scholarly journals VP16.06: Left atrial isomerism associated with genetic microdeletion syndrome

2020 ◽  
Vol 56 (S1) ◽  
pp. 120-120
Author(s):  
R. Garcia Rodriguez ◽  
Y. Gil Gonzalez ◽  
R. Garcia‐Delgado ◽  
J. Segura Gonzalez ◽  
I. Ortega Cárdenes ◽  
...  
Keyword(s):  
Left Atrial ◽  
Microdeletion Syndrome ◽  
Atrial Isomerism

Prenatal ultrasound diagnosis of pulmonary atresia in combination with left atrial isomerism

2017 ◽  
Author(s):  
M Medvedev, M.V. Kubrina, O.S. Zarubina et all
Keyword(s):  
Left Atrial ◽  
Reverse Flow ◽  
Ductus Arteriosus ◽  
Pulmonary Atresia ◽  
Prenatal Ultrasound ◽  
Ultrasound Diagnosis ◽  
Right Atrial ◽  
Second Trimester ◽  
Left And Right ◽  
Atrial Isomerism

Two cases of prenatal ultrasound diagnosis of left atrial isomerism in the second trimester of gestation is presented. These two cases were in combination with pulmonary atresia and right aortic arch. Left atrial isomerism was identify by the digit-like shape of the left and right atrial appendages. The pulmonary atresia was identified on the basis of reverse flow in small pulmonary artery. A right aortic was identified by “U”-shaped confluence of aorta and ductus arteriosus in view of three vessels and trachea. The trachea was located between the vessels. The pregnancies were terminated and prenatal diagnosis was conformed at autopsy

‘Sinus node’ dysfunction associated with left atrial isomerism

2008 ◽  
Vol 9 (9) ◽  
pp. 953-956 ◽  
Author(s):  
Paolo Ferrero ◽  
Riccardo Massa ◽  
Claudia Amellone ◽  
Giampaolo Trevi
Keyword(s):  
Left Atrial ◽  
Sinus Node ◽  
Sinus Node Dysfunction ◽  
Atrial Isomerism

Unusual drainage of the inferior caval vein in left atrial isomerism

1989 ◽  
Vol 24 (1) ◽  
pp. 35-39 ◽  
Author(s):  
Nathan Roguin ◽  
Simha Milo ◽  
Bernardo Vidne
Keyword(s):  
Left Atrial ◽  
Caval Vein ◽  
Inferior Caval Vein ◽  
Atrial Isomerism

scholarly journals Impact of gastrointestinal comorbidities in patients with right and left atrial isomerism

2021 ◽  
pp. 1-8
Author(s):  
Anastasia Fotaki ◽  
Victoria L. Doughty ◽  
Winston Banya ◽  
Stefano Giuliani ◽  
Sarah Bradley ◽  
...  
Keyword(s):  
Abdominal Surgery ◽  
Left Atrial ◽  
Right Atrial ◽  
Medium Term ◽  
Heterotaxy Syndrome ◽  
Term Survival ◽  
Ladd Procedure ◽  
Atrial Isomerism ◽  
The Impact ◽  
Gastrointestinal Abnormalities

Abstract Background and aim: Heterotaxy syndrome, being right atrial isomerism (RAI) or left atrial isomerism (LAI), often presents with Congenital Heart Disease (CHD). Intestinal abnormalities, including malrotation are common. We assessed the spectrum of gut abnormalities and their impact on medium-term outcome in a cohort of patients with fetal and postnatal diagnoses of heterotaxy syndrome. Methods: We reviewed the cardiology records of heterotaxy syndrome patients from two centres, regarding the presence of CHD, time for cardiac intervention, presence of gastrointestinal abnormalities, and type/time of surgery. A questionnaire about gastrointestinal status was sent to patients <18 years old. Kaplan–Meier curves were derived for survival data and freedom from intervention. Results: Data were included for 182 patients (49 RAI and 133 LAI) of 247 identified. Questionnaires were sent to 77 families and 47 replied. CHD was present in all RAI and 61.7% of LAI cases. Thirty-eight patients had abdominal surgery (20.9%), similar for RAI and LAI (20.4% versus 21%, p> 0.99): Ladd procedure in 17 (44.7%), non-Ladd in 12 (31.5%), and both procedures in 9 (23.7%). Ten-year freedom from Ladd procedure for all was 86% for the whole cohort (RAI = 87%; LAI = 85%, p = 0.98). Freedom from any gastrointestinal surgery at 10 years was 79% for the whole cohort (RAI = 77%; LAI = 80%, p = 0.54). Ten-year freedom from cardiac surgery was 31% for the whole cohort (RAI = 6%; LAI = 43%, p < 0.0001). Conclusions: In our cohort, one in five patients required abdominal surgery, mostly in their first year of life, similar for RAI and LAI. Between 1 and 10 years of follow-up, the impact of gastrointestinal abnormalities on outcome was minimal. Medium term survival was related to CHD.

Cardiac Rhythm Disturbances in Patients with Left Atrial Isomerism

2001 ◽  
Vol 24 (11) ◽  
pp. 1631-1638 ◽  
Author(s):  
MEI-HWAN WU ◽  
JOU-KOU WANG ◽  
JIUNN-LEE LIN ◽  
LING-PING LAI ◽  
HUNG-CHI LUE ◽  
...  
Keyword(s):  
Left Atrial ◽  
Cardiac Rhythm ◽  
Atrial Isomerism

Heterotaxy with left atrial isomerism in a patient with deletion 18p

2000 ◽  
Vol 94 (3) ◽  
pp. 198-200 ◽  
Author(s):  
Maria Cristina Digilio ◽  
Bruno Marino ◽  
Aldo Giannotti ◽  
Roberto Di Donato ◽  
Bruno Dallapiccola
Keyword(s):  
Left Atrial ◽  
Atrial Isomerism

Outcomes of left atrial isomerism over a 28-year period at a single institution

2001 ◽  
Vol 10 (1) ◽  
pp. 82
Author(s):  
T. Gilljam ◽  
B.W. McCrindle ◽  
J.F. Smallhorn
Keyword(s):  
Left Atrial ◽  
Single Institution ◽  
Atrial Isomerism
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