scholarly journals VP52.01: Fetoscopic prenatal diagnosis of esophageal atresia with tracheoesophageal fistula associated with congenital diaphragmatic hernia

2021 ◽  
Vol 58 (S1) ◽  
pp. 306-306
Author(s):  
J. Otaño ◽  
J. Sabrià ◽  
O. Gómez ◽  
E. Eixarch ◽  
M. Bennasar ◽  
...  
Keyword(s):  
Prenatal Diagnosis ◽  
Congenital Diaphragmatic Hernia ◽  
Esophageal Atresia ◽  
Diaphragmatic Hernia ◽  
Tracheoesophageal Fistula

scholarly journals Intraoperative acidosis and hypercapnia during thoracoscopic repair of congenital diaphragmatic hernia and esophageal atresia/tracheoesophageal fistula

2017 ◽  
Vol 27 (8) ◽  
pp. 841-848 ◽  
Author(s):  
Augusto Zani ◽  
Ruben Lamas‐Pinheiro ◽  
Irene Paraboschi ◽  
Sebastian K. King ◽  
Justyna Wolinska ◽  
...  
Keyword(s):  
Congenital Diaphragmatic Hernia ◽  
Esophageal Atresia ◽  
Diaphragmatic Hernia ◽  
Tracheoesophageal Fistula ◽  
Thoracoscopic Repair

scholarly journals Prenatal diagnosis, imaging, and prognosis in Congenital Diaphragmatic Hernia

2020 ◽  
Vol 44 (1) ◽  
pp. 51163 ◽  
Author(s):  
Anne-Gael Cordier ◽  
Francesca M. Russo ◽  
Jan Deprest ◽  
Alexandra Benachi
Keyword(s):  
Prenatal Diagnosis ◽  
Congenital Diaphragmatic Hernia ◽  
Diaphragmatic Hernia

scholarly journals CONGENITAL DIAPHRAGMATIC HERNIA - PRENATAL DIAGNOSIS AND SURVIVAL

1999 ◽  
Vol 45 (6) ◽  
pp. 919-919
Author(s):  
E Garne ◽  
P Quataert ◽  
C De Vigan ◽  
H Mendizabal ◽  
D Igoe ◽  
...  
Keyword(s):  
Prenatal Diagnosis ◽  
Congenital Diaphragmatic Hernia ◽  
Diaphragmatic Hernia

Selected Midline Defect Associations: A Population Study

PEDIATRICS ◽  
1989 ◽  
Vol 84 (2) ◽  
pp. 266-272
Author(s):  
Muin J. Khoury ◽  
José F. Cordero ◽  
Joseph Mulinare ◽  
John M. Opitz
Keyword(s):  
Cleft Palate ◽  
Esophageal Atresia ◽  
Diaphragmatic Hernia ◽  
Neural Tube ◽  
Neural Tube Defects ◽  
Imperforate Anus ◽  
Tracheoesophageal Fistula ◽  
Congenital Defects ◽  
Midline Defect ◽  
Midline Defects

Using data from the population-based Metropolitan Atlanta Congenital Defects Program, the association of seven relatively common and easily ascertainable groups of midline defects was studied. These defects were neural tube defects (575 patients), oral clefts (633 patients), omphalocele (141 patients), esophageal atresia/tracheoesophageal fistula (88 patients), imperforate anus (151 patients), conotruncal heart defects (289 patients), and diaphragmatic hernia (75 patients). Known syndromes were excluded from the analysis. Of 1743 infants with at least one midline defect, 86 (4.9%) had at least a second midline defect, and 9 (0.5%) had two additional midline defects. Pairwise analysis of the seven defects shows that, although most midline defects tend to be statistically associated with other midline defects, specific combinations of midline defects are seen. For example, neural tube defects are more strongly associated with cleft lip with or without cleft palate than with cleft palate alone; imperforate anus is more strongly associated with spina bifida than with anencephaly or encephalocele. Moreover, some combinations of defects are not observed (eg, neural tube defect and conotruncal heart defect, clefts and diaphragmatic hernia, omphalocele and esophageal atresia/tracheoesophageal fistula). These data point to the need for further refinement in the study of the association of midline defects in terms of embryologic and pathogenetic mechanisms because most midline defects tend to occur as an isolated defect, some midline defects occur with nonmidline defects (such as limb defects), and specific associations among midline defects are observed.

