P19.09: The syndrome of right atrial isomerism: prenatal diagnosis and outcome - 2 case reports with literature analysis

2015 ◽  
Vol 46 ◽  
pp. 184-184
Author(s):  
W. Han ◽  
M. Xie ◽  
Y. Wang ◽  
H. Cao ◽  
L. Hong
2017 ◽  
Vol 70 (16) ◽  
pp. C160
Author(s):  
Yu Wang ◽  
ManYing Xie ◽  
Wei Feng ◽  
JiaBao Yin ◽  
Ming Sang ◽  
...  

Author(s):  
M.V. Medvedev , M.V. Kubrina , O.L. Galkina et all

A retrospective analysis of 21 cases of prenatal diagnosed of pulmonary atresia with intact ventricular septum (PA-IVS) is presented. In the study of the four chambers view of the fetal heart the right ventricle was hypoplastic in 16 (76.1 %), normal in 5 (23.8 %) cases. Tricuspid atresia identified in 8 (38 %) cases. The dysplasia of the tricuspid valve identified in 5 (23.8 %) cases. In 2 (8.7 %) cases PA-IVS were in combination with atrioventricular defects. The changes of the tricuspid valve were not identified in 6 (28.5 %) cases. In 100 % cases reduced pulmonary artery with retrograde flow in the pulmonary valve was registrated. Hydrops fetal is detected in 2 (9.5 %) cases. The left aortic arch was in 17 (80.9 %) cases and right aortic arch – 4 (19.1 %). The average gestational age at prenatal diagnosis was 22,6 weeks (range 11–32 weeks). Early diagnosis is represented by one case in 11 weeks. Cardiac defects were registered in 6 (28.5 %) cases and extracardiac defects in 5 (23.8 %) cases. Ventriculocoronary arterial communications were found in 2 (9.5 %) cases of PA-IVS. In 3 (13 %) cases were in combination with heterotaxy syndrome. In 2 (8.7 %) cases PA-IVS were in combination with left atrial isomerism and 1 (4.8 %) with right atrial isomerism. Outcomes in fetuses with PA-IVC: termination of pregnancy — 13 (61.9 %), fetal death — 2 (9.5 %), neonatal death — 5 (23.8 %) cases, only 1 (4.8 %) survivor.


2018 ◽  
Vol 52 ◽  
pp. 238-238
Author(s):  
Y. Wang ◽  
M. Xie ◽  
W. Feng ◽  
J. Yin ◽  
S. Zhou ◽  
...  

2019 ◽  
Vol 54 (S1) ◽  
pp. 312-312
Author(s):  
J. Xu ◽  
Y. Wang ◽  
J. Yin ◽  
J. Zhang ◽  
Y. Hua ◽  
...  

Author(s):  
M Medvedev, M.V. Kubrina, O.S. Zarubina et all

Two cases of prenatal ultrasound diagnosis of left atrial isomerism in the second trimester of gestation is presented. These two cases were in combination with pulmonary atresia and right aortic arch. Left atrial isomerism was identify by the digit-like shape of the left and right atrial appendages. The pulmonary atresia was identified on the basis of reverse flow in small pulmonary artery. A right aortic was identified by “U”-shaped confluence of aorta and ductus arteriosus in view of three vessels and trachea. The trachea was located between the vessels. The pregnancies were terminated and prenatal diagnosis was conformed at autopsy


Author(s):  
Márcia Marinho ◽  
Sara Nunes ◽  
Cátia Lourenço ◽  
Mónica Melo ◽  
Cristina Godinho ◽  
...  

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