Double-outlet right ventricle with absent left ventricle and mitral atresia in a fetus with a deletion 22q12

2004 ◽  
Vol 24 (9) ◽  
pp. 708-712 ◽  
Author(s):  
Aurore L'Herminé-Coulomb ◽  
Lucille Houyel ◽  
Azzedine Aboura ◽  
François Audibert ◽  
Dorothée Dal Soglio ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Mitral Atresia

The spectrum of disease in double outlet right ventricle

2020 ◽  
pp. 73-84
Author(s):  
Andrew Ho ◽  
Tara Bharucha
Keyword(s):  
Left Ventricle ◽  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Pulmonary Stenosis ◽  
Double Outlet Right Ventricle ◽  
Term Infant ◽  
Management Options ◽  
Surgical Options ◽  
Learning Points ◽  
Blalock Taussig Shunt

Although often used as a diagnosis in its own right, double outlet right ventricle is more accurately merely a description of the ventriculo-arterial connection in a congenitally malformed heart, and use of the term must always be allied with further description of the anatomy. In this chapter we describe a term infant born at 3.4 kg following an antenatal diagnosis of double outlet right ventricle (DORV) with noncommitted ventricular septal defect (VSD), side-by-side great arteries and pulmonary stenosis. There was a duct-dependent pulmonary circulation in the neonatal period, and the infant underwent placement of a Blalock-Taussig shunt. Following multi-modality cardiac imaging, he underwent to complete surgical repair at 16 months of age, with VSD enlargement, tunnelled closure of the VSD to commit the left ventricle to the aorta, and augmentation of the pulmonary outflow tract. Through the chapter, we emphasise the importance of a detailed anatomical description and thorough investigation in this family of defects, in order to allow an understanding of the physiology, clinical behaviour and the management options available for individual patients. Learning points in the chapter include discussion regarding the definitions of DORV, detailed descriptions of the major anatomical groups and a synopsis of the more common surgical options.

scholarly journals Double-outlet right ventricle with tunnel from left ventricle to aorta

1976 ◽  
Vol 71 (5) ◽  
pp. 685-690 ◽  
Author(s):  
William H. Neches ◽  
Elinor Dankner ◽  
Sang C. Park ◽  
Cora C. Lenox ◽  
James R. Zuberbuhler ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle

Unguarded mitral orifice, mirror-imaged atrial arrangement, and discordant atrioventricular connections

1999 ◽  
Vol 9 (5) ◽  
pp. 478-483 ◽  
Author(s):  
Satoshi Yasukochi ◽  
Gengi Satomi ◽  
Insam Park ◽  
Masahiko Ando ◽  
Kazuo Momma
Keyword(s):  
Left Ventricle ◽  
Right Ventricle ◽  
Double Outlet Right Ventricle ◽  
Cardiac Malformation ◽  
Atrioventricular Junction ◽  
Mitral Orifice ◽  
Pulmonary Valvar Stenosis

AbstractWe report two autopsy proven cases of unguarded mitral orifice associated with mirror-imaged atrial arrangement, discordant atrioventricular connections, double outlet right ventricle, pulmonary valvar stenosis or atresia, and atrialisation of the morphologically left ventricle. The morphologically left atrioventricular junction was devoid of valvar leaflets, and there was no tension apparatus within the ventricle. To the best of our knowledge, this is the first description of this rare cardiac malformation

Primary Intracardiac Repair of Double Outlet Right Ventricle and Ventricular Septal Defect without Pulmonary Stenosis

1995 ◽  
Vol 3 (3-4) ◽  
pp. 103-108
Author(s):  
KG Jaya Prasanna ◽  
Krishna Subramony Iyer ◽  
Rajesh Sharma ◽  
Balram Airan ◽  
Ivatury Mrityonjaya Rao ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Ventricular Septal Defect ◽  
Right Ventricle ◽  
Septal Defect ◽  
Arterial Switch Operation ◽  
Pulmonary Stenosis ◽  
Double Outlet Right Ventricle ◽  
Arterial Switch ◽  
Intracardiac Repair ◽  
Switch Operation

From January 1991' to May 1994, 29 patients with double outlet right ventricle with ventricular septal defect, without pulmonary stenosis underwent primary intracardiac repair at the All India Institute of Medical Sciences, New Delhi. Patients were classified into 4 groups based on location of the ventricular septal defect. The ventricular septal defect was subaortic in 11, subpulmonary in 13, doubly committed subarterial in 1, and noncommitted in 4 patients. Surgical treatment consisted of intraventricular routing of the left ventricle to the aorta (17), and the left ventricle to the pulmonary artery followed by an arterial switch operation (12). There were 4 (13.9%) early deaths. Follow-up ranged from 3 months to 3 years (mean, 1.5 years). There was no late mortality. Three patients had residual ventricular septal defect, one of whom has undergone reoperation. One patient has a gradient of 25 mmHg across the left ventricular outflow tract. Double outlet right ventricle with subpulmonic ventricular septal defect was found to be a significant risk factor for early mortality (p = 0.03). The subgroup of double outlet right ventricle with subpulmonic ventricular septal defect who had a combination of single coronary artery and post arterial switch operation was particularly prone to pulmonary hypertensive crisis and hospital death (p = 0.002).

scholarly journals Implantation of a stent in a stenotic conduit between the left ventricle and aorta in a patient undergone surgery for a double outlet right ventricle

2018 ◽  
Vol 6 (4) ◽  
pp. 194-197
Author(s):  
Sophie Samyn ◽  
Marielle Morissens ◽  
Ahmed Sanoussi ◽  
José Castro Rodriguez
Keyword(s):  
Left Ventricle ◽  
Right Ventricle ◽  
Pulmonary Stenosis ◽  
Balloon Catheter ◽  
Double Outlet Right Ventricle ◽  
Complex Congenital Heart Disease ◽  
Surgery Complications ◽  
Percutaneous Approach ◽  
Additional Surgery ◽  
High Operative Risk

Abstract Reinterventions for surgery complications in adult patients with complex congenital heart disease are often difficult and have a high operative risk. If anatomically possible, a percutaneous approach is an alternative to surgery. We report the case of a 36 year-old patient who underwent surgery for a double outlet right ventricle with transposition of the great arteries and pulmonary stenosis. On the days following the surgery, the patient was hemodynamically unstable due to a stenosis of the intraventricular Dacron conduit between the left ventricle and the aorta. Because of the fragility of the patient, additional surgery was not possible and a percutaneous approach was preferred. A Cheatham Platinum stent mounted on a balloon-in-balloon catheter was implanted with success in the stenotic intraventricular Dacron conduit.

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