Mediastinal extramedullary hematopoiesis mimicking a neuroblastic tumor in a patient with beta-thalassemia

2013 ◽  
Vol 60 (4) ◽  
pp. 711-712 ◽  
Author(s):  
Ernesto Montaruli ◽  
Francesca Marchetti Rosa ◽  
Anu Paul ◽  
Hélène Martelli ◽  
Catherine Guettier ◽  
...  
Keyword(s):  
Extramedullary Hematopoiesis ◽  
Beta Thalassemia ◽  
Neuroblastic Tumor

Spinal cord compression due to extramedullary hematopoiesis in beta-thalassemia

2020 ◽  
Vol 78 (10) ◽  
pp. 663-664
Author(s):  
Renan Ramon Souza LOPES ◽  
Larissa Soares CARDOSO ◽  
Franz ONISHI
Keyword(s):  
Spinal Cord ◽  
Spinal Cord Compression ◽  
Extramedullary Hematopoiesis ◽  
Cord Compression ◽  
Beta Thalassemia

scholarly journals Extramedullary Hematopoiesis Presenting as a Right Adrenal Mass in a Patient With Beta Thalassemia

2014 ◽  
Vol 6 (5) ◽  
Author(s):  
Hossein Karami ◽  
Mehrnoush Kosaryan ◽  
Mehrdad Taghipour ◽  
Rayka Sharifian ◽  
Aili Aliasgharian
Keyword(s):  
Adrenal Mass ◽  
Extramedullary Hematopoiesis ◽  
Beta Thalassemia

Presence of the IVS-I-6-Mutated Allele in Beta-Thalassemia Major Patients Correlates with Extramedullary Hematopoiesis Incidence

2017 ◽  
Vol 137 (3) ◽  
pp. 175-182 ◽  
Author(s):  
Nikolaos Sousos ◽  
Despoina Adamidou ◽  
Philippos Klonizakis ◽  
Alexandra Agapidou ◽  
Stamatia Theodoridou ◽  
...  
Keyword(s):  
Middle Eastern ◽  
Thalassemia Major ◽  
Extramedullary Hematopoiesis ◽  
Biological Factor ◽  
Beta Thalassemia ◽  
Eastern Region ◽  
Hematopoietic Tissue ◽  
Multicenter Studies ◽  
Clinical Issue

Extramedullary hematopoiesis (EMH) results from the extension of hematopoietic tissue beyond the confines of the bones. Since the initiation of regular transfusion programs from an early age for all thalassemia major (ΤΜ) patients, EMH has not been considered a clinical issue anymore. The present study aims to record the prevalence of EMH in chronically transfused ΤΜ patients followed at our institution and to investigate possible risk factors associated with its occurrence. The project was designed as a retrospective, nonexperimental, descriptive, exploratory study. In total, the study enrolled 104 patients. EMH was revealed in 15/104 (14%) patients. The presence of intravening sequence (IVS)-I-6 was significantly related with the development of EMH (p < 0.05). No other demographic or biological factor studied was found to be related with the presence of EMH. The study stresses a profound incidence of asymptomatic EMH in a solid group of well-transfused ΤΜ patients. Given the high incidence of the IVS-I-6 allele in the Mediterranean and Middle Eastern region, high-quality, prospective, multicenter studies could confirm the association of EMH occurrence with the presence of the IVS-I-6 mutation and further evaluate the exact role of this mutation in the EMH process.

scholarly journals Intracranial Extramedullary Hematopoiesis in Beta-Thalassemia

2012 ◽  
Vol 13 (2) ◽  
pp. 240 ◽  
Author(s):  
Bivek Karki ◽  
Yi-Kai Xu ◽  
Karuna Tamrakar ◽  
Yuan-Kui Wu
Keyword(s):  
Extramedullary Hematopoiesis ◽  
Beta Thalassemia
Sign in / Sign up

Export Citation Format

Share Document