oxidation ◽

Human Skin ◽

Skin Fibroblasts ◽

Acid Oxidation ◽

Human Skin Fibroblasts ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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Identification of fatty acid oxidation disorder patients with lowered acyl-CoA thioesterase activity in human skin fibroblasts

European Journal of Clinical Investigation ◽

10.1111/j.1365-2362.2005.01447.x ◽

2005 ◽

Vol 35 (1) ◽

pp. 38-46 ◽

Cited By ~ 7

Author(s):

M. C. Hunt ◽

J. Ruiter ◽

P. Mooyer ◽

C. W. T. van Roermond ◽

R. Ofman ◽

...

Keyword(s):

Fatty Acid ◽

Fatty Acid Oxidation ◽

Human Skin ◽

Skin Fibroblasts ◽

Acid Oxidation ◽

Fatty Acid Oxidation Disorder ◽

Human Skin Fibroblasts

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A method for quantitative acylcarnitine profiling in human skin fibroblasts using unlabelled palmitic acid: diagnosis of fatty acid oxidation disorders and differentiation between biochemical phenotypes of MCAD deficiency

Biochimica et Biophysica Acta (BBA) - Molecular and Cell Biology of Lipids ◽

10.1016/s1388-1981(02)00296-2 ◽

2002 ◽

Vol 1584 (2-3) ◽

pp. 91-98 ◽

Cited By ~ 48

Author(s):

Jürgen G Okun ◽

Stefan Kölker ◽

Andreas Schulze ◽

Dirk Kohlmüller ◽

Katharina Olgemöller ◽

...

Keyword(s):

Fatty Acid ◽

Palmitic Acid ◽

Fatty Acid Oxidation ◽

Human Skin ◽

Skin Fibroblasts ◽

Acid Oxidation ◽

Human Skin Fibroblasts ◽

Mcad Deficiency ◽

Fatty Acid Oxidation Disorders

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Peroxisomal fatty acid oxidation capacity is more resistant to ischaemic and reperfusion injury than mitochondrial fatty acid oxidation capacity in feline hearts

Acta Physiologica Scandinavica ◽

10.1046/j.1365-201x.1996.498243000.x ◽

1996 ◽

Vol 157 (2) ◽

pp. 133-145 ◽

Cited By ~ 1

Author(s):

H. BRUNVAND ◽

L. FRØYLAND ◽

J. WESTBY ◽

E. HEXEBERG ◽

R. K. BERGE ◽

...

Keyword(s):

Fatty Acid ◽

Reperfusion Injury ◽

Fatty Acid Oxidation ◽

Acid Oxidation ◽

Mitochondrial Fatty Acid Oxidation ◽

Oxidation Capacity ◽

Mitochondrial Fatty Acid ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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Eicosapentaenoic and docosahexaenoic acid affect mitochondrial and peroxisomal fatty acid oxidation in relation to substrate preference

Lipids ◽

10.1007/s11745-999-0445-x ◽

1999 ◽

Vol 34 (9) ◽

pp. 951-963 ◽

Cited By ~ 124

Author(s):

Lise Madsen ◽

Arild C. Rustan ◽

Hege Vaagenes ◽

Kjetil Berge ◽

Endre Dyrøy ◽

...

Keyword(s):

Fatty Acid ◽

Docosahexaenoic Acid ◽

Fatty Acid Oxidation ◽

Substrate Preference ◽

Acid Oxidation ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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Peroxisomal fatty acid oxidation and glycolysis are triggered in mouse models of lesional atopic dermatitis.

JID Innovations ◽

10.1016/j.xjidi.2021.100033 ◽

2021 ◽

pp. 100033

Author(s):

P. Pavel ◽

G. Leman ◽

M. Hermann ◽

C. Ploner ◽

T.O. Eichmann ◽

...

Keyword(s):

Atopic Dermatitis ◽

Fatty Acid ◽

Fatty Acid Oxidation ◽

Mouse Models ◽

Acid Oxidation ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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Peroxisomal fatty acid oxidation disorders and 58 kDa sterol carrier protein X (SCPx): activity measurements in liver and fibroblasts using a newly developed method

The Journal of Lipid Research ◽

10.1016/s0022-2275(20)34472-2 ◽

2000 ◽

Vol 41 (3) ◽

pp. 336-342

Author(s):

Sacha Ferdinandusse ◽

Simone Denis ◽

Emanuel van Berkel ◽

Georges Dacremont ◽

Ronald J.A. Wanders

Keyword(s):

Fatty Acid ◽

Fatty Acid Oxidation ◽

Acid Oxidation ◽

Carrier Protein ◽

Sterol Carrier Protein ◽

Fatty Acid Oxidation Disorders ◽

Activity Measurements ◽

Protein X ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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An Increase in Peroxisomal Fatty Acid Oxidation Is Not Sufficient to Prevent Tissue Lipid Accumulation in hHTg Rats

Annals of the New York Academy of Sciences ◽

10.1111/j.1749-6632.2002.tb04265.x ◽

2006 ◽

Vol 967 (1) ◽

pp. 71-79 ◽

Cited By ~ 2

Author(s):

J. UKROPEC ◽

I. KLIMEŠ ◽

D. GAŠPERÍKOVÁ ◽

E. DEMCÁKOVÁ ◽

C. A. DREVON ◽

...

Keyword(s):

Fatty Acid ◽

Fatty Acid Oxidation ◽

Lipid Accumulation ◽

Acid Oxidation ◽

Tissue Lipid ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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Mitochondrial and peroxisomal fatty acid oxidation capacities increase in the skeletal muscles of young pigs during early postnatal development but are not affected by cold stress

Reproduction Nutrition Development ◽

10.1051/rnd:2003013 ◽

2003 ◽

Vol 43 (2) ◽

pp. 155-166 ◽

Cited By ~ 6

Author(s):

Patrick Herpin ◽

Annie Vincent ◽

Martine Fillaut ◽

Bruno Piteira Bonito ◽

Jean-Fran�ois Hocquette

Keyword(s):

Fatty Acid ◽

Cold Stress ◽

Postnatal Development ◽

Fatty Acid Oxidation ◽

Skeletal Muscles ◽

Acid Oxidation ◽

Early Postnatal Development ◽

Young Pigs ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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206 Atopic dermatitis is associated with increased peroxisomal fatty acid oxidation in the epidermis

Journal of Investigative Dermatology ◽

10.1016/j.jid.2019.07.207 ◽

2019 ◽

Vol 139 (9) ◽

pp. S250

Author(s):

P. Pavel ◽

G. Leman ◽

M. Hermann ◽

T. Eichmann ◽

F. Radner ◽

...

Keyword(s):

Atopic Dermatitis ◽

Fatty Acid ◽

Fatty Acid Oxidation ◽

Acid Oxidation ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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Dietary sesamin and docosahexaenoic and eicosapentaenoic acids synergistically increase the gene expression of enzymes involved in hepatic peroxisomal fatty acid oxidation in rats

Metabolism ◽

10.1016/j.metabol.2005.09.013 ◽

2006 ◽

Vol 55 (3) ◽

pp. 381-390 ◽

Cited By ~ 11

Author(s):

Premakumara G. Arachchige ◽

Yoko Takahashi ◽

Takashi Ide

Keyword(s):

Gene Expression ◽

Fatty Acid ◽

Fatty Acid Oxidation ◽

Acid Oxidation ◽

Peroxisomal Fatty Acid Oxidation ◽

Peroxisomal Fatty Acid

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