Inflammatory myofibroblastic tumor as a second neoplasm after Wilms tumor

2014 ◽  
Vol 62 (6) ◽  
pp. 1075-1077 ◽  
Author(s):  
Michael V. Ortiz ◽  
Christopher T. Rossi ◽  
D. Ashley Hill ◽  
Phillip C. Guzzetta ◽  
Faisal Qureshi ◽  
...  
Keyword(s):  
Inflammatory Myofibroblastic Tumor ◽  
Wilms Tumor ◽  
Second Neoplasm

scholarly journals Case Report: Inflammatory myofibroblastic tumor causes formation of an ileal conglomerate in a patient previously treated for Wilms’ tumor

F1000Research ◽  
2017 ◽  
Vol 6 ◽  
pp. 677
Author(s):  
Julie Leganger ◽  
Rikke Raagaard Soerensen ◽  
Jacob Rosenberg ◽  
Jakob Burcharth
Keyword(s):  
Small Intestine ◽  
Case Report ◽  
Terminal Ileum ◽  
Inflammatory Myofibroblastic Tumor ◽  
Wilms Tumor ◽  
Pathology Report ◽  
Subsequent Formation ◽  
Meckel’S Diverticulitis ◽  
History Of ◽  
Small Intestinal

Introduction: Inflammatory myofibroblastic tumors (IMTs) are uncommon mesenchymal lesions classified by WHO as neoplasms of uncertain behavior. Morphologically, IMTs are composed of proliferating spindled myofibroblastic cells accompanied by a marked - usually chronic - inflammatory infiltrate. The etiology is unknown, but several theories have been suggested, including an association with Wilms’ tumor. IMTs are rarely diagnosed in adults and have been reported in various organs. IMTs are considered benign but with a potential to recur at their primary site. Case report: A 44-year-old female experienced intermittent severe abdominal pain, loose stools and a visible abdominal bulge. In early childhood the patient had been treated for a Wilms’ tumor. At admission Meckel’s diverticulitis was suspected, but during surgery a tumor in the terminal ileum, creating a conglomerate of small intestinal loops, was observed and completely resected.  The pathology report characterized the tumor as a histologically benign inflammatory myofibroblastic tumor. Postoperatively, the patient experienced several complications including an anastomotic leakage and subsequent formation of an abscess and transcutaneous fistula. Discussion: IMTs rarely arise in the small intestine, and to our knowledge the manifestation of a small intestine conglomerate has not been described previously. Making the diagnosis is difficult, and numerous differential diagnoses were possible in this case. Approximately 8-25% of IMTs in the gastrointestinal tract recur locally. Complete surgical resection is the treatment of choice, and re-excision is the preferred therapy for local recurrence.  To our knowledge, no guidelines concerning follow-ups are available. Conclusion: IMTs in the terminal ileum can mimic Meckel’s diverticulitis and present with symptoms of obstructive ileus due to the formation of a conglomerate of small intestinal loops. Furthermore, IMTs should be considered as a diagnostic possibility in patients with a past medical history of Wilms’ tumor.

Inflammatory Myofibroblastic Tumor of the Kidney and Bilateral Lung Nodules in a Child Mimicking Wilms Tumor With Lung Metastases

2015 ◽  
Vol 37 (6) ◽  
pp. e390-e393 ◽  
Author(s):  
Mehmet S. Dogan ◽  
Selim Doganay ◽  
Gonca Koc ◽  
Sureyya B. Gorkem ◽  
Ekrem Unal ◽  
...  
Keyword(s):  
Inflammatory Myofibroblastic Tumor ◽  
Wilms Tumor ◽  
Lung Metastases ◽  
Lung Nodules ◽  
Bilateral Lung

scholarly journals Case Report: Inflammatory myofibroblastic tumor causes formation of an ileal conglomerate in a patient previously treated for Wilms’ tumor

F1000Research ◽  
2017 ◽  
Vol 6 ◽  
pp. 677
Author(s):  
Julie Leganger ◽  
Rikke Raagaard Soerensen ◽  
Jacob Rosenberg ◽  
Jakob Burcharth
Keyword(s):  
Small Intestine ◽  
Case Report ◽  
Terminal Ileum ◽  
Inflammatory Myofibroblastic Tumor ◽  
Wilms Tumor ◽  
Pathology Report ◽  
Subsequent Formation ◽  
Meckel’S Diverticulitis ◽  
History Of ◽  
Small Intestinal

