Demyelination in the spinal cord of murine globoid cell leukodystrophy (the twitcher mouse)

H. Takahashi; K. Suzuki

doi:10.1007/bf00687612

Demyelination in the spinal cord of murine globoid cell leukodystrophy (the twitcher mouse)

Acta Neuropathologica ◽

10.1007/bf00687612 ◽

1984 ◽

Vol 62 (4) ◽

pp. 298-308 ◽

Cited By ~ 31

Author(s):

H. Takahashi ◽

K. Suzuki

Keyword(s):

Spinal Cord ◽

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

Globoid Cell

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Hematopoietic Cell Transplantation in Murine Globoid Cell Leukodystrophy (the Twitcher Mouse) Effects on Galactosylceramidase and Psychosine Levels in the Nervous System

Annals of the New York Academy of Sciences ◽

10.1111/j.1749-6632.1988.tb51471.x ◽

1988 ◽

Vol 529 (1 Fourth Colloq) ◽

pp. 242-245 ◽

Cited By ~ 1

Author(s):

ANDREW M. YEAGER ◽

TAKAO ICHIOKA ◽

YASUO KISHIMOTO

Keyword(s):

Nervous System ◽

Cell Transplantation ◽

Hematopoietic Cell Transplantation ◽

Hematopoietic Cell ◽

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

Globoid Cell

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Diffusion tensor imaging detects axonal injury and demyelination in the spinal cord and cranial nerves of a murine model of globoid cell leukodystrophy

NMR in Biomedicine ◽

10.1002/nbm.1420 ◽

2009 ◽

Vol 22 (10) ◽

pp. 1100-1106 ◽

Cited By ~ 21

Author(s):

A. Alex Hofling ◽

Joong Hee Kim ◽

Corinne R. Fantz ◽

Mark S. Sands ◽

Sheng-Kwei Song

Keyword(s):

Spinal Cord ◽

Diffusion Tensor Imaging ◽

Murine Model ◽

Diffusion Tensor ◽

Axonal Injury ◽

Cranial Nerves ◽

Globoid Cell Leukodystrophy ◽

Globoid Cell

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Nerve conduction studies in the Twitcher mouse (murine globoid cell leukodystrophy)

Journal of the Neurological Sciences ◽

10.1016/0022-510x(86)90116-4 ◽

1986 ◽

Vol 74 (2-3) ◽

pp. 307-318 ◽

Cited By ~ 21

Author(s):

Eitoku Toyoshima ◽

Andrew M. Yeager ◽

Susan Brennan ◽

George W. Santos ◽

Hugo W. Moser ◽

...

Keyword(s):

Nerve Conduction ◽

Nerve Conduction Studies ◽

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

Globoid Cell

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Globoid cell leukodystrophy: Specialized contact of globoid cell with astrocyte in the brain of twitcher mouse

Acta Neuropathologica ◽

10.1007/bf00688603 ◽

1982 ◽

Vol 58 (4) ◽

pp. 237-242 ◽

Cited By ~ 4

Author(s):

H. Takahashi ◽

K. Suzuki

Keyword(s):

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

The Brain ◽

Globoid Cell

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Suppression of galactosylceramidase (GALC) expression in the twitcher mouse model of globoid cell leukodystrophy (GLD) is caused by nonsense-mediated mRNA decay (NMD)

Neurobiology of Disease ◽

10.1016/j.nbd.2006.03.005 ◽

2006 ◽

Vol 23 (2) ◽

pp. 273-280 ◽

Cited By ~ 18

Author(s):

Wing C. Lee ◽

Yuen K. Tsoi ◽

Chad A. Dickey ◽

Michael W. DeLucia ◽

Dennis W. Dickson ◽

...

Keyword(s):

Mouse Model ◽

Mrna Decay ◽

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

Nonsense Mediated Mrna Decay ◽

Globoid Cell

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Bone Marrow Transplantation Augments the Effect of Brain- and Spinal Cord-Directed Adeno-Associated Virus 2/5 Gene Therapy by Altering Inflammation in the Murine Model of Globoid-Cell Leukodystrophy

Journal of Neuroscience ◽

10.1523/jneurosci.1802-11.2011 ◽

2011 ◽

Vol 31 (27) ◽

pp. 9945-9957 ◽

Cited By ~ 44

Author(s):

A. S. Reddy ◽

J. H. Kim ◽

J. A. Hawkins-Salsbury ◽

S. L. Macauley ◽

E. T. Tracy ◽

...

Keyword(s):

Spinal Cord ◽

Gene Therapy ◽

Bone Marrow ◽

Bone Marrow Transplantation ◽

Murine Model ◽

Marrow Transplantation ◽

Globoid Cell Leukodystrophy ◽

Adeno Associated Virus ◽

Brain And Spinal Cord ◽

Globoid Cell

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Metabolism of galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy

Biochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism ◽

10.1016/0005-2760(86)90105-0 ◽

1986 ◽

Vol 879 (2) ◽

pp. 215-220 ◽

Cited By ~ 11

Author(s):

Kobayashi Takuro ◽

Shinnoh Nobue ◽

Kuroiwa Yoshigoro

Keyword(s):

Animal Model ◽

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

Globoid Cell

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Hematopoietic Cell Transplantation in Murine Globoid Cell Leukodystrophy (The Twitcher Mouse)—A Model of a Human Sphingolipidosis (Krabbe Disease)

Recent Advances and Future Directions in Bone Marrow Transplantation - Experimental Hematology Today—1987 ◽

10.1007/978-1-4612-3762-4_7 ◽

1988 ◽

pp. 36-44

Author(s):

Andrew M. Yeager ◽

Takao Ichioka ◽

Eitoku Toyoshima ◽

Yasuo Kishimoto ◽

Susan Brennan ◽

...

Keyword(s):

Cell Transplantation ◽

Hematopoietic Cell Transplantation ◽

Hematopoietic Cell ◽

Krabbe Disease ◽

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

Globoid Cell

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Hematopoietic cell transplantation in murine globoid cell leukodystrophy (the twitcher mouse): effects on levels of galactosylceramidase, psychosine, and galactocerebrosides.

Proceedings of the National Academy of Sciences ◽

10.1073/pnas.84.12.4259 ◽

1987 ◽

Vol 84 (12) ◽

pp. 4259-4263 ◽

Cited By ~ 51

Author(s):

T. Ichioka ◽

Y. Kishimoto ◽

S. Brennan ◽

G. W. Santos ◽

A. M. Yeager

Keyword(s):

Cell Transplantation ◽

Hematopoietic Cell Transplantation ◽

Hematopoietic Cell ◽

Globoid Cell Leukodystrophy ◽

Twitcher Mouse ◽

Globoid Cell

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Genetic background markedly influences vulnerability of the hippocampal neuronal organization in the ?twitcher? mouse model of globoid cell leukodystrophy

Journal of Neuroscience Research ◽

10.1002/jnr.20190 ◽

2004 ◽

Vol 77 (4) ◽

pp. 507-516 ◽

Cited By ~ 17

Author(s):

Kumiko Tominaga ◽

Junko Matsuda ◽

Makiko Kido ◽

Etsuo Naito ◽

Ichiro Yokota ◽

...

Keyword(s):

Mouse Model ◽

Genetic Background ◽

Globoid Cell Leukodystrophy ◽

Neuronal Organization ◽

Twitcher Mouse ◽

Globoid Cell

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