scholarly journals PRENATAL DIAGNOSIS AND SURGICAL INNOVATIONS IN CONGENITAL DIAPHRAGMATIC HERNIA: EVALUATION OF PRE- AND POST-OPERATIVE MANAGEMENT

2014 ◽  
Vol 6 (1) ◽  
Author(s):  
R. Angotti ◽  
F. Molinaro ◽  
K. Bici ◽  
E. Cerchia ◽  
M. Sica ◽  
...  
Keyword(s):  
Intensive Care Unit ◽  
Intensive Care ◽  
Prenatal Diagnosis ◽  
Minimally Invasive ◽  
Congenital Diaphragmatic Hernia ◽  
Diaphragmatic Hernia ◽  
Young Patients ◽  
Surgical Techniques ◽  
Female Ratio ◽  
Access Surgery

Introduction. Congenital diaphragmatic hernia (CDH) is still today considered a challenge from surgeons. Considerable progress in prenatal diagnosis, intensive care unit of neonates and surgical techniques, with the possibility to perform minimally access surgery, widely increased survival rates. The aim of this study is to analyze our series about long and short-term outcomes, also considering the progress made by minimally invasive techniques. Methods. The study was performed at Pediatric Surgery of Siena. It is a retrospective study that analyzed all patients with CDH (Bochdalek) treated in the last 14 years, from 2000 to 2013. Sex, side of the defect, presence of prenatal diagnosis, age of onset and symptoms, associate malformation, herniated organs, surgical technique and site of surgery, complications, recurrences, survival and followup were analyzed. Results. We included 23 patients. Five of them, were ruled out because of affected by diaphragmatic eventration or acquired diaphragmatic hernia. Forteen patients (77%) presented left CDH and 4 patients (23%) a right one. The male female ratio were 14:4. Prenatal diagnosis was performed in 5 patients (27,5%) at a mean gestational age of 29 weeks. Forteen patients (77%) had an early onset of symptoms (first day of life). Most common symptoms were respiratory distress and cyanosis; 4 patients (23%) had a late onset of symptoms, at a mean age of 9 months, and most common symptoms were failure to thrive and vomiting. Seven patients (39%) had associated malformation: common mesenterium (5 pts-71%). The colon was the most commonly herniated organ, present in 15 patients (83%), followed by small intestine in 13 patients (72%), stomach in 11 patients (61%), spleen in 9 patients (50%) and liver in 4 patients (23%). Seventeen patients (94,5%) underwent open surgery: 10 of them (59%) underwent a subcostal laparotomy approach, 7 of them (41%) underwent a supraumbelical laparotomy approach; 1 patient (5%) underwent minimally access surgery with thoracoscopy access. We performed performed surgery in the intensive care unit in 3 patients (16,5%). Six patients (33%) developed minor postoperatory complications. No patient had recurrence. Four patients died so we report a mortality rate of 23%. A follow-up investigation, with an average duration of 87 months, it is still going on in 5 patients (27,5%). Conclusions. The our survival rate was 77% and it reflects the encouraging reported data in the recent literature. These results are due to the reliability of the new resuscitation strategies, such as high-frequency oscillatory ventilation and the use of NO, the ability to perform surgery in the neonatal intensive care unit and, especially, to successfully perform minimally invasive surgery in newborn. The improvement of the survival showed the increasing of long-term morbidity end the requirement of a multidisciplinary followup. For these reasons, a multidisciplinary pathway for the management of young patients has been created, to follow them in a standardized way as early as the prenatal diagnosis.

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