Introduction: Inflammatory myofibroblastic tumors (IMTs) are uncommon mesenchymal lesions classified by WHO as neoplasms of uncertain behavior. Morphologically, IMTs are composed of proliferating spindled myofibroblastic cells accompanied by a marked - usually chronic - inflammatory infiltrate. The etiology is unknown, but several theories have been suggested, including an association with Wilms’ tumor. IMTs are rarely diagnosed in adults and have been reported in various organs. IMTs are considered benign but with a potential to recur at their primary site. Case report: A 44-year-old female experienced intermittent severe abdominal pain, loose stools and a visible abdominal bulge. In early childhood the patient had been treated for a Wilms’ tumor. At admission Meckel’s diverticulitis was suspected, but during surgery a tumor in the terminal ileum, creating a conglomerate of small intestinal loops, was observed and completely resected.  The pathology report characterized the tumor as a histologically benign inflammatory myofibroblastic tumor. Postoperatively, the patient experienced several complications including an anastomotic leakage and subsequent formation of an abscess and transcutaneous fistula. Discussion: IMTs rarely arise in the small intestine, and to our knowledge the manifestation of a small intestine conglomerate has not been described previously. Making the diagnosis is difficult, and numerous differential diagnoses were possible in this case. Approximately 8-25% of IMTs in the gastrointestinal tract recur locally. Complete surgical resection is the treatment of choice, and re-excision is the preferred therapy for local recurrence.  To our knowledge, no guidelines concerning follow-ups are available. Conclusion: IMTs in the terminal ileum can mimic Meckel’s diverticulitis and present with symptoms of obstructive ileus due to the formation of a conglomerate of small intestinal loops. Furthermore, IMTs should be considered as a diagnostic possibility in patients with a past medical history of Wilms’ tumor.

Role of dactinomycin in the improved survival of children with Wilms' tumor

JAMA ◽  
1966 ◽  
Vol 195 (12) ◽  
pp. 1005-1009 ◽  
Author(s):  
D. J. Fernbach
Keyword(s):  
Wilms Tumor

Minimally Invasive Approach for Wilms Tumor Treatment in a Small Child - A Case Report

Urology ◽  
2020 ◽  
Author(s):  
Alexandre Azevedo Ziomkowski ◽  
João Rafael Silva Simões Estrela ◽  
Nilo Jorge Carvalho Leão Barretto ◽  
Nilo César Leão Barretto
Keyword(s):  
Case Report ◽  
Minimally Invasive ◽  
Wilms Tumor ◽  
Small Child ◽  
Tumor Treatment ◽  
Minimally Invasive Approach ◽  
Invasive Approach

919: Ureteral Extension in Childhood Renal Tumors: A Report From the National Wilms Tumor Study Group (NWTSG)

2007 ◽  
Vol 177 (4S) ◽  
pp. 305-305
Author(s):  
Shane Daley ◽  
Michael Ritchey ◽  
Robert Shamberger ◽  
Robert Sawin ◽  
Thomas Hamilton ◽  
...  
Keyword(s):  
Wilms Tumor ◽  
Renal Tumors ◽  
Study Group ◽  
Tumor Study ◽  
Tumor Study Group

918: B7-H1 Expression Predicts Tumor Recurrence in Patients with Favorable Histology Wilms’ Tumor

2007 ◽  
Vol 177 (4S) ◽  
pp. 304-305
Author(s):  
Jonathan C. Routh ◽  
Richard A. Ashley ◽  
Thomas J. Sebo ◽  
Christine M. Lohse ◽  
Douglas A. Husmann ◽  
...  
Keyword(s):  
Tumor Recurrence ◽  
Wilms Tumor ◽  
Favorable Histology

566: Comparative Genomic Hybridization of Chemotherapy Survived Wilms' Tumor Cells

2004 ◽  
Vol 171 (4S) ◽  
pp. 150-151
Author(s):  
Thorsten Schlomm ◽  
Bastian Gunawan ◽  
Hans J. Schulten ◽  
Norbert Graf ◽  
Ivo Leuschner ◽  
...  
Keyword(s):  
Tumor Cells ◽  
Comparative Genomic Hybridization ◽  
Wilms Tumor ◽  
Comparative Genomic ◽  
Genomic Hybridization
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