scholarly journals VP22.24: Idiopathic DA constriction observed during left isomerism

2021 ◽  
Vol 58 (S1) ◽  
pp. 194-194
Author(s):  
G. Garayeva ◽  
A.T. Farajov ◽  
G. Mammadova ◽  
A. Azimova
Keyword(s):  
Left Isomerism

scholarly journals Anesthetic implications of total anomalous systemic venous connection to left atrium with left isomerism

2012 ◽  
Vol 15 (2) ◽  
pp. 134 ◽  
Author(s):  
ParimalaPrasanna Simha ◽  
AM Jagadeesh ◽  
MuralidharaDanappa Patel
Keyword(s):  
Left Atrium ◽  
Left Isomerism

scholarly journals Pre natal evaluation of heterotaxy syndrome by fetal echocardiography and correlating with autopsy

Ultrasound ◽  
2019 ◽  
Vol 27 (2) ◽  
pp. 111-121
Author(s):  
Madhavilatha Routhu ◽  
Imran Ali Mohammad
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Right Atrial ◽  
Heterotaxy Syndrome ◽  
Fetal Autopsy ◽  
Cardiac Anomalies ◽  
Left Isomerism ◽  
Right Isomerism ◽  
Visceral Heterotaxy

Introduction Heterotaxy syndrome/ isomerism is characterized by an abnormal symmetry of the viscera that are normally dissimilar due to abnormal lateralization of thoracic and abdominal viscera and is frequently associated with complex cardiac anomalies. Isomerism may be of right or left. Materials and methods This article describes the morphological characteristics of heterotaxy and suggests an approach in evaluating the spectrum of abnormalities associated with this syndrome. This study is based on 12 cases diagnosed on antenatal ultrasound as heterotaxy syndrome. Results of the examinations were re-evaluated and compared by fetal autopsy. Result Based on the following echocardiographic criteria, a diagnosis of left isomerism was made if there was viscerocardiac heterotaxy associated with an interruption of inferior vena cava or with bilateral finger-like atrial appendages or if it was associated with heart block. If there was evidence of viscerocardiac heterotaxy with complex cardiac anomalies then it was diagnosed as right atrial isomerism or visceral heterotaxy syndrome. We diagnosed 6/12 as left isomerism and rest of the cases as right isomerism/visceral heterotaxy syndrome. In Autopsy we evaluated visceral situs and morphology of the lungs and the main bronchi, the state of the liver, spleen, bowel, and the precise anatomy of the heart and confirmed 4/12 as left isomerism 4/12 as right isomerism and two cases as visceral heterotaxy syndrome (VHS). Rest of the two cases were included in the study despite missing autopsy data, as the combination of abnormal situs with interrupted inferior vena cava, and cardiac malformation allowed a diagnosis of left isomerism with high probability. Conclusion In this study, we aimed to find common features of heterotaxy syndrome on prenatal ultrasound as well as on fetal autopsy. This syndrome should be accurately diagnosed in the prenatal period in order to allow appropriate counseling of parents.

Hepatic venous connection to a persistent inferior caval vein in left isomerism

1990 ◽  
Vol 11 (9) ◽  
pp. 845-847 ◽  
Author(s):  
J. GUENTHARD ◽  
J. S. CARVALHO ◽  
R. H. ANDERSON ◽  
M. L. RlGBY
Keyword(s):  
Caval Vein ◽  
Inferior Caval Vein ◽  
Left Isomerism

Where's the spleen? Looking for the spleen and assessing its function in the syndromes of isomerism

1997 ◽  
Vol 7 (3) ◽  
pp. 347-357 ◽  
Author(s):  
Colin Kit Lun Phoon
Keyword(s):  
Spatial Resolution ◽  
Peripheral Blood ◽  
Antimicrobial Prophylaxis ◽  
Close Association ◽  
Young Infant ◽  
Management Strategies ◽  
Peripheral Blood Smear ◽  
Splenic Tissue ◽  
Splenic Function ◽  
Left Isomerism

AbstractDespite the close association of certain constellations of cardiac malformations with splenic status (right isomerism / asplenia, left isomerism / polysplenia), the association is not perfect. Given the risk of infection in the patient lacking splenic tissue, it seems prudent to assess the state of the spleen separately from the cardiovascular system, in order to decide on antimicrobial prophylaxis. A wide variety of tests is available to assess splenic function and/or anatomy. Counting pitted erythrocytes or Howell-Jolly bodies in the peripheral blood smear can be a good indicator of the lack of splenic function, although the former appears more sensitive and quantitative than the latter. Radionuclide spleen scans can provide both anatomic and functional information about the spleen, and may be a useful adjunctive test. Relatively poor spatial resolution, and interfering hepatic activity (even with spleen-specific scans), mitigate its usefulness in the young infant. The reliability of computed tomography and magnetic resonance imaging in detecting splenic tissue in the heterotaxy syndromes is unproven and perhaps only fair at best. They are probably most helpful as adjunctive tests. Ultrasonography offers excellent spatial resolution, portability, and lack of ionizing radiation, but is operator- and patient-dependent. Nonetheless, ultrasonography, coupled with an examination of the peripheral blood for Howell-Jolly bodies or pitted erythrocytes, is probably the set of tests with highest sensitivity and greatest convenience. Management strategies for the asplenic patient are also discussed.

A Case of Coarctation of Aorta with Left Isomerism Associated with Inferior Vena Cava Interruption and Polysplenia

2007 ◽  
Vol 15 (1) ◽  
pp. 27 ◽  
Author(s):  
Gwan Hyeop Sohn ◽  
Kyoung Min Byun ◽  
Hye Jin Han ◽  
Hak Jin Kim ◽  
Jin Oh Choi ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Coarctation Of Aorta ◽  
Left Isomerism

Determining bronchial morphology for the purposes of segregating so-called heterotaxy

2015 ◽  
Vol 26 (4) ◽  
pp. 725-737 ◽  
Author(s):  
Rohit S. Loomba ◽  
Andrew N. Pelech ◽  
Parinda H. Shah ◽  
Robert H. Anderson
Keyword(s):  
Bronchial Tree ◽  
Clinical Findings ◽  
Chest Radiographs ◽  
Clinical Entity ◽  
Imaging Modalities ◽  
Clinical Imaging ◽  
Cardiac Morphology ◽  
Abdominal Organs ◽  
Left Isomerism ◽  
Routine Clinical Imaging

AbstractIntroductionHeterotaxy is a unique clinical entity in which lateralisation of the thoraco-abdominal organs is abnormal, typically with isomerism of the bronchial tree and atrial appendages. This study was carried out to determine whether routine clinical imaging such as chest radiographs, angiographic images, and CT/MRI can determine bronchial isomerism, and how sidedness of bronchial isomerism correlates with overall features anticipated in hearts with isomeric atrial appendages.Methods and resultsWe identified 73 patients with heterotaxy, in whom imaging clearly demonstrated the bronchial tree, seen at our institution since 1998. We calculated bronchial angles and lengths using all the available imaging modalities to determine the presence and sidedness of bronchial isomerism. This was then compared with the anticipated presence of isomeric atrial appendages based on the overall clinical findings, as the appendages themselves had not specifically been imaged.The ratio of bronchial lengths revealed bronchial isomerism in all patients, with bronchial angles permitting distinction of right as opposed to left isomerism. We noted discordances between the identified bronchial isomerism and the presumed arrangement of the atrial appendages in nearly 20% of the patients in our cohort.ConclusionRoutine clinical imaging with chest radiographs, angiographic imaging, and CT/MRI can determine the presence of bronchial isomerism in patients with so-called heterotaxy. Right as opposed to left isomerism can be distinguished based on bronchial angles. The finding of bronchial isomerism correlates well, but not totally, with the presumed isomerism of the atrial appendages as predicted from the identified intra-cardiac morphology.

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