Retinal Pathology and Function in a Cln3 Knockout Mouse Model of Juvenile Neuronal Ceroid Lipofuscinosis (Batten Disease)

2002 ◽  
Vol 19 (4) ◽  
pp. 515-527 ◽  
Author(s):  
Gail M. Seigel ◽  
Andrew Lotery ◽  
Ari Kummer ◽  
David J. Bernard ◽  
Nicholas D.E. Greene ◽  
...  
Keyword(s):  
Mouse Model ◽  
Knockout Mouse ◽  
Neuronal Ceroid Lipofuscinosis ◽  
Batten Disease ◽  
Juvenile Neuronal Ceroid Lipofuscinosis ◽  
Knockout Mouse Model ◽  
Ceroid Lipofuscinosis ◽  
Retinal Pathology ◽  
And Function

Altered Flurothyl Seizure Induction Latency, Phenotype, and Subsequent Mortality in a Mouse Model of Juvenile Neuronal Ceroid Lipofuscinosis/Batten Disease

Epilepsia ◽  
2002 ◽  
Vol 43 (10) ◽  
pp. 1137-1140 ◽  
Author(s):  
Elizabeth Kriscenski-Perry ◽  
Craig D. Applegate ◽  
Andrew Serour ◽  
Timothy R. Mhyre ◽  
Christopher C. Leonardo ◽  
...  
Keyword(s):  
Mouse Model ◽  
Neuronal Ceroid Lipofuscinosis ◽  
Batten Disease ◽  
Juvenile Neuronal Ceroid Lipofuscinosis ◽  
Ceroid Lipofuscinosis

Late onset neurodegeneration in the Cln3−/− mouse model of juvenile neuronal ceroid lipofuscinosis is preceded by low level glial activation

2004 ◽  
Vol 1023 (2) ◽  
pp. 231-242 ◽  
Author(s):  
Charlie C. Pontikis ◽  
Claire V. Cella ◽  
Nisha Parihar ◽  
Ming J. Lim ◽  
Shubhodeep Chakrabarti ◽  
...  
Keyword(s):  
Mouse Model ◽  
Late Onset ◽  
Neuronal Ceroid Lipofuscinosis ◽  
Glial Activation ◽  
Juvenile Neuronal Ceroid Lipofuscinosis ◽  
Low Level ◽  
Ceroid Lipofuscinosis

scholarly journals Quantifying physical decline in juvenile neuronal ceroid lipofuscinosis (Batten disease)

Neurology ◽  
2011 ◽  
Vol 77 (20) ◽  
pp. 1801-1807 ◽  
Author(s):  
J. M. Kwon ◽  
H. Adams ◽  
P. G. Rothberg ◽  
E. F. Augustine ◽  
F. J. Marshall ◽  
...  
Keyword(s):  
Neuronal Ceroid Lipofuscinosis ◽  
Batten Disease ◽  
Juvenile Neuronal Ceroid Lipofuscinosis ◽  
Physical Decline ◽  
Ceroid Lipofuscinosis
Sign in / Sign up

Export Citation Format

Share